Presentation
The present assessment may be a valuable algorithm to validly quantify CC in PD. Parkinson-Kongress 2015 Berlin. To cite this abstract in AMA style: T. Schmidt, G. Ebersbach, G. Doreen. [mdsabstracts.org]
Get a quick and memorable overview of anatomy, pathophysiology, and clinical presentation from the precision and beauty of Netter and Netter-style plates that highlight key neuroanatomical and neurologic concepts. [books.google.com]
Methods: A 42-year-old male, presented with dystonia of 5-year duration, that initially started with cervical dystonia and later progressed to severe disturbance of posture causing involuntary truncal flexion induced by standing or sitting. [neurologyindia.com]
Here we present 11 patients from 8 families with a late-onset axial myopathy associated with RYR1 variants. [kclpure.kcl.ac.uk]
Entire Body System
-
Military Personnel
[…] pain and abnormal curvature of the spine were caused by a vertebral destructive process, perhaps he never named this entity. 1–3 The term camptocormia was first used by Souques and Rosanoff-Saloff (cyphose hystérique, 1915) to describe bent spine in military [elsevier.es]
-
Episodic Weakness
Weakness 464 Case 73B An African American Man with Hyperthyroidism and Acute Paralysis 470 Case 74 A Boy with Large Muscles Leg Pain and Elevated Serum Creatine Kinase 472 Case 75 A Woman with Proximal Muscle Weakness Calf Hypertrophy Heel Contractures [books.google.de]
-
Difficulty Walking
Walking and Ataxia 415 Case 66 A Man with Progressive Neuropathy and Congestive Heart Failure 422 Case 67 An Elderly Woman with a Progressive Neuropathy 429 Case 68 A Young Woman with Difficulty Swallowing 433 Case 69 A Young Woman with Intermittent [books.google.de]
Musculoskeletal
-
Leg Pain
[…] with Proximal Weakness 448 Case 72 A Young Woman with Distal Upper Extremity Weakness 454 Case 73A A Young Man with Episodic Weakness 464 Case 73B An African American Man with Hyperthyroidism and Acute Paralysis 470 Case 74 A Boy with Large Muscles Leg [books.google.de]
-
Calf Hypertrophy
Hypertrophy Heel Contractures and Elevated Serum Creatine Kinase 480 Case 76 A Young Man with Distal Leg Wasting and Normal Sensation 484 Case 77 A Woman with Droopy Eyelids and Difficulty Swallowing 493 Case 78 A Man with Facial and Shoulder Muscle [books.google.de]
Eyes
-
Kayser-Fleischer Ring
The workup for secondary dystonia including slit lamp examination for Kayser-Fleischer ring and serum copper studies did not reveal any abnormality. Magnetic resonance imaging of the brain was unremarkable. [neurologyindia.com]
Psychiatrical
-
Hysteria
Conversion reaction, psychogenic Dissociative convulsions Dissociative disorder with mixed symtom presentation Globus hystericus Hysterical ataxia Hysterical blindness Psychologic conversion disorder Applies To Astasia-abasia, hysterical Conversion hysteria [icd9data.com]
[…] by a vertebral destructive process, perhaps he never named this entity. 1–3 The term camptocormia was first used by Souques and Rosanoff-Saloff (cyphose hystérique, 1915) to describe bent spine in military personnel (“bent back of soldiers” or “war hysteria [elsevier.es]
In our case, a possibility of disorders attributed to hysteria, malingering, or other psychiatric diagnosis were all excluded. [surgicalneurologyint.com]
-
Anger
He also had improvement in anxiety, anger outbursts, and had significant weight gain. » Conclusion In this case report, the first from India, we have shown the efficacy of GPi DBS in the treatment of drug refractory dystonia associated camptocormia. [neurologyindia.com]
Urogenital
-
Dark Urine
[…] and Later Contractures 503 Case 80 A Woman with Longstanding Weakness and Foot Deformities 510 Case 81 A Woman with Droopy Eyelids and Ophthalmoplegia 515 Case 82 A Man with Weakness and Swelling in the Neck 522 Case 83 A Woman with Muscle Pains and Dark [books.google.de]
Neurologic
-
Unable to Walk
The first patient, a 26-year-old woman, suffered for 3 years from such severe camptocormia that she became unable to walk and was confined to bed or a wheelchair. [semanticscholar.org]
In severe cases, patients with camptocormia are unable to walk. [foundationdystoniaresearch.org]
-
Foot Drop
Case 58A A Woman with Leg Numbness Pain Weakness and Slow Nerve Conduction Velocities 372 Case 58B A Boy with Leg Weakness 375 Case 59 A Man with Hand Weakness and Numbness After Skiing 383 Case 60 A Man with Recurrent Foot Drop 386 Case 61 An Elderly [books.google.de]
-
Areflexia
67 An Elderly Woman with a Progressive Neuropathy 429 Case 68 A Young Woman with Difficulty Swallowing 433 Case 69 A Young Woman with Intermittent Weakness and a Positive Family History of Similar Problems 436 Case 70 A Woman with Muscle Weakness and Areflexia [books.google.de]
Workup
The workup for secondary dystonia including slit lamp examination for Kayser-Fleischer ring and serum copper studies did not reveal any abnormality. Magnetic resonance imaging of the brain was unremarkable. [neurologyindia.com]
(See Workup.) Table 4. [emedicine.medscape.com]
Other Test Results
-
Slow Nerve Conduction Velocities
Case 58A A Woman with Leg Numbness Pain Weakness and Slow Nerve Conduction Velocities 372 Case 58B A Boy with Leg Weakness 375 Case 59 A Man with Hand Weakness and Numbness After Skiing 383 Case 60 A Man with Recurrent Foot Drop 386 Case 61 An Elderly [books.google.de]
Treatment
Every entry features description, etiology, epidemiology, pathogenesis, risk factors, clinical features, natural history, diagnosis, red flags, treatment, prognosis, helpful hints, and suggested readings on two facing pages for easy access to key information [books.google.com]
Although DBS has been effective in the treatment of movement disorders and is rapidly being explored for the treatment of other neurologic disorders, the scientific understanding of its mechanism(s) of action remains unclear. [elsevier.es]
Conclusions: In this report, we have shown the efficacy of GPi DBS in the treatment of drug refractory dystonia associated camptocormia. [neurologyindia.com]
Prognosis
Every entry features description, etiology, epidemiology, pathogenesis, risk factors, clinical features, natural history, diagnosis, red flags, treatment, prognosis, helpful hints, and suggested readings on two facing pages for easy access to key information [books.google.com]
Prognosis - Camptocormism Not supplied. Treatment - Camptocormism Treatment of secondary forms of BSS is dependent upon the cause. Resources - Camptocormism [checkorphan.org]
Treatment and prognosis [ edit ] Treatment and management [ edit ] Thymatron IV used for electroconvulsive therapy Due to the wide range of causes of camptocormia, there is no one treatment that suits all patients. [en.wikipedia.org]
Associated monoclonal gammopathy carries an unfavorable prognosis [ 4 ]. The idiopathic form of SLONM typically presents after age 40 and evolves subacutely [ 4 ]. Limb-girdle weakness and atrophy are the main symptoms. [em-consulte.com]
Prognosis Patients with MSA have a poor prognosis. The disease progresses rapidly. Median survivals of 6.2-9.5 years from the onset of first symptoms have been reported since the late 20th century. [emedicine.medscape.com]
Etiology
Every entry features description, etiology, epidemiology, pathogenesis, risk factors, clinical features, natural history, diagnosis, red flags, treatment, prognosis, helpful hints, and suggested readings on two facing pages for easy access to key information [books.google.com]
This study aims to eludicate the etiology of PD-associated CC and HD via a multidisciplinary approach (clinical examination, electromyography, MRI, genetic analysis, muscle morphology) centering on the histology of the paraspinal muscles. [ncbi.nlm.nih.gov]
Presentation, etiology, diagnosis, and management of camptocormia. Eur Neurol 2010;64:1-8. 2. Umemura A, Oka Y, Ohkita K, Yamawaki T, Yamada K. Effect of subthalamic deep brain stimulation on postural abnormality in Parkinson disease. [neurologyindia.com]
Epidemiology
Every entry features description, etiology, epidemiology, pathogenesis, risk factors, clinical features, natural history, diagnosis, red flags, treatment, prognosis, helpful hints, and suggested readings on two facing pages for easy access to key information [books.google.com]
Ataxia, Antibody & Biopsy, Patient Info "Bent Spine" Syndrome 2 Luke 13:11 - And behold, there was a woman who had a spirit of infirmity eighteen years, and was bent over and could in no way raise herself up Etiology: Family history positive in up to 50% Epidemiology [neuromuscular.wustl.edu]
Epidemiology The lack of consistent diagnostic criteria could explain small number of epidemiological studies regarding prevalence of PS in PD patients. [dovepress.com]
Epidemiology Among the 16 patients with camptocormia that have been described by Azher & Jankovic 2005, the most frequent etiology is PD. The reported prevalence of camptocormia in PD varies widely. [intechopen.com]
Camptocormia in Parkinson disease: an epidemiological and clinical study. J. Neurol. Neurosurg. Psychiatry 2009; 80: 145–148. Tolosa E., Compta Y. Dystonia in Parkinson’s disease. J. Neurol. 2006; 253(Suppl.): 7–13. [annaly-nevrologii.com]
Pathophysiology
Get a quick and memorable overview of anatomy, pathophysiology, and clinical presentation from the precision and beauty of Netter and Netter-style plates that highlight key neuroanatomical and neurologic concepts. [books.google.com]
Pathophysiology The pathophysiological mechanisms underlying PS in PD patients have not been fully explained. [dovepress.com]
The pathophysiology of camptocormia is as heterogenous as the causes of underlying diseases are, but recent work has provided some insights into the pathophysiology of PD-associated camptocormia and opened options for treatement. [frontiersin.org]
Katz et al has proposed an important role for mechanical factors in the evolution of head drop. 2 A similar pathophysiology may cause camptocormia in IBM. [jnnp.bmj.com]
PATHOPHYSIOLOGICAL CONCEPTS The pathophysiological concepts for camptocormia are as heterogenous as the causes of the syndrome. [content.iospress.com]
Prevention
Prevention - Camptocormism Not supplied. Diagnosis - Camptocormism Diagnosis of axial myopathy is based upon CT/MRI scans demonstrating a lot of fatty infiltration of paravertebral muscles. [checkorphan.org]
As kyphosis can eventually lead to disastrous consequences, a preventive treatment like SpineCor , which simultaneously addresses the neurological, muscular and skeletal aspects of the affliction can be of benefit to the patient. [cliniquespinecor.ca]
The treatment includes symptomatic treatment for back pain, treatment of osteoporosis in elderly to prevent osteoporotic vertebral fractures. [boneandspine.com]
Postural orientation and equilibrium: what do we need to know about neural control of balance to prevent falls? Age Ageing. 2006;35(Suppl 2):ii7–ii11. 49. Vitale C, Falco F, Trojano L, et al. [dovepress.com]