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Hypoplastic Kidney

Renal Hypoplasia


Presentation

  • The early detection of hemochromatosis in the presented case may delay organ damage and failure due to iron overload.[ncbi.nlm.nih.gov]
  • CASE PRESENTATION: We report a novel phenotype, with the typical features of hyperuricemia and renal deterioration, but with the additional unexpected feature of unilateral renal hypoplasia.[ncbi.nlm.nih.gov]
  • To report a case of 18-year-old girl presented with urinary leakage occurring between normal voids that at 11-year-old was found to have, at cistoscopy and vaginoscopy, an left ureteral ectopy into the vagina with a non demonstrable corresponding kidney[ncbi.nlm.nih.gov]
  • […] and Diagnosis 256 Double Urethra and Accessory Urethra 257 Incomplete Dorsal Accessory Urethrablind 258 Incomplete Dorsal Accessory UrethraCommunicating with the Urethra 259 Etiology and Pathology 261 Clinical Presentation 268 Diagnosis 270 Treatment[books.google.com]
  • Written by leading pathologists, this second edition presents an up-to-date, concise presentation of major pathological, clinical, pathophysiological, and genetic information for over 240 diagnoses.[books.google.com]
Low Set Ears
  • Babies with bilateral renal agenesis will have a number of unique characteristics: dry loose skin, wide-set eyes, prominent folds at the inner corner of each eye, sharp nose, and large low-set ears with lack of ear cartilage.[health.state.mn.us]
Frontal Bossing
  • Facial features were mildly dysmorphic with frontal bossing, sharply depressed nasal bridge, prominent nasal tip, short philtrum and downturned mouth. Right ear lobule was large. There were bilateral single to bridged palmar creases.[ashg.org]
Incontinence
  • Abstract Ureteral ectopy into the vagina is a cause of pseudo-incontinence. When the corresponding kidney has a good function, the treatment of choice is the ureter reimplantation, otherwise the alternative is partial or total nephrectomy.[ncbi.nlm.nih.gov]
  • PubMed Google Scholar Freedman, E.R., Rickwood, A.M.K. (1994) Urinary incontinence due to unilateral vaginally ectopic single ureter. Br. J. Urol. 73, 716–717.[link.springer.com]

Workup

  • Topics include: Non-neoplastic diseases in kidney cancer; Nephrectomy for non-neoplastic causes; Autopsy renal pathology; Practical approach to kidney donation workup; Kidney allograft pathology; Renal infections; Amyloidosis - all subtypes; Histologic[books.google.com]
  • The thrombophilic workup was negative. Patients were treated with conservative therapy: low molecular weight heparin anticoagulants converted later to oral anticoagulant with resolution of symptoms and disappearance of the thrombus.[actamedicamarisiensis.ro]
Small Kidney
  • Renal hypoplasia refers to a congenitally small kidney where there is essentially normal residual parenchyma but smaller calyces, lobules and papillae.[radiopaedia.org]
  • You are here: Urology Textbook Kidneys Congenital renal hypoplasia Definition of Renal Hypoplasia Renal hypoplasia is a congenital small kidney with diminished renal function, which has a normal tissue architecture.[urology-textbook.com]
  • In many cases, the small kidney also shows signs of dysplasia on ultrasound, leading to the diagnosis of renal hypodysplasia.[oxfordmedicine.com]
  • The patient’s maternal aunt was also in established renal failure and in addition to one small kidney on ultrasound suffered with gout.[bmcnephrol.biomedcentral.com]

Treatment

  • When the corresponding kidney has a good function, the treatment of choice is the ureter reimplantation, otherwise the alternative is partial or total nephrectomy.[ncbi.nlm.nih.gov]
  • Positive PET scan areas should be biopsied to confirm the presence of metastatic disease before excluding patients from surgical treatment.[ncbi.nlm.nih.gov]
  • 271 Prognosis 278 References 281 Anomalies of the Male Genitalia By RoBERT J PRENTIss With 15 Figures 287 Method of Examination 288 Surgical Treatment 289 Surgical Principles 292[books.google.com]
  • Prepare for clinical challenges and save time in addressing them thanks to expert advice on treatment options from international contributors.[books.google.com]

