Presentation
Leading experts from Latin America, Africa, Near and Middle East, Indian Subcontinent, Far East, Oceania and Australia present their expert insights into specific conditions, as well as progress and challenges in the development of the specialty. [books.google.com]
A 51-year-old man presented with acute urinary retension. On examination urinary bladder was palpable up to the umbilicus. After catheterization a vague lump was palpable on the left side of suprapubic region. [indianjurol.com]
Entire Body System
- Anemia
[…] condition Always bilateral Symptoms occur after age 40 Kidneys are very large and studded with cysts There may be cysts in the liver, spleen, and pancreas Symptoms include microscopic or gross hematuria, flank pain, hypertension Laboratory tests may show anemia [clevelandurology.net]
There are several multi-organ syndromes associated with renal agenesis and hypoplasia: Miller-Dieker syndrome DiGeorge syndrome Brachio-oto-renal syndrome Fanconi anemia Fraser syndrome Kallmann syndrome Klinefelter syndrome Rokitansky-Küster-Hauser syndrome [clinicaladvisor.com]
As with all such disorders, complications such as growth failure, metabolic bone disease, anemia, metabolic acidosis, and other disorders of fluid and electrolyte metabolism may occur. [emedicine.medscape.com]
[…] develops over short period of time such as days or weeks; elevated creatinine, hematuria, hypertension, sepsis, severe dehydration; normal or enlarged, hydronephrosis, abnormal resistive index Develops over a longer period of time such as months or years; anemia [quizlet.com]
- Surgical Procedure
It assumes a great importance in the context of present day surgical procedures like percutaneous nephrectomy and diagnostic evaluation of the kidney donors, etc. [ 6 ]. [omicsonline.org]
Gastrointestinal
- Nausea
In their lawsuits, Plaintiffs accuse GlaxoSmithKline of promoting Zofran “off label,” for the unapproved indication of nausea and vomiting during pregnancy. [zofranlegal.com]
Cardiovascular
- Hypertension
Unilateral renal hypoplasia unlike Ask-Upmark kidney (segmental renal hypoplasia) seldom causes hypertension. A case of an infant whose hypertension disappeared after removal of a hypoplastic kidney is reported. [ncbi.nlm.nih.gov]
Local pain, hypertension and urinary tract infections are common manifestations in renal hypoplasia. Blood pressure may be normalized after nephrectomy. Hypertension seems to be the most dangerous feature. [link.springer.com]
[…] congénitale Malformation Rein pathologie Afrique Keyword (en) Congenital Case study Human Hypertension Segmental hypoplasia Nephrectomy Pathogenesis Kidney Symptomatology Treatment Morocco Cardiovascular disease Urinary system disease Surgery Congenital [pascal-francis.inist.fr]
Portal hypertension may be treated by portacaval or splenorenal shunts, which reduce morbidity but not mortality. [merckmanuals.com]
The early history of hypertension is not a story of progressive achievement. [books.google.de]
Urogenital
- Kidney Failure
It is very rare for a baby to be born with kidney failure. Occasionally, a young baby or child has kidney failure. [infokid.org.uk]
Kidney failure Most people with ARPKD will eventually develop kidney failure at some point in their life. [nhs.uk]
Signs in babies are kidney failure and breathing problems. Signs in children older than 1 year are high blood pressure or enlarged kidneys. [urologyhealth.org]
Over time, if these problems are not corrected, they can damage the one working kidney and lead to total kidney failure. [medicinenet.com]
Since most cases of UPJ obstruction are corrected early in life, it rarely progress to kidney failure. [nationwidechildrens.org]
- Renal Insufficiency
Abstract A case of renal cortical hypoplasia in a Cocker Spaniel bitch is presented. The dog, under clinical observation between the ages of 15 to 26 months, was found to have advancing chronic renal insufficiency. [ncbi.nlm.nih.gov]
Epidemiology of Renal Hypoplasia 2.5% is the risk for unilateral renal hypoplasia. Signs and Symptoms of Renal Hypoplasia Unilateral renal hypoplasia causes no symptoms. Bilateral renal hypoplasia can be the cause of renal insufficiency. [urology-textbook.com]
For those with advanced renal insufficiency (chronic kidney disease [CKD] Stage 3 or 4) PTH, Vit D 25 and Vit D 1,25 would also be included. [renalandurologynews.com]
Many neonates die in the first few days or weeks of life from pulmonary insufficiency. Most who survive develop progressive renal failure often requiring renal replacement therapy. [merckmanuals.com]
Workup
Topics include: Non-neoplastic diseases in kidney cancer; Nephrectomy for non-neoplastic causes; Autopsy renal pathology; Practical approach to kidney donation workup; Kidney allograft pathology; Renal infections; Amyloidosis - all subtypes; Histologic [books.google.com]
The thrombophilic workup was negative. Patients were treated with conservative therapy: low molecular weight heparin anticoagulants converted later to oral anticoagulant with resolution of symptoms and disappearance of the thrombus. [actamedicamarisiensis.ro]
X-Ray
- Small Kidney
[…] re·nal hy·po·pla·si·a an abnormally small kidney that is morphologically normal but has either a reduced number of nephrons or smaller nephrons. re·nal hy·po·pla·si·a ( rē'năl hī'pō-plā'zē-ă ) An abnormally small kidney that is morphologically normal [medical-dictionary.thefreedictionary.com]
Renal hypoplasia refers to a congenitally small kidney where there is essentially normal residual parenchyma but smaller calyces, lobules and papillae. [radiopaedia.org]
