Comparing clinical features of patients presenting with 'typical' features, to those with 'atypical' findings, the second group presented psychomotor delay before status epilepticus. [readbyqxmd.com]

Cerebral venous thrombosis (CVT) most often has a subacute presentation; however, a minority of patients present with thunderclap headache. [neupsykey.com]

We present a 47-year-old patient treated with phenytoin, lamotrigine and clobazam for 7years. He presented with hepatic ... 115 Autoimmunity, seizures, and status epilepticus. [biomedsearch.com]

Niger: A retrospective case series. ( 30890411 ) 2019 2 Hemiconvulsion-hemiplegia-epilepsy syndrome in a child with pre-existing cerebral pathology. ( 28652222 ) Ponnusamy A....Nv Moosa A. 2017 3 Hemiconvulsion-Hemiplegia-Epilepsy Syndrome in a Girl Presented [malacards.org]

He presented left temporal lobe epilepsy with sei-zures presenting as oral automatisms preceding right armclonic jerks. [docslide.com.br]

• Epilepsy

  1 Hemiconvulsion-hemiplegia-epilepsy syndrome in Niger: A retrospective case series. ( 30890411 ) 2019 2 Hemiconvulsion-hemiplegia-epilepsy syndrome in a child with pre-existing cerebral pathology. ( 28652222 ) Ponnusamy A....Nv Moosa A. 2017 3 Hemiconvulsion-Hemiplegia-Epilepsy [malacards.org]

  Sentences Mobile Notably, the influence of various precipitants varies with the epilepsy syndrome. Classification of epilepsies and particularly of epilepsy syndromes will change with advances in research. [eng.ichacha.net]

  Epilepsy with centrotemporal spikes “Rolandic epilepsy” versus “benign childhood epilepsy with centrotemporal spikes (BECTS)” 2.1. Definition In 1958, Beaussart was the first to recognize benign focal epilepsies. [intechopen.com]

• Inflammation

  Several factors might contribute to the pathogenesis of HH/HHE syndrome: 1. prolonged febrile seizure in which inflammation may worsen the level of cell injury; 2. inflammation and prolonged ictal activity that act on blood-brain-barrier permeability; [ncbi.nlm.nih.gov]

  We therefore propose to group these conditions under the concept of acute encephalopathy with inflammation-mediated status epilepticus. [plu.mx]

  The role of inflammation is hypoth-esized with a vicious circle involving inflammationand seizure activity facilitated by brainmaturationputting them under the concept of acute enceph-alopathy with inflammation-mediated status epi-lepticus.KEY WORDS: [documents.tips]

  […] the pathogenesis of HH/HHE syndrome 1 : prolonged seizure of long duration (possibly unnoticed) impairing metabolism of neuronal cells and leading to excitotoxic cell damage prolonged febrile seizure with an aggravation of cell injury by co-existent inflammation [radiopaedia.org]

  Postnatal inflammation increases seizure susceptibility in adults rats // J. Neurosci. — 2008. — 28. — 6904-13. Wang S., Cheng Q., Malik S., Yang J. [inj.zaslavsky.com.ua]

• Swelling

  Neuroradiological studies showed unilateral edematous swelling of the epileptic hemisphere at the time of initial status epilepticus (SE). [ncbi.nlm.nih.gov]

  Head CT on the sixth day of admission indicated that hemispheric swelling had stabilized, and repeat MRI/MRS on day 8 was essentially unchanged. [frontiersin.org]

  […] indicate that there is arelationship between a sequence of events includingearly repetitive seizures, brain edema, cortical andsubcortical atrophy, and chronic epilepsy in many ofthe cases.4 It is clear from pathologic examinationsthat the hemispheric swelling [myslide.es]

  […] first year of life.19 As previouslyreported, the left hemisphere was more frequently affectedthan the right,20 but the small number of cases does notpermit identification of any difference in age of occurrenceaccording to the side.Extension of brain swelling [docslide.com.br]

  HHS is characterized by prolonged (in hours), unilateral, clonic convulsions that can be missed initially. [3] The earliest changes in the brain occurs at the time of status epilepticus, which can be appreciated as a unilateral hemispheric swelling that [neurologyindia.com]

• Sepsis

  […] effects: concentric visual field deficits, irritability, insomnia, hypotonia Follow with ERG ACTH 75 U/m 2 IM bid x2wks, then taper 50-90% response by 7-10 days Especially if cryptogenic Adverse effects: irritability, cerebral atrophy, hypertension, sepsis [emilytam.com]

