Presentation
Cavernous hemangiomatosis of the colon and liver in a 38-year-old woman presenting with a history of cramp like abdominal pain and a mass in the right iliac fossa are presented. [ncbi.nlm.nih.gov]
Entire Body System
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Coarctation of the Aorta
[…] of the aorta and cardiac defects, and eye abnormalities) syndrome (PHACES, if sternal clefting/supraumbilical raphe is included). [ncbi.nlm.nih.gov]
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Recent Viral Illness
A viral etiology has been proposed in several patients with PVOD who recounted a recent viral illness (, 1, , 10 ). [pubs.rsna.org]
Respiratoric
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Sputum
There was no history of fever, cough, sputum, wheezing, or hemoptysis. Examination revealed mild central cyanosis, tachycardia, and loud P 2. There were no murmurs or congestive heart failure. [circ.ahajournals.org]
Serial acid-fast bacilli tests in induced sputum were negative. An electrocardiogram showed signs of right ventricular overload. [scielo.br]
Gastrointestinal
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Epigastric Pain
A 35 year-old woman presented to hospital with main complaint of epigastric pain and abdominal fullness. An enhanced computed tomography scan revealed a massive liver tumor in right lobe about 150 mm in size. [ncbi.nlm.nih.gov]
Cardiovascular
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Vascular Disease
Abstract Pulmonary capillary hemangiomatosis (PCH) is a rare and an only recently described vascular disease. [doi.org]
Abstract: Intrathoracic manifestations of collagen vascular diseases are very common. [rb.org.br]
Neurologic
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Meningism
Diffuse neonatal hemangiomatosis presents with multiple, progressive, rapidly growing cutaneous hemangiomas associated with widespread visceral hemangiomas in the liver, lungs, gastrointestinal tract, brain, and meninges. [ncbi.nlm.nih.gov]
Workup
During a further workup, we obtained previous outside abdominal US images taken 8 years earlier, and they showed diffuse and inhomogeneous echogenicity throughout the liver, suggesting pre-existing diffuse hemangiomatosis ( Fig. 3 ). [e-ultrasonography.org]
X-Ray
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Kerley A Lines
(a) Radiograph collimated to the right lower lobe demonstrates numerous Kerley B lines (arrow). [pubs.rsna.org]
There were no Kerley-B lines or pleural effusion. The ECG showed right axis deviation and right ventricular hypertrophy with ST–T changes ( Figure 2 ). [circ.ahajournals.org]
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Kerley B Lines
(a) Radiograph collimated to the right lower lobe demonstrates numerous Kerley B lines (arrow). [pubs.rsna.org]
There were no Kerley-B lines or pleural effusion. The ECG showed right axis deviation and right ventricular hypertrophy with ST–T changes ( Figure 2 ). [circ.ahajournals.org]
Axis
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Right Axis Deviation
The ECG showed right axis deviation and right ventricular hypertrophy with ST–T changes ( Figure 2 ). The echocardiogram showed a dilated right ventricle with mild tricuspid regurgitation and decreased systolic function. [circ.ahajournals.org]
Electrocardiography typically demonstrates right axis deviation and right ventricular hypertrophy. [pubs.rsna.org]
Hypertrophy
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Ventricular Hypertrophy
ECG showing sinus tachycardia and partial right bundle-branch block with right ventricular hypertrophy. Figure 3. [circ.ahajournals.org]
Electrocardiography typically demonstrates right axis deviation and right ventricular hypertrophy. [pubs.rsna.org]
Treatment
The possibility of multiple organ involvement and the exacerbating effects of erythropoietin treatment should be considered in cases in which multiple cutaneous hemangiomas develop in preterm infants receiving erythropoietin treatment. [ncbi.nlm.nih.gov]
Median survival without treatment is 3 years.Imatinib may be of use.Epoprostenol does not appear to be of use. [en.wikipedia.org]
Prognosis
We report the clinical and histological findings and discuss about the impact of this unexpected and not-previously described associated lesion on the prognosis and on the therapeutic strategy in patients with pulmonary hypertension associated with congenital [ncbi.nlm.nih.gov]
Disease (PVOD) Primary Pulmonary Hypertension (PPH) Chronic Pulmonary Thromboemboli Pathology Some evidence that proliferation of thin-walled capillaries in PCH is histologic reaction to PVOD Clinical Issues Normal pulmonary capillary wedge pressure Prognosis [radiologykey.com]
Prognosis is poor, with an estimated mean survival of 36 months. 1 A 53-year old man, former smoker (39 pack-years), presented with worsening dyspnoea upon exertion and fatigue lasting 4 years. [archbronconeumol.org]
Etiology
Our findings cannot exclude a neoplastic origin from splenic sinuses but, finally, the etiology and pathogenesis of this vascular lesion remain uncertain. [ncbi.nlm.nih.gov]
Unlike most pathology textbooks, diseases are grouped on the basis of pathologic findings rather than etiology, mirroring the actual practice of surgical pathology. [books.google.com]
The natural history and its etiology are uncertain, although in the literature have been cited the role of steroids and metoclopramide. [journals.lww.com]
[…] rare cases without recognizable causative background disease ( Am J Surg Pathol 2006;30:850 ) Epidemiology Very rare, mostly in adults Mean age 30 years, range 2-71 years Pathophysiology Chronic passive congestion may lead to capillary proliferation Etiology [pathologyoutlines.com]
Epidemiology
Consider diagnosis of "secondary PCH" or PCH-like changes for proliferations seen in association with other disorders, reserving "primary PCH" for extremely rare cases without recognizable causative background disease ( Am J Surg Pathol 2006;30:850 ) Epidemiology [pathologyoutlines.com]
Pathophysiology
[…] seen in association with other disorders, reserving "primary PCH" for extremely rare cases without recognizable causative background disease ( Am J Surg Pathol 2006;30:850 ) Epidemiology Very rare, mostly in adults Mean age 30 years, range 2-71 years Pathophysiology [pathologyoutlines.com]
Pulmonary hypertension in collagen vascular disease may result from a range of different pathophysiological mechanisms including loss of pulmonary capillary network as a result of fibrotic interstitial disease; intrinsic pulmonary arteriopathy with vascular [rb.org.br]
Pathophysiology The precise etiology of IH remains unknown. Viral causes have been speculated, but none elucidated. [clinicalgate.com]
Prevention
CONCLUSION: We report our experience with a single patient of Hemangiomatosis induced heart failure which responded to propranolol combined with medication to control heart failure and failure to thrive prevention. [ncbi.nlm.nih.gov]
It is well known that thyroid hormones are necessary for growth and development during early infancy and that the early detection and treatment of hypothyroidism is important to prevent growth retardation and intellectual loss[ 10 ]. [jmedicalcasereports.biomedcentral.com]
Health professionals are encouraged to take the ESC/ERS Guidelines fully into account when exercising their clinical judgment, as well as in the determination and the implementation of preventive, diagnostic or therapeutic medical strategies; however, [pdfslide.net]
In it you will find a wide variety of medications to treat most diseases and their prevention. LDN has not been specifically tested to treat CFS! [celiac365.com]
G. (1993) Failure of the Flashlamp- Pumped Pulsed Dye Laser to Prevent Progression to Deep Hemangioma. Pediat. Derm., 10, 1, 77-80. Go to original source... Go to PubMed... [biomed.papers.upol.cz]