Presentation
In the present report, we describe a case of PEH in a 39-yr-old woman. Immunohistochemically, the tumor cells were positive for CD34. [pesquisa.bvsalud.org]
The present case, on review and correlation with histomorphology, depicts most of the cytologic features of hepatic EH. [cytojournal.com]
It often presents in infancy with cardiac failure because of extensive arteriovenous shunting within the lesion. [en.wikipedia.org]
Entire Body System
- Asymptomatic
60% women No predisposing factors; occasional cases reported in vinyl chloride workers, women on oral contraceptives, hepatitis B / C patients, following hepatic trauma Symptoms: abdominal pain, weight loss, hepatic venous outflow obstruction; 40% are asymptomatic [pathologyoutlines.com]
[…] origin of the celiac artery and a decrease in the diameter distally, indicating significant shunting, is seen on angiograms. [16] Because most hemangioendotheliomas in infants sponanteously involute and regress within the first 12 to 18 months of life, asymptomatic [en.wikipedia.org]
Some cases of partial spontaneous regression were also reported in some asymptomatic patients. [ncbi.nlm.nih.gov]
- Inflammation
Interferon: The body produces interferon to combat infections or control inflammation. [en.wikipedia.org]
- Lymphadenopathy
[…] anemia are also statistically worse, as well as those presenting pleural invasion and pleural effusion on chest X-ray at detection, extensive intravascular, endobronchial or intestinal tumor spread, hilar metastases or liver involvement, peripheral lymphadenopathy [ncbi.nlm.nih.gov]
Gastrointestinal
- Abdominal Mass
Newborn with abdominal mass and distention. Consultant for Pediatricians. 2010;9:168-173. ^ Banks T, Podraza J. What's Your Diagnosis? Newborn with abdominal mass and distention. Condultant for Pediatricians. 2010;9:168-173. External links [ edit ] [en.wikipedia.org]
Neurologic
- Confusion
Jun 15, 2001 · Inflammatory pseudotumor of the liver, a rare benign lesion, is often confused with the malignant tumors. Until 1998, less than 80 cases had been reported in the world[1,2]. [sultowanigh.ml]
In the lung and liver, common sites of metastatic tumor, it was most likely to be confused with carcinoma a far more common type of tumor. [en.wikipedia.org]
- Irritability
/3 Sickling sensations of the left arm 1/3 Radzikowska 18 1 0/1 62 Multiple bilateral Interferon-2 None 6 months (then lost at observation) Cough Osteo-articular pain Ye 19 1 0/1 55 Multiple bilateral None (refused) Liver 7 months Pleuritic pain and irritable [ncbi.nlm.nih.gov]
Workup
Therefore, preoperative diagnostic workup is of utmost importance to differentiate it from other primary and metastatic tumors of the liver. [bib.irb.hr]
Treatment
•Others like surgery can be done as treatment for the virus during its most severe. [en.wikipedia.org]
Prognosis
Although the metastatic rate in this series was 27%, the prognosis is considered much more favorable than that of other hepatic malignancies. [scienceopen.com]
A standardized treatment algorithm for HEH already does not exist, due to its infrequency and variable prognosis. [eprints.bice.rm.cnr.it]
Weiss in 1996 as "spindle cell hemangioma", rather than hemangioendothelioma, due to the excellent prognosis observed in a group of 78 patients. [5] Retiform hemangioendothelioma (also known as a "Hobnail hemangioendothelioma" [3] ) is a low-grade angiosarcoma [en.wikipedia.org]
Etiology
Epithelioid hemangioendothelioma (EHE) is a rare neoplasm of vascular origin that occurs in the liver and other organs; its etiology is unknown. [scienceopen.com]
The etiology is still a dilemma. Studies about suggestive hypothesis are ongoing. [ncbi.nlm.nih.gov]
Epidemiology
Epidemiology [ edit ] It is so rare that only 0.01 percent of the cancer population has it and it affects about 1 person in every 1,000,000 worldwide. [4] Around 20 cases are diagnosed in America every year – the cause is unknown. [5] It is unresponsive [en.wikipedia.org]
Journal Journal ID (nlm-ta): Pan Afr Med J Journal ID (iso-abbrev): Pan Afr Med J Journal ID (publisher-id): PAMJ Title: The Pan African Medical Journal Publisher: The African Field Epidemiology Network ISSN (Electronic): 1937-8688 Publication date (Electronic [scienceopen.com]
Prevention
Because the lesion may otherwise mimic a hepatic tumor, knowledge of these findings may prevent unnecessary biopsy or inappropriate treatment. Inflammatory pseudotumor of the liver: 13 cases of MRI. [sultowanigh.ml]
When the lesions are small and limited in number, some authors recommend surgical resection or an preventive approach to asymptomatic patients. Successful curative resection achieves good outcomes. [ncbi.nlm.nih.gov]