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Humero-Ulnar Synostosis

Humero-Ulnar Fusion


Presentation

  • Of special value is the thorax and various conditions that exhibit that sign. presentation of variability of the condition with age.[books.google.de]
  • .; Gordon, Emma; Lynch, Sally A. 2018-01-01 00:00:00 CLINICAL REPORTWe present a male infant, the second child of non‐consanguineous Irish parents, who was initially seen in the Genetics clinic at seven months of age.[deepdyve.com]
  • Here, we present a unique case of bilateral humeroradial synostosis. The case presented here is of a 18-month boy, born with bilateral humeroradial synostosis and no other anamoly.[wajradiology.org]
  • The wrist joint in CRUS had three levels of radial and ulnar bone location: 68.6% present the (0) variant (articular plates located at the same level), 5.7% present the (–) variant (the ulnar head was located proximal to the radius articular plate); and[journals.eco-vector.com]
Broad Thumb
  • Humeroradial synostosis, together with brachy-cephaly, mild syndactyly, and broad thumbs and toes, also occurs with Pfeiffer syndrome (acrocephalosyn-dactyly, OMIM 101600) (Martsolfet al. 1971).Humero-radio-ulnar synostosis has been noted in association[rrnursingschool.biz]
Arachnodactyly
  • […] also displays craniosynostosis with brachy-cephaly and frontal bossing, midface hypoplasia, choanal atresia, depressed nasal bridge, dysplastic ears, stenotic external auditory canals, bowed femurs, joint contractures, narrow chest with gracile ribs, arachnodactyly[rrnursingschool.biz]
Pseudotumor
  • […] of the gastrointestinal tract in infancy and childhood 508 Benign pneumatosis 509 Reduced intestinal gas 510 Increased distance between the intestinal loops 511 Intraabdominal cysts in children 512 Migratory peritoneal calcifications 514 Peritoneal pseudotumors[books.google.com]
Stridor
  • […] density along the inner wall of the upper chest in the newborn 290 The respiratory system of the older infant chilld and youngster 28 Upper airways narrowing or obstruction in infancy and children 291 Retropharyngeal softtissue thickening in children 292 Stridor[books.google.com]
Pleural Effusion
  • effusion 350 Pleural effusion with or without pulmonary pathology 351 Parietal pleural thickening without pleural fluid 352 Localized pleural thickening in children 353 The Mediastinum and the Diaphragm Mediastinum 1 Pneumomediastinum in infancy and[books.google.com]
Ulcer
  • […] stomach in infants 476 Antral outlet obstruction of the stomach 477 Coarse mucosal folds or mucosal irregularities of the stomach 478 Pneumatosis or air in the gastric wall 479 Duodenal obstruction with or without its luminal distention 480 Duodenal ulcer[books.google.com]
Dysplastic Ears
  • The syndrome also displays craniosynostosis with brachy-cephaly and frontal bossing, midface hypoplasia, choanal atresia, depressed nasal bridge, dysplastic ears, stenotic external auditory canals, bowed femurs, joint contractures, narrow chest with gracile[rrnursingschool.biz]
Platyspondyly
  • Roberts-SC phocomelia syndrome (OMIM 268300) manifests with limb reduction defects (absent, hypoplastic, bowed, and deformed long and short tubular bones, missing rays), fused thin ribs with abnormal rib number, and platyspondyly with reduced intervertebral[rrnursingschool.biz]
Hip Pain
  • Utilize the very latest approaches in hip surgery including hip resurfacing, hip preservation surgery, and treatment of hip pain in the young adult; and get the latest information on metal-on-metal hips so you can better manage patients with these devices[books.google.com]

Workup

Bowel Distention
  • distention 484 Malabsorption patterns of the small bowel 486 Fixed stiff small bowel loops 487 Destruction of the small bowel mucosa 488 Deformation of the terminal ileum 489 Lesions mimikig regional enteritis 490 Abnormalities of the ileocecal valve[books.google.com]
Atelectasis
  • […] chest in the newborn 283 Unilateral hyperlucent thorax in the newborn 284 Coarse parenchymal markings with irregular bilateral changes and hyperinflation in the newborn 285 Cystlike structures in the lung parenchyma of the newborn 286 Neonatal platlet atelectasis[books.google.com]
Hyperlucent Lungs
  • lung 313 Bilateral underaeration of the lungs in the pediatric age 315 Pneumonia pattern in children 316 Acute alveolar disease 317 Lobar pneumonia in children 318 Homogeneous lobar or segmental opacification 319 Round pneumonia 320 Pulmonary round lesions[books.google.com]
Colonic Stricture
  • stricture or narrowing 496 Segmental colonic narrowing in children 497 Toxic megacolon 498 Distention of the small andor large bowelnonobstructive paralytic ileus 499 Distended large bowel 500 Large bowel obstruction 502 Large retrorectal space 503 Large[books.google.com]
Pleural Effusion
  • effusion 350 Pleural effusion with or without pulmonary pathology 351 Parietal pleural thickening without pleural fluid 352 Localized pleural thickening in children 353 The Mediastinum and the Diaphragm Mediastinum 1 Pneumomediastinum in infancy and[books.google.com]