Prognosis

  • Diagnosis 256 Double Urethra and Accessory Urethra 257 Incomplete Dorsal Accessory Urethrablind 258 Incomplete Dorsal Accessory UrethraCommunicating with the Urethra 259 Etiology and Pathology 261 Clinical Presentation 268 Diagnosis 270 Treatment 271 Prognosis[books.google.com]
  • Prognosis is directly related to the presence and severity of chronic kidney disease.[clinicaladvisor.com]
  • […] decompression or excision of cysts do not improve renal function There is no higher incidence of renal cell carcinoma in these patients 50% of the children of affected adults will have the disease When the disease affects children, it has a very poor prognosis[clevelandurology.net]
  • What is my baby's long-term prognosis? A baby with unilateral MCDK with no other birth defects has a normal life expectancy. For a child with only one kidney that works, that kidney may be a little bigger than normal.[chw.org]

Etiology

  • […] and Pathology 254 Clinical Presentation and Diagnosis 256 Double Urethra and Accessory Urethra 257 Incomplete Dorsal Accessory Urethrablind 258 Incomplete Dorsal Accessory UrethraCommunicating with the Urethra 259 Etiology and Pathology 261 Clinical[books.google.com]
  • Review paper about unilateral renal agenesis Ongoing controversies regarding etiology, diagnosis, treatment Long-term follow-up studies of patients with renal hypoplasia/dysplasia/agenesis are needed to provide insight into prognostic factors identified[clinicaladvisor.com]
  • ., Husmann, D.A. et al. (1994) Hydronephrosis in renal ectopia: Incidence, etiology and significance. J. Urol. 151, 1660–1661. PubMed Google Scholar Gray, S.W., Skandalakis, J.E. (eds) (1972) Embriology for Surgeons .[link.springer.com]

Epidemiology

  • Epidemiology of Renal Hypoplasia 2.5% is the risk for unilateral renal hypoplasia. Signs and Symptoms of Renal Hypoplasia Unilateral renal hypoplasia causes no symptoms. Bilateral renal hypoplasia can be the cause of renal insufficiency.[urology-textbook.com]
  • […] kidney、renal dysplasia)」「腎低形成(hypoplastic kidney、renal hypoplasia)」「腎無形成(renal agenesis)」「逆流性腎症(reflux nephropathy)」「水腎症(hydronephrosis)」「膀胱尿管逆流(vesicoureteric reflux)」「腎盂尿管移行部狭窄(pelviureteric junction obstruction)」「後部尿道弁(posterior urethral valves)」「疫学(epidemiology[natureasia.com]
  • Epidemiology Frequency United States Exact frequency of oligomeganephronia is difficult to determine.[emedicine.medscape.com]
Sex distribution
Age distribution

Pathophysiology

  • Written by leading pathologists, this second edition presents an up-to-date, concise presentation of major pathological, clinical, pathophysiological, and genetic information for over 240 diagnoses.[books.google.com]
  • Brenner/Rector remains the go-to resource for practicing and training nephrologists and internists who wish to master basic science, pathophysiology, and clinical best practices.[books.google.com]
  • View Article PubMed PubMed Central Google Scholar Hoyer JR, Seiler MW: Pathophysiology of Tamm-Horsfall protein. Kidney Int. 1979, 16: 279-289. 10.1038/ki.1979.130.[bmcnephrol.biomedcentral.com]
  • CrossRef PubMed Google Scholar Koff, S.A. (1990) Pathophysiology of ureteropelvic junction obstructions. Urol. Clin. North. Am. 17, 263–272.[link.springer.com]
  • Pathophysiology Oligomeganephronia results from arrested development of the metanephric blastema at 14-20 weeks' gestation, with subsequent hypertrophy of glomeruli and tubules in the kidney.[emedicine.medscape.com]

Prevention

  • Treatment is focused on preventing progression to stage 5, end-stage renal disease.[clinicaladvisor.com]
  • Some types of VUR may be treated with antibiotics to prevent infections, while others may require surgery to prevent the backflow of urine to occur.[nationwidechildrens.org]
  • Is chronic lung disease in low birth weight infants preventable? A survey of eight centers. ‎ Página 84 - Tanner JM, Whitehouse RH, Marubini E, Resele LF. The adolescent growth spurt of boys and girls of the Harpenden growth study. ‎[books.google.es]
  • OUTCOME Aggressive medical and surgical intervention should be able to prevent or treat most complications of these abnormalities.[chargesyndrome.org]
  • They may also be given a type of medication called a surfactant, which helps prevent tiny air sacs inside the lungs known as alveoli collapsing. The more working alveoli your baby has, the better their ability to breathe.[nhs.uk]

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