Presentation
In the present report, we describe a case of PEH in a 39-yr-old woman. Immunohistochemically, the tumor cells were positive for CD34. [pesquisa.bvsalud.org]
The present case, on review and correlation with histomorphology, depicts most of the cytologic features of hepatic EH. [cytojournal.com]
It often presents in infancy with cardiac failure because of extensive arteriovenous shunting within the lesion. [en.wikipedia.org]
Entire Body System
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Falling
Signs and symptoms [ edit ] They have been described as masses that fall between a hemangioma and angiosarcoma. [en.wikipedia.org]
[…] confirmed these findings using electron microscopy and revealed a diffuse cytoplasmic staining of the malignant cells with a factor VIII-related antigen. 8 The recent World Health Organization (WHO 2002) classification describes EHE as lesions that fall [ncbi.nlm.nih.gov]
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Pseudotumor
Hepatic Pseudotumor Due To Nodular Fatty Sparing: The. OBJECTIVE. [sultowanigh.ml]
Gastrointestinal
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Abdominal Mass
Newborn with abdominal mass and distention. Consultant for Pediatricians. 2010;9:168-173. Banks T, Podraza J. What's Your Diagnosis? Newborn with abdominal mass and distention. Condultant for Pediatricians. 2010;9:168-173. External links [ edit ] [en.wikipedia.org]
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Abdominal Pain
pain, weight loss, hepatic venous outflow obstruction; 40% are asymptomatic FNA not recommended as even small biopsies can be misleading Indolent and slow growing; 5 year survival of 43% 50% have extrahepatic involvement at diagnosis, which does not [pathologyoutlines.com]
At the last follow-up (14 months after diagnosis), he is well appearing except for mild abdominal pain. » Discussion EH is a distinctive vascular tumor occurring mostly in soft tissues of extremities and lung. [3] Involvement of liver may be seen as a [cytojournal.com]
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Loss of Appetite
This rare tumor is briefly discussed along with its distinctive histologic features and various differential diagnoses. » Case Report A 2 3 -year-old male presented with a 10 - month history of persistent upper abdominal pain associated with loss of appetite [cytojournal.com]
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Upper Abdominal Pain
This rare tumor is briefly discussed along with its distinctive histologic features and various differential diagnoses. » Case Report A 2 3 -year-old male presented with a 10 - month history of persistent upper abdominal pain associated with loss of appetite [cytojournal.com]
Cardiovascular
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Thrombosis
Inflammatory cellular infiltrate, congestion in the adjacent lung parenchyma and fibrin thrombosis are usually not seen. [ncbi.nlm.nih.gov]
Liver, Gall & Pancreas
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Hepatomegaly
Contrast-enhanced computed tomography (CECT) scan showed hepatomegaly, more in the left lobe than the right lobe with heterogeneous attenuation and variegated enhancement of right lobe. [cytojournal.com]
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Hepatic Mass
Currently there is an increasing use of guided fine needle aspiration cytology (FNAC) in diagnosis of accessible visceral lesions, especially hepatic masses. [cytojournal.com]
Skin
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Subcutaneous Nodule
nodule. [2] : 601 Kaposiform hemangioendothelioma (also known as "Infantile kaposiform hemangioendothelioma" [3] ) is an uncommon vascular tumor, first described by Niedt, Greco, et al. [en.wikipedia.org]
Workup
Therefore, preoperative diagnostic workup is of utmost importance to differentiate it from other primary and metastatic tumors of the liver. [bib.irb.hr]
Ultrasound
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Enlargement of the Liver
Symptoms are rare, however, they may cause pain, nausea, or enlargement of the liver. CT scan or MRI is generally used to diagnose hepatic hemangiomas. Hepatic hemangiomaMultimedia EncyclopediaHealth. [sultowanigh.ml]
Treatment
Treatment [ edit ] Treatment is varied and depends on the site and extent of tumor involvement, site(s) of metastasis, and specific individual factors. [en.wikipedia.org]
Prognosis
Weiss in 1996 as "spindle cell hemangioma", rather than hemangioendothelioma, due to the excellent prognosis observed in a group of 78 patients. [5] Retiform hemangioendothelioma (also known as a "Hobnail hemangioendothelioma" [3] ) is a low-grade angiosarcoma [en.wikipedia.org]
The clinical signs and the prognosis of this tumor are quite variable. From the present case report, the authors have sought to contribute with literature data. Hepatic Pseudotumor Due To Nodular Fatty Sparing: The. OBJECTIVE. [sultowanigh.ml]
Etiology
The etiology is still a dilemma. Studies about suggestive hypothesis are ongoing. [ncbi.nlm.nih.gov]
Epidemiology
Epidemiology [ edit ] It is so rare that only 0.01 percent of the cancer population has it and it affects about 1 person in every 1,000,000 worldwide. [4] Around 20 cases are diagnosed in America every year – the cause is unknown. [5] It is unresponsive [en.wikipedia.org]
Prevention
Because the lesion may otherwise mimic a hepatic tumor, knowledge of these findings may prevent unnecessary biopsy or inappropriate treatment. Inflammatory pseudotumor of the liver: 13 cases of MRI. [sultowanigh.ml]
When the lesions are small and limited in number, some authors recommend surgical resection or an preventive approach to asymptomatic patients. Successful curative resection achieves good outcomes. [ncbi.nlm.nih.gov]