Treatment

  • Make informed clinical choices for each patient, from diagnosis and treatment selection through post-treatment strategies and management of complications, with new evidence-based criteria throughout.[books.google.com]
  • It is reasonable to start CRUS surgical treatment at the age of 3 years. 5. All deformity variants are indications for surgical treatment, considering that treatment technique selection is determined by the degree of its severity. 6.[journals.eco-vector.com]
  • CLOSE Medical Disclaimer The medical information on this site is provided as an information resource only, and is not to be used or relied on for any diagnostic or treatment purposes.[diseaseinfosearch.org]
  • Two-stage double-level rotational osteotomy in the treatment of congenital radioulnar synostosis. Acta Orthop Belg . 2007 Dec. 73(6):704-9. [Medline] . Green WT, Mital MA. Congenital radio-ulnar synostosis: surgical treatment.[emedicine.medscape.com]
  • Two-stage double-level rotational osteotomy in the treatment of congenital radioulnar synostosis. Acta Orthop Belg. 2007 Dec. 73(6):704-9. [Medline]. Green WT, Mital MA. Congenital radio-ulnar synostosis: surgical treatment.[emedicine.medscape.com]

Prognosis

  • This entity can be distinguished from the TAR syndrome (thrombocytopenia and absent radii) by the distinctive orthopedic issues, different underlying genetic mutations, and a more worrisome prognosis for CAMT than for TAR.[mayoclinic.pure.elsevier.com]
  • Prognosis - Humeroradial synostosis Not supplied. Treatment - Humeroradial synostosis Not supplied. Resources - Humeroradial synostosis Not supplied.[checkorphan.org]
  • Conservative observation Surgical early presentation (infancy) radial head reduction must have only mild deformity of radial head and capitellum technique: osteotomy of radius annular ligament reconstruction late presentation radial head excision Outcomes: Prognosis[posna.org]
  • Home Fever Tests * Home Ear Infection Tests * Home Flu Tests * Home Andropause Tests * Prostate Health: Home Testing: * Home Prostate Tests * Home PSA Antigen Tests * Home Testosterone Tests * Mental Health: Home Testing: * Home Emotional Stress Tests Prognosis[checkorphan.org]
  • Posttraumatic radioulnar synostosis is a separate entity from the congenital form, having a different cause, treatment, and prognosis. [3] The traumatic form can occur anywhere between the radius and ulna along the length of the interosseous membrane.[emedicine.medscape.com]

Etiology

  • Part A DOI: 10.1002/ajmg.a.38632 Congenital anomalies of the upper limbs are rare and etiologically heterogeneous.[semanticscholar.org]
  • […] interstitial and granulonodulo alveolar pattern 324 Interstitialreticular pulmonary pattern 326 Disseminated interstitial pneumonitis 327 The miliary pattern of pneumonia 328 Short linear andor wedgeshaped densities 329 Pulmonary edema in infancy and childhood Etiology[books.google.com]
  • Etiology unknown Genetics not specified 1/3 associated with other skeletal dysplasias Incidence unknown Associated Conditions radioulnar synostosis, ulnar dysplasia, nail-patella syndrome Clinical Evaluation: History / Exam Findings child is usually presents[posna.org]
  • These conditions were ruled out as a possible etiology in this case, as there is no evidence of remodeling or callous formation associated with fracture healing.[mcclungmuseum.utk.edu]
  • Introduction Definition bony bridge between the proximal radius and ulna Etiology forearm begins as a single cartilaginous anlage and divides from distal to proximal into the radius and ulna in the 7th week in utero failure of differentiation results[orthobullets.com]

Epidemiology

  • Post-traumatic radioulnar synostosis Epidemiology This is much more common Rate between 2-6% (the latter figure in a series which used a single incision approach to the forearm).[nsec.com.au]
  • […] proximal radius and ulna Etiology forearm begins as a single cartilaginous anlage and divides from distal to proximal into the radius and ulna in the 7th week in utero failure of differentiation results in synostosis in proximal aspect of the forearm Epidemiology[orthobullets.com]
  • […] separation of the distal radius and ulna for a time the proximal radius and ulna are united and share a common perichondrium abnormal genetic or teratogenic factors operating at this time would interfere with proximal radioulnar joint morphogenesis Epidemiology[gait.aidi.udel.edu]
  • Chung KC, Spilson SV (2001) The frequency and epidemiology of hand and forearm fractures in the United States. J Hand Surg Am 26(5):908–915 CrossRef PubMed Google Scholar 2.[link.springer.com]
  • […] radius and ulna, or injury to the interosseous membrane. [14] Patients with closed head injuries (skull/cranial trauma) appear to be more prone to this complication, presumably for the same reason that they develop heterotopic ossification . [15, 16] Epidemiology[emedicine.medscape.com]
Sex distribution
Age distribution

Pathophysiology

  • Groves later postulated that the success of treatment depended on where in the forearm synostosis had occurred. [4, 5] Pathophysiology The skeletal anomaly includes varying degrees of proximal radial and ulnar fusion, with or without involvement of the[emedicine.medscape.com]

Prevention

  • Prevention - Humeroradial synostosis Not supplied. Diagnosis - Humeroradial synostosis Not supplied. Prognosis - Humeroradial synostosis Not supplied. Treatment - Humeroradial synostosis Not supplied. Resources - Humeroradial synostosis Not supplied.[checkorphan.org]
  • Careful dissection with minimal periosteal disruption prevents the further stimulation of bone, limiting recurrence.[emedicine.medscape.com]
  • These involve excision of synostosis and interposition of inert tissue to prevent reformation of synostosis, However, synostosis typically recurs inspite of the interposition of silicone, fat, or muscle.[boneandspine.com]
  • The contracted soft tissues will also prevent any meaningful return of motion. Derotation and fixation in the derotated position is preferred.[nsec.com.au]
  • The accurate adaptation of the trochlea of the humerus, with its prominences and depressions, to the trochlear notch of the ulna, prevents any lateral movement.[en.wikipedia.org]

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