Simultaneous presentation of IgG4-related chronic peri-aortitis and coeliac disease in a patient with Marfan's Syndrome Title: Simultaneous presentation of IgG4-related chronic peri-aortitis and coeliac disease in a patient with Marfan's Syndrome Authors [spiral.imperial.ac.uk]

Storiform fibrosis was also present. Obliterative phlebitis, depicted in this figure, was shown in a vein running adjacent to an artery (top of figure). [em-consulte.com]

To review the prevalence, mechanisms, presentations and clinical significance of aortic involvement in rheumatic inflammatory diseases. Methods. [scinapse.io]

The case presented was that of a 53-year-old woman who developed aortitis with no past history of inflammatory disease, presenting with severe aortic regurgitation. [heart.bmj.com]

She had received 1 month of oral prednisone (dose unclear) 4 months prior to presentation. Her vital signs were unremarkable, including symmetric blood pressures in all 4 limbs. [jrheum.org]

Despite extensive workup, no … View Full Text Request Permissions If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. [heart.bmj.com]

If the pathologic workup for this case had ceased with only two cassettes of aortic wall, then the aortitis would have been misclassified as lymphoplasmacytic, and would raise suspicion for IgG4-related aortitis [ 13 ]. [uscapknowledgehub.org]

[…] infiltration of IgG4-positive plasma cells, storiform fibrosis, obliterative phlebitis, and elevated concentration serum IgG4. 2 Tissue biopsy is the gold standard for diagnosis of IgG4-related disease; however, imaging is an important part of the diagnostic workup [circimaging.ahajournals.org]

Diagnostic workup for IgG4-RD requires a high index of suspicion, and further workup often includes the results of serological testing for elevated levels of IgG4. [readbyqxmd.com]

[…] fibrosis. [14] Chronic periaortitis had been recognized as a common manifestation of IgG4RD, and it commonly affects abdominal aorta; it often coexists with autoimmune pancreatitis, another prototype manifestation of this disease. [15] In the diagnostic workup [indianjrheumatol.com]

At 1 month following treatment, her IgG4 levels had fallen to 31 mg/dL. [mdedge.com]

Treatment of the aortitis may prevent progression of the IgG4-related systemic disease to involvement of other organs. IgG4-related systemic disease should be considered in all patients with aortitis judged to be of unknown etiology. [ncbi.nlm.nih.gov]

Textbook of Systemic Vasculitis is an up-to-date and forward looking guide to the condition, featuring potential future developments, as well as reviewing advances in treatment over the past half-century. [books.google.com]

Further studies into diagnostic criteria, disease prevalence, prognosis, therapeutic interventions, and differentiating possible localized hypersensitivity reactions from systemic disease are areas of active investigation. [ncbi.nlm.nih.gov]

[…] of chapters throughout allows readers to easily scan through for the information required Useful summary boxes outline the main points of each condition including aetiology, pathology, epidemiology, clinical features, investigations, management and prognosis [books.google.com]

Female patients seem to have milder inflammation and a better visual prognosis. [medworm.com]

In conclusion the data show a rather good overall prognosis of CP and they question a central role of IgG4 in the pathogenesis of periaortitis. [rheuma-schweiz.ch]

Retroperitoneal fibrosis Periaortic and aortic inflammation associated with retroperitoneal and mediastinal fibrosis Behcet's disease Genital and oral aphthous ulcers, uveitis Sarcoidosis Interstitial lung diseases Relationship between postoperative prognosis [freethesaurus.com]

IgG4-related systemic disease should be considered in all patients with aortitis judged to be of unknown etiology. [Indexed for MEDLINE] Free full text [ncbi.nlm.nih.gov]

The secondary headaches include a diverse and fascinating array of etiologies which can mimic primary headache disorders ranging from the rare to the mundane and from the well established to the highly controversial. [books.google.com]

Stone and his colleagues concluded that IgG4-related systemic disease should be considered in all patients with aortitis of unknown etiology, and noted that treatment might prevent progression of the systemic disease to other organs. [mdedge.com]

Their etiology varies greatly based on patient’s age and other clinicopathologic determinants. [ijcep.com]

IgG4-related systemic disease should be considered in all patients with aortitis judged to be of unknown etiology. [docplayer.net]

Management of Acute Hemorrhage Platelets Plasma and Specialized Coagulation Concentrate New Approaches for the Therapy of Bleeding Disorders Overview of Venous Thromboembolism Thrombophilia Genetics Epidemiology and Risk Factors for Venous Clinical Manifestations [books.google.de]

Textbook of Systemic Vasculitis is an in-depth guide to the epidemiology, classification and genetics of systemic vasculitis as well as imaging, symptoms and management of the disease. [books.google.com]

Manifestations and Diagnosis of Venous Venous Thrombosis in Unusual Sites Victor J Marder Hylton V Joffe and Sam Schulman Prevention of Venous Thromboembolic Disease Treatment of Venous Thromboembolic Disease Overview of Arterial Thrombotic Disorders Pathophysiology [books.google.de]

Mediterr J Rheumatol 2016;27(4):191-3 58-year-old patient with IgG4-related thoracic aortitis Authors Information Department of Pathophysiology, Medical School, University of Athens, Athens, Greece Abstract We report a 58-year-old male with a one-month [mjrheum.org]

It should be regarded as a generalized disease with three