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Hypertrophic Interstitial Neuropathy

Neuritis Hypertrophic Interstitial


Presentation

  • Two pitfalls are present for the student, however. First, the abnormalities are superimposed on a changing, developing brain, not a rather static, mature organ.[books.google.com]
  • Fenton, MD present Imaging Painful Spine Disorders, the diagnostic companion to Image-Guided Spine Intervention, with 1,400 high-quality radiographic images to help you diagnose common and rare spine pain conditions.[books.google.de]
  • None of these features were present in our patients. Features of Wegener's granulomatosis were not present in any of the patients reported here.[neurologyindia.com]
  • The most intense lymphocytic inflammation was present focally in lumbar nerve roots (Figure 1D).[path.upmc.edu]
  • Case report presentation and review of the literature. Jpn Heart J. 1990;31:404-410. Mitchell GW, Response to immunosuppressive therapy in patients with hereditary motor and sensory neuropathy and associated dysimmune neuromuscular disorders.[rarediseases.org]
Fever
  • […] neuropathic spondylopathy in syringomyelia ( G95.0 ) neuropathic spondylopathy in tabes dorsalis ( A52.11 ) nonsyphilitic neuropathic spondylopathy NEC ( G98.0 ) spondylitis in syphilis (acquired) ( A52.77 ) tuberculous spondylitis ( A18.01 ) typhoid fever[icd10data.com]
  • During this period she was having increasing frequency and intensity of headaches and intermittent low grade fever for which she was started on antitubercular therapy.[neurologyindia.com]
  • […] the face Dermoid cyst of the neck Dermoid or epidermoid cyst of the central nervous system Dermolytic epidermolysis bullosa Dermoodontodysplasia Dermotrichic syndrome Desbuquois dysplasia Desbuquois syndrome DESC syndrome DES embryofetopathy Desert fever[orpha.net]
Pathologist
  • […] interstitial hypertrophic neuropathy Roussy, Gustave, French pathologist, 1874-1948.[medical-dictionary.thefreedictionary.com]
  • GROSS AND MICROSCOPIC DESCRIPTIONS: Autopsy examination was limited to the 1350 gram formalin-fixed brain, spinal cord, skeletal muscle, and a peripheral nerve segment submitted by the referring pathologist.[path.upmc.edu]
Hyperthermia
  • Encephalopathy in Hyperthermia 134 Arsenical Encephalopathy 136 Anoxic 148 Central Pontine Myelinolysis 158 Infarcts with Arterial Thrombosis 160 Infarcts with Cerebral Embolism 164 Aseptic 166 Embolism Following Cardiac Surgery 166 Thromboembolism Associated[books.google.com]
Surgical Procedure
  • First Metatarsal Shaft in Hallux Abducto Valgus 557 Mau and Ludloff Osteotomies 572 Arthrodesis of the First Metatarsophalangeal Joint 581 Juvenile Hallux Abducto Valgus Deformity 609 Traditional Procedures for the Repair of Hallux Abducto Valgus 623 Surgical[books.google.com]
Spine Pain
  • Fenton, MD present Imaging Painful Spine Disorders, the diagnostic companion to Image-Guided Spine Intervention, with 1,400 high-quality radiographic images to help you diagnose common and rare spine pain conditions.[books.google.de]
Back Pain
  • No other reference features as many case studies illustrating the imaging presentation of back pain, provides a detailed differential diagnosis, and points out clinical pitfalls and common diagnosis errors quite like this one.[books.google.de]
Ataxia
  • Dejerine-Roussy syndrome - see under Dejerine Roussy-Cornil syndrome - occasional lancinating pains, with peripheral weakness, fasciculation, visual disturbance, and ataxia.[medical-dictionary.thefreedictionary.com]
  • , ataxy, ataxic R27.0 ICD-10-CM Diagnosis Code R27.0 Ataxia, unspecified 2016 2017 2018 2019 Billable/Specific Code Type 1 Excludes ataxia following cerebrovascular disease ( I69. with final characters -93) Roussy-Lévy G60.0 Atrophy, atrophic (of) muscle[icd10data.com]