You are here: Urology Textbook > Kidneys > Congenital renal hypoplasia Definition of Renal Hypoplasia Renal hypoplasia is a congenital small kidney with diminished renal function, which has a normal tissue architecture. [urology-textbook.com]
In many cases, the small kidney also shows signs of dysplasia on ultrasound, leading to the diagnosis of renal hypodysplasia. [oxfordmedicine.com]
Treatment
Treatment In most cases, there is no treatment needed before birth. Options Very rarely, there is concern that the problems with the baby’s kidneys and/or lungs are very severe, and may mean that he or she will not be able to live a normal life. [infokid.org.uk]
271 Prognosis 278 References 281 Anomalies of the Male Genitalia By RoBERT J PRENTIss With 15 Figures 287 Method of Examination 288 Surgical Treatment 289 Surgical Principles 292 [books.google.com]
[…] chronic kidney disease (CKD) and kidney failure Treatments for these common problems are described below. [nhs.uk]
Prognosis
Diagnosis 256 Double Urethra and Accessory Urethra 257 Incomplete Dorsal Accessory Urethrablind 258 Incomplete Dorsal Accessory UrethraCommunicating with the Urethra 259 Etiology and Pathology 261 Clinical Presentation 268 Diagnosis 270 Treatment 271 Prognosis [books.google.com]
Prognosis is directly related to the presence and severity of chronic kidney disease. [clinicaladvisor.com]
Management Prenatally and following birth, resuscitation decisions should be discussed with the family and based on the child's prognosis. [patient.info]
[…] decompression or excision of cysts do not improve renal function There is no higher incidence of renal cell carcinoma in these patients 50% of the children of affected adults will have the disease When the disease affects children, it has a very poor prognosis [clevelandurology.net]
What is my baby's long-term prognosis? A baby with unilateral MCDK with no other birth defects has a normal life expectancy. For a child with only one kidney that works, that kidney may be a little bigger than normal. [chw.org]
Etiology
[…] and Pathology 254 Clinical Presentation and Diagnosis 256 Double Urethra and Accessory Urethra 257 Incomplete Dorsal Accessory Urethrablind 258 Incomplete Dorsal Accessory UrethraCommunicating with the Urethra 259 Etiology and Pathology 261 Clinical [books.google.com]
Hypothyroidism, usually of autoimmune etiology and only occasionally of nonautoimmune etiology, has been reported to be associated with dRTA. [thetrp.net]
Review paper about unilateral renal agenesis Ongoing controversies regarding etiology, diagnosis, treatment Long-term follow-up studies of patients with renal hypoplasia/dysplasia/agenesis are needed to provide insight into prognostic factors identified [clinicaladvisor.com]
Google Scholar Gleason, P.E., Kelalis, P.P., Husmann, D.A. et al. (1994) Hydronephrosis in renal ectopia: Incidence, etiology and significance. J. Urol. 151, 1660–1661. PubMed Google Scholar Gray, S.W., Skandalakis, J.E. [link.springer.com]
Epidemiology
Epidemiology of Renal Hypoplasia 2.5% is the risk for unilateral renal hypoplasia. Signs and Symptoms of Renal Hypoplasia Unilateral renal hypoplasia causes no symptoms. Bilateral renal hypoplasia can be the cause of renal insufficiency. [urology-textbook.com]
[…] kidney、renal dysplasia)」「腎低形成(hypoplastic kidney、renal hypoplasia)」「腎無形成(renal agenesis)」「逆流性腎症(reflux nephropathy)」「水腎症(hydronephrosis)」「膀胱尿管逆流(vesicoureteric reflux)」「腎盂尿管移行部狭窄(pelviureteric junction obstruction)」「後部尿道弁(posterior urethral valves)」「疫学(epidemiology [natureasia.com]
Epidemiology Frequency United States Exact frequency of oligomeganephronia is difficult to determine. [emedicine.medscape.com]
Epidemiology Incidence BRA is thought to occur in 1 in 5,000 births whilst unilateral renal agenesis (URA) is more common and occurs in about 1 in 1,000. [ 4 ] An Italian study showed a 5:2 male:female ratio. [ 5 ] Potter's original series similarly showed [patient.info]
Pathophysiology
Written by leading pathologists, this second edition presents an up-to-date, concise presentation of major pathological, clinical, pathophysiological, and genetic information for over 240 diagnoses. [books.google.com]
Pathophysiology Oligomeganephronia results from arrested development of the metanephric blastema at 14-20 weeks' gestation, with subsequent hypertrophy of glomeruli and tubules in the kidney. [emedicine.medscape.com]
CrossRef PubMed Google Scholar Koff, S.A. (1990) Pathophysiology of ureteropelvic junction obstructions. Urol. Clin. North. Am. 17, 263–272. [link.springer.com]
View Article PubMed PubMed Central Google Scholar Hoyer JR, Seiler MW: Pathophysiology of Tamm-Horsfall protein. Kidney Int. 1979, 16: 279-289. 10.1038/ki.1979.130. [bmcnephrol.biomedcentral.com]
Prevention
Some types of VUR may be treated with antibiotics to prevent infections, while others may require surgery to prevent the backflow of urine to occur. [nationwidechildrens.org]
Treatment is focused on preventing progression to stage 5, end-stage renal disease. [clinicaladvisor.com]
[…] urogenital anomalies, tongue cysts, limb shortness, eye abnormalities, defects of the heart, gallbladder agenesis, and ear malformations. 1953) observed that maternal vitamin A deficiency resulted in renal hypoplasia in rats which was reported to have been prevented [medical-dictionary.thefreedictionary.com]
OUTCOME Aggressive medical and surgical intervention should be able to prevent or treat most complications of these abnormalities. [chargesyndrome.org]
Is chronic lung disease in low birth weight infants preventable? A survey of eight centers. Página 84 - Tanner JM, Whitehouse RH, Marubini E, Resele LF. The adolescent growth spurt of boys and girls of the Harpenden growth study. [books.google.es]