• Fatigue

  Gitelman's Syndrome Jane's diagnosis with Gitelman's Syndrome came after symptoms of fatigue, and a lowered immunity to common viruses. [rarevoices.org.au]

• Vomiting

  Some mothers will find their children retching or even vomiting in bed, if seizures start during night sleep, though most of the kids will wake up complaining of nausea and tendency to vomit. [intechopen.com]

  Vaccination, Valproate, Sodium (Divalproex Sodium, Depakote[registered])Valproic Acid (VPA, Depakene[registered])Valpromide (Amide of Valproic Acid) (Depamide[registered])Versive (S)Vertiginous (S)Vestibulogenic (5)Vigabratin (Sabrilo)Violence, Visual (S)Vomiting [buffalolib.org]

  Early-onset benign childhood occipital epilepsy (Panayiotopoulos type) Half as frequent as BECTS, excellent prognosis Age 1-14 years (typical 5 years) Seizure-types: Autonomic/behavioral disturbances with vomiting, gaze deviation, impaired consciousness [emilytam.com]

  Reversible posterior leukoencephalopathy syndrome is a clinico-radiological syndrome characterized by headache, vomiting, seizures, and visual disturbances along with the radiological findings of posterior leukoencephalopathy. [biomedsearch.com]

• Nausea

  Two-thirds of seizures occur during sleep, including daytime naps, and they usually begin with emetic symptoms (nausea, retching with or without vomiting). [intechopen.com]

  The first symptoms I started experiencing were severe headaches that lead to me suffering nausea each day. [rarevoices.org.au]

  Autonomic seizures with nausea And emesis predominate in BCEOS-1 (21). Focal-onset seizures are also prominent in BFNS, BFNIS, FFEVF, HHE, RS, and IPOLE (19,20,26,32—34). [aibolita.com]

• Muscle Weakness

  weakness, hypertrophic cardiomyopathy, dementia, deafness, multiple lipomata, short stature Pathological features: Ragged-red fibers Lesions of dentate and inferior olives Degeneration of cerebellum, brainstem, and spinal cord Astrocytosis, demyelination [emilytam.com]

• Encephalopathy

  The acute encephalopathies of obscure origin in infants and children. Brain. 1961 Dec;84:680–708. [rarediseases.org]

  Early myoclonic encephalopathy Early-onset epileptic encephalopathy and intellectual disability due to GRIN2A mutation Epilepsy syndrome Epilepsy with myoclonic absences Epilepsy-telangiectasia syndrome Epileptic encephalopathy with global cerebral demyelination [se-atlas.de]

  […] syndrome Dravet syndrome Lennox-Gastaut syndrome Landau-Kleffner syndrome Epilepsy with continuous spikes and waves during slow-wave sleep Myoclonic encephalopathy in non-progressive disorders Atypical benign partial epilepsy of childhood Hypothalamic [ci.nii.ac.jp]

  PCDH19 gene-related epilepsy shares several clinical features with other early-onset epileptic encephalopathies, such as FIRES ( febrile infection related epilepsy syndrome ) Lennox-Gastaut syndrome or epilepsy of unknown origin. [eng.ichacha.net]

• Febrile Seizures

  […] rate No effective management Febrile seizures Simple febrile seizures Lasts Not recurring within 24 hrs No post-ictal neuro deficits Complex febrile seizures Lasts >15 minutes Recurrent within 24 hrs Focal seizure Todd’s paresis Epidemiology Most commonly [emilytam.com]

  […] syndromes in infancy Febrile seizures Epilepsy with febrile seizures plus Benign infantile seizures Myoclonic epilepsy in infancy 10 - Epileptic encephalopathies in infancy and early childhood West syndrome Dravet syndrome Lennox-Gastaut syndrome Landau-Kleffner [ci.nii.ac.jp]

  […] complex febrile seizures. [molgen.vib-ua.be]

  Seizure semiology was defined according to the International League Against Epilepsy classification. [22] Febrile seizure was defined as a seizure occurring in childhood between 1 month and 5 years of age, associated with a febrile illness not caused [annalsofian.org]

• Convulsions

  Clinical manifestations Sudden unilateral clonic convulsions that last for hours or days if not appropriately treated. Consciousness may be intact. [epilepsy.com]

  At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. [link.springer.com]

  Abstract Hemiconvulsion-Hemiplegia (HH) syndrome is an uncommon consequence of prolonged focal febrile convulsive seizures in infancy and early childhood. [ncbi.nlm.nih.gov]

  Radiology and Imaging, Kasturba Medical College Manipal, Udupi, Karnataka, India Correspondence to Dr Ramesh Y Bhat, docrameshbhat{at}yahoo.co.in Summary Hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome involves initial sudden and prolonged unilateral convulsive [casereports.bmj.com]

  Gitiaux, Francis Brunelle, Olivier Dulac, Nathalie Boddaert, Rima Nabbout Developmental Medicine and Child Neurology 2013, 55 (12): 1150-8 23924283 AIM: Hemiconvulsion-hemiplegia syndrome (HHS) is a rare severe epilepsy of infancy consisting of unilateral convulsive [readbyqxmd.com]

• Aphasia

  The face is always involved and aphasia is present if the dominant side is affected. These signs distinguish acquired post-convulsive from congenital hemiplegia. Diagnostic procedures Should include CSF examination. [epilepsy.com]

  Mri Brain Radiology Aphasia Coding Addiction Neuroscience Massage Medicine Universe Forward wernicke's encephalopathy - wernicke's encephalopathy - Mammary body infiltration plus peri aqueductal gray and medial thalamus and hypothalamus Medical School [pinterest.fr]

  LKS is likely when the EEG of a child with acquired aphasia shows bitemporal spikes and/or CSWS; the resolution of aphasia with antiepileptic therapy is confirmatory (110). [aibolita.com]

  Vol 11, No 3 (2016) LANDAU–KLEFFNER SYNDROME (ACQUIRED EPILEPTIC APHASIA) WITH A FOCUS ON ELECTROENCEPHALOGRAPHIC CRITERIA Abstract PDF (Rus) similar documents K. Yu. Mukhin "... [rjdn.abvpress.ru]

  AneurysmsArterialAngelman syndromeAngioma, Animal Models of the EpilepsiesAnoxia/Hypoxia, Anticonvulsant/Antiepileptic Drug, (AED) LevelsAnticonvulsant/AntiepilepticDrug MechanismsAntiepileptic Drugs(AEDs)Antipsychotic DrugsAnxiety disorders and (S)Aphasia [buffalolib.org]

• Paresis

  Paresis of the right hand continues at the age of 4 years and 8 months; no further seizures have occurred and the patient's psychic development is normal. [ibecs.isciii.es]

  AAN practice guidelines Evaluating first nonfebrile seizure: Electrolytes, tox screen, lumbar puncture only if clinically indicated EEG is recommended Neuroimaging Urgent if prolonged Todd’s paresis or prolonged decreased LOC Non-urgent if cognitive or [emilytam.com]

  Hemiconvulsive SE is more common in younger children, may be followed by Todd’s paresis, usually sparing the face. Opercular status is encountered as part of the atypical evolution sometimes encountered in the syndrome. [intechopen.com]

Metabolic workup during admission, however, was equivocal, and the patient’s presentation likely had a multifactorial etiology. [frontiersin.org]

Bibliographic Information A clinical guide to epileptic syndromes and their treatment : based on the ILAE classifications and practice parameter guidelines C.P. [ci.nii.ac.jp]

Management options* Immediate seizure control (treating status epilepticus with benzodiazepines) and treatment of the underlying illness are essential. Drug treatment is needed for focal epilepsy. Hemispherectomy is beneficial. [epilepsy.com]

2.00 ADD COURSE Common Foodborne Diseases: Causes, Diagnosis & Treatment 2.00 ADD COURSE Common Oral Lesions 2.00 ADD COURSE Common Sexually Transmitted Diseases: Diagnosis and Treatment 2.00 ADD COURSE Communication and Teamwork for Patient Safety 1.00 [ceuprofessoronline.com]

In the failure of conservative treatment with anticonvulsants, epilepsy surgery may be indicated 7. History and etymology It was first described by the French neurologist Henri Jean Pascal Gastaut (1915-1995) et al. in 1960 4. [radiopaedia.org]

Part of its diagnosis includes not responding to traditional treatment for seizures. According to Wells, less than 100 cases of FIRES have been reported worldwide. [childnervoussystem.blogspot.com]

Course and prognosis Prognosis for both idiopathic childhood occipital epilepsy and idiopathic photosensitive occipital lobe epilepsy is variable. About 50–60% of Gastaut type have remission of seizures within 2–4 years of them starting. [intechopen.com]

Early-onset benign childhood occipital epilepsy (Panayiotopoulos type) Half as frequent as BECTS, excellent prognosis Age 1-14 years (typical 5 years) Seizure-types: Autonomic/behavioral disturbances with vomiting, gaze deviation, impaired consciousness [emilytam.com]

Prognosis Depends on cause and speed of effective acute management. Focal seizures appear within 1 to 5 years in 80% of the patients. Secondarily generalized tonic-clonic seizures and often convulsive status epilepticus are common. [epilepsy.com]

[…] subcortical cavitations in the affected hemisphere reduced caliber of ACA, MCA or PCA on the affected side small corpus callosum ipsilateral hemispheric volume loss with a shift of midline structures usually lack hemosiderin on T2*/ SWI Treatment and prognosis [radiopaedia.org]

[…] knowledge of PS is now based includes over 800 cases of all races; there are few epilepsy syndromes which are better characterised. " What emerges are a remarkably uniform clinical picture and a diagnosis which is strikingly useful in helping predict prognosis [eng.ichacha.net]

While a great number of textbooks have been devoted to various medical aspects of chi- hood epilepsy (diagnosis, genetics, etiology, drug and surgical treatment, etc.), there have been no comprehensive accounts of the cognitive consequences of this condition [books.google.com]

The etiologies and the underlying mechanisms remain to be understood. Using a review of the literature, we summarized the data of the last 20 years. It appears that idiopathic HH/HHE syndrome is the most common reported form. [ncbi.nlm.nih.gov]

They are organised into groups, and further divided into clinical, etiological or histopathological sub-types. [orpha.net]

Etiology Central nervous system (CNS) infection such as herpes encephalitis. A few may be traumatic or vascular. Frequently no cause is found. High family incidence of febrile seizures. [epilepsy.com]

Friedman, CR, Neimann, J., Wegener, HC, and Tauxe, RV Epidemiology of Campylobacter jejuni infections in the United States and other industrialized nations. [books.google.es]

Definitions Making the correct diagnosis in epilepsies The ILAE classification of epileptic seizures and epileptic syndromes Epidemiology of epilepsies 2 - Epileptic seizures and their classification The formal definition of epileptic seizures Classification [ci.nii.ac.jp]

Epidemiology Berry aneurysms form of aneurysms of the central nervous. [pinterest.fr]

Epidemiology Panayiotopoulos syndrome cases vary between late infancy where cases present in the late infancy period and the age of early adolescence at the age of 14 years. [intechopen.com]

They constitute key instruments for increasing knowledge on Rare Diseases by pooling data for fundamental and clinical research, epidemiological research, and real-life post-marketing observational studies. [eurordis.org]

Its cause and pathophysiology ( cause and mechanisms by which damage occurs ) are different from other epilepsies, although the symptoms are very similar to other epileptic syndromes, such as Generalized epilepsy with febrile seizures plus ( GEFS + ), [eng.ichacha.net]

In the laboratory, I use both in vivo and in vitro studies to develop new possible treatments for the control of seizures and seizure-induced brain damage, but also to understand the pathophysiology of such a complex process. [chusj.org]

The severe impairments associated with HHEsyndrome makes it imperative that continued re-search into the pathophysiology and treatment of thedisorder is performed. [myslide.es]

Auvin S, Devisme L, Maurage CA, Soto-Ares G, Cuisset JM, Leclerc F, Vallée L (2007) Neuropathological and MRI findings in an acute presentation of hemiconvulsion–hemiplegia: a report with pathophysiological implications. [link.springer.com]

Abuse and Neglect in Healthcare 2.00 ADD COURSE Preventing Allergic Reactions to Natural Rubber Latex in the Workplace 2.00 ADD COURSE Preventing Needlestick Injuries in Health Care Settings 2.00 ADD COURSE Prevention of Hepatitis A Through Active or [ceuprofessoronline.com]

[…] is better than cure and early and aggressive termination of seizures is considered the most effective way to prevent post-convulsive hemiplegia 9. [radiopaedia.org]

Career Summary My research focuses on the mechanisms of seizure-induced brain damage and how to prevent it. [chusj.org]

Aggressive anticonvulsive therapy is important to prevent/milden often developing hemiatrophy and permanent epilepsy. [pinterest.pt]