  • Early signs in childhood include disability in locomotion out of proportion to measurable weakness, later with frank sensory ataxia, deformities of the spine and feet and increase in the total protein in cerebrospinal fluid.[pediatrics.aappublications.org]
  • […] disorders of the peripheral nervous system Excludes: • neuralgia NOS ( M79.2 ) • neuritis NOS ( M79.2 ) • peripheral neuritis in pregnancy ( O26.82- ) • radiculitis NOS ( M54.10 ) G60 Hereditary and idiopathic neuropathy ICD-10-CM Index References • Ataxia[coding-pro.com]
  • […] neuropathy, types I-IV Hypertrophic neuropathy of infancy Peroneal muscular atrophy (axonal type) (hypertrophic type) Roussy-Levy syndrome G60.1 Refsum's disease Inclusion term(s): Infantile Refsum disease G60.2 Neuropathy in association with hereditary ataxia[icd10coded.com]
Peripheral Neuropathy
  • neuropathy Peripheral neuropathy, idiopathic Peripheral neuropathy, paraneoplastic Polyneuropathy Polyneuropathy (disorder of multiple nerves) Polyneuropathy (multiple nerve disorder) Polyneuropathy due to lyme disease Polyneuropathy, paraneoplastic[icd9data.com]
  • Peripheral Neuropathy 2. Peripheral Neuropathy DEFINITION:It is inflammation and degeneration of the peripheral nerves and/or the cranial nerves resulting in impairment of the conductivity of these nerves 3.[slideshare.net]
  • Similar Codes ICD-9 Code ICD-9 Description 356.0 Hereditary peripheral neuropathy 356.1 Peroneal muscular atrophy 356.2 Hereditary sensory neuropathy 356.3 Refsum's disease 356.4 Idiopathic progressive polyneuropathy 356.8 Other specified idiopathic peripheral[healthprovidersdata.com]
  • Refsum's Disease (disorder of lipid metabolism) a) Biochemical defect: deficiency of phytanic oxidase; increased phytanic acid in plasma. b) Clinical expression: peripheral neuropathy signs, sometimes cerebellar signs. c) Therapy: low phytol diet (phytol[kobiljak.msu.edu]
  • ., Hypertrophic peripheral neuropathy (Dejerine-Sottas disease) associated with heart block. Case report presentation and review of the literature. Jpn Heart J. 1990;31:404-410.[rarediseases.org]
Cranial Neuropathy
  • The authors describe a patient with complex cranial neuropathy caused by pathologically proved hypertrophic interstitial neuropathy. Plain and contrast-enhanced MR studies were performed prior to surgical exploration.[ncbi.nlm.nih.gov]
  • Type your tag names separated by a space and hit enter Abstract The authors describe a patient with complex cranial neuropathy caused by pathologically proved hypertrophic interstitial neuropathy.[unboundmedicine.com]
  • Abstract American Journal of Neuroradiology November 1992, 13 (6) 1552-1554; Abstract The authors describe a patient with complex cranial neuropathy caused by pathologically proved hypertrophic interstitial neuropathy.[ajnr.org]
  • Since we could not document raised ICP or hydrocephalus in any of the cases, the headache possibly denotes dural inflammation. [5] Cranial neuropathies were present in all the cases.[neurologyindia.com]
Areflexia
  • The disease is characterized by an early-onset (i.e. in childhood) demyelinating neuropathy, and usually manifests as gradual progression of distal weakness, sensory loss, and areflexia in the legs.[radiopaedia.org]
  • Other symptoms may include pain in the extremities, curvature of the spine, clawed hands, foot deformities, ataxia, peripheral areflexia, and slow acquisition of motor skills in childhood.[en.wikipedia.org]
  • They showed decreased reactivity to electric stimulation, areflexia, marked distal sensory loss in all four extremities, and incoordination in the arms, Romberg’s sign, miosis, decreased pupillary reaction to light, and nystagmus.[karger.com]
Cranial Nerve Involvement
  • Cranial nerve involvement is reportedly seen in 15% of cases. Genetics It is largely inherited as an autosomal recessive condition, with occasional sporadic cases 1 .[radiopaedia.org]
  • Lower cranial nerve involvement, especially VIII and X, was most commonly observed.[neurologyindia.com]

Workup

Slow Nerve Conduction Velocities
  • Classification and Variants Dyck [ 8 ] characterised this as an autosomal recessive form: HMSN type III or Dejerine-Sottas disease: a severe, demyelinating neuropathy, presenting in infancy with delayed motor development, very slow nerve conduction velocities[karger.com]

Treatment

  • Keep your memory fresh with the current nomenclature of various types of disc herniations, listed in a separate, illustrated chapter, and get a brief overview of the major treatment options currently available for each particular disorder.[books.google.de]
  • Treatment of Guillain Barre Syndrome 19. Thank you[slideshare.net]
  • […] of benign paroxysmal positional vertigo Evidence-based guideline update: Pharmacologic treatment for episodic migraine prevention in adults Practice parameter: Evidence-based guidelines for migraine headache (an evidence-based review) Evidence-based[neurology.org]
  • The possibility that continuing allergic factors are of importance was explored by treatment with cortisone. One child exhibited encouraging evidence of improvement on this regimen.[pediatrics.aappublications.org]
  • 雑誌 Cardiovasc J S Afr 14:145-55 (2003) 文献 PMID: 11716909 著者 Franz WM, Muller OJ, Katus HA タイトル Cardiomyopathies: from genetics to the prospect of treatment.[genome.jp]

Prognosis

  • For cases with bilateral renal dysplasia, the prognosis is guarded. If renal function is preserved, the prognosis is good when early surgery is done. True prune belly syndrome seems to have a better long-term prognosis.[onlinelibrary.wiley.com]
  • […] of European and Afro‐Asian origin Michael Yablonski , Albert Behar , Henry Ungar , Joseph Resch , Milton Alter Full Text (PDF) Subdural collections of fluid in infants and children A study of 62 patients with special reference to factors influencing prognosis[neurology.org]
  • PATOLOGIA NEOPLASTICA Back 9322 NEOPLASIE A PROGNOSI FAVOREVOLE CON MODESTA COMPROMISSIONE FUNZIONALE 0 0 11 9323 NEOPLASIE A PROGNOSI FAVOREVOLE CON GRAVE COMPROMISSIONE FUNZIONALE 0 0 70 9325 NEOPLASIE A PROGNOSI INFAUSTA O PROBABILMENTE SFAVOREVOLE[studiolegaleoldrini.it]

Etiology

  • Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology.[icd10coded.com]
  • A review of the literature indicates that among chronic polyneuropathies of unknown etiology a number of different causes may lead to a common pathology, based on an increase in fibrous tissue and eventuating in hypertrophy.[pediatrics.aappublications.org]
  • Presence of granulomas or vasculitis aids in establishing a specific etiology. None of our patients agreed for a dural biopsy.[neurologyindia.com]
  • HIV associated neuropathies Late stages of HIV associated neuropathies Distal symmetrical polyneuropathy Lumbosacral polyradiculopathy Autonomic neuropathy Any stages of HIV associated neuropathies Mononeuropathies Herpes zoster radiculitis Potential etiologies[quizlet.com]
  • However, the etiology and true incidence of these malformations are not known with certainty.[onlinelibrary.wiley.com]

Pathophysiology

  • The pathophysiology of neurological disorders in childhood is based on the same principles of the organization, structure, and function of the nervous sys tem as apply to adults. Two pitfalls are present for the student, however.[books.google.com]

Prevention

  • - 0% Emergent - ED Care Needed - Preventable/Avoidable - 0% Emergent - ED Care Needed - Not Preventable/Avoidable - 0% Primary diagnosis of injury 0% Primary diagnosis of mental health problems 0% Primary diagnosis of substance abuse 0% Primary diagnosis[medicbind.com]
  • Search for this keyword Advertisement Popular on Neurology Most Read Most Cited The terrorist inside my husband's brain Self-treatment of benign paroxysmal positional vertigo Evidence-based guideline update: Pharmacologic treatment for episodic migraine prevention[neurology.org]
  • […] like HMSN Type I, but with optic atrophy and deafness Hereditary Motor Sensory Neuropathy (HMSN) Type VI An acute autoimmune demyelinating polyneuropathy Mortality is 3% to 5% This is a medical/neurological emergency that must be recognized early to prevent[quizlet.com]
  • Sonographic diagnosis of fetal urinary tract malformations has proved to be useful in the prevention of serious renal damage in children and young adults, and the diagnostic accuracy of sonography in prenatal diagnosis urinary tract malformations is constantly[onlinelibrary.wiley.com]
  • Aim of the therapy is to prevent permanent damage to neural structures. 1. Masson C, Boukriche Y, Colombani JM : Inflammatory hypertrophic cranial pachymeningitis. Presse Med 2001; 95 : 65-70. 2.[neurologyindia.com]

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