Pathologist’s conclusion Pathology findings were summarized as diffuse immune complex glomerulopathy with mild measngial hypercellularity, fibrous crescents and secondary global and segmental glomerulosclerosis, immune complex tubulointerstitial nephritis [omicsonline.org]

Patients with this condition are likely to have systemic involvement, including angioedema, arthralgias, pulmonary disease, abdominal or chest pain, fever, renal disease, and episcleritis. [diseaseinfosearch.org]

licensee BioMed Central Ltd. 2014 Received: 6 May 2014 Accepted: 28 August 2014 Published: 22 October 2014 Abstract Introduction Hypocomplementemic urticarial vasculitis syndrome is a rare disorder characterized by chronic urticarial vasculitis, arthralgia [jmedicalcasereports.biomedcentral.com]

AHA-syndrome was ruled out based on the absence of arthritis/ arthralgia, Cogan’s syndrome due to the absence of keratitis (despite hearing loss). [omicsonline.org]

Overview A rare condition characterized by the presence of recurring urticarial vasculitis, arthralgia or arthritis and hypocomplementemia. [checkorphan.org]

Urticaria and arthralgias as manifestations of necrotizing angiitis (vasculitis). J Invest Dermatol 1974;63:485-90. [ PUBMED ] 2. Soter NA. Cutaneous necrotizing vasculitis. [ijdvl.com]

From Wikidata Jump to navigation Jump to search No description defined Chronic urticaria as a manifestation of venulitis Hypocomplementemic urticarial vasculitis syndrome Hypocomplementemic vasculitis Unusual lupus-like syndrome Mac Duffie syndrome Anti-C1q [wikidata.org]

[…] common diagnosis in patients with hives –Often related to food or drug allergies, bites, or stings –25% of patients with one episode will progress to chronic urticaria * Chronic urticaria –Idiopathic in 50% of cases –Chronic idiopathic urticaria spontaneously [checkorphan.org]

Associations Hepatitis-B virus, Sjögren syndrome, systemic lupus erythematosus, myeloma, IgM gammopathy, pregnancy, cancer, solar urticaria, cold urticaria, and drugs (e.g., diltiazem). [medical-dictionary.thefreedictionary.com]

The KI challenges in the two sensitive patients precipitated urticaria, angioedema, polymyalgias, conjunctivitis, and coryza. [annals.org]

A rare autoimmune disease characterized by recurrent urticaria (nettle rash), first described in the 1970s. There is no defined paradigm for the syndrome aetiology and severity in progression. [en.wikipedia.org]

From Wikidata Jump to navigation Jump to search No description defined Chronic urticaria as a manifestation of venulitis Hypocomplementemic urticarial vasculitis syndrome Hypocomplementemic vasculitis Unusual lupus-like syndrome Mac Duffie syndrome Anti-C1q [wikidata.org]

urticaria * Chronic urticaria –Idiopathic in 50% of cases –Chronic idiopathic urticaria spontaneously resolves within 2 years in 80% of patients –Criterion for chronic urticaria is duration of more than 6 weeks * Occult infection (e.g., sinusitis, oral [checkorphan.org]

Urticarial vasculitis (also known as "chronic urticaria as a manifestation of venulitis", "hypocomplementemic urticarial vasculitis syndrome", "hypocomplementemic vasculitis" and "unusual lupus-like syndrome") is a skin condition characterized by fixed [en.wikipedia.org]

The four sensitive patients were strikingly similar in that they exhibited hypocomplementemia and dermal vasculitis associated with chronic urticaria or systemic lupus erythematosus, suggesting that other patients with similar clinical features may be [annals.org]

There was scleral erythema, urticaria on the torso, palpable purpura on the legs, and swelling and tenderness of the hand joints. A diagnostic procedure was performed. Funding and Disclosures This case was presented at the Rheumatology Grand Rounds. [nejm.org]

Physical exam Palpable purpura is pathognomonic for vasculitis. Palpable purpura consists of elevated, nonblanching erythematous lesions. [bobbybukamd.com]

Suggested Listings for Evaluation: DETERMINATION LISTING REMARKS Meets 14.02 114.02 Equals 3.02 A * Adjudicators may, at their discretion, use the Medical Evidence of Record or the listings suggested to evaluate the claim. [secure.ssa.gov]

Absence of a circulating complement activator and the low serum C3 and C5 levels suggested the presence of a solid-phase complement activator, possibly related to renal or systemic vascular endothelium. [ncbi.nlm.nih.gov]

Hypocomplementemia, negative immune profile and evidence of vasculitis on skin biopsy suggested a diagnosis of hypocomplementemic urticarial vasculitis. The patient responded to a course of steroids.(JAPI 2000; 48 : 536-537) [japi.org]

The four sensitive patients were strikingly similar in that they exhibited hypocomplementemia and dermal vasculitis associated with chronic urticaria or systemic lupus erythematosus, suggesting that other patients with similar clinical features may be [annals.org]

Further course and work-up Few days later her abdomen pain and nausea resolved, her liver enzymes normalized, creatinine decreased to 179 μmol/L, other routine labs did not changed much, but she complained recurrence of skin rush (Figure 1), eye redness [omicsonline.org]

Regenerative activity in liver biopsy. Fig. 4. Regenerative activity in liver biopsy. [academic.oup.com]

A liver biopsy was performed and showed features of chronic hepatitis with scarce fibrosis. In the meantime, liver enzyme levels returned to the normal range (ALT 22 U/L, normal 10-30, AST 28 U/L, normal 10-36). [scielo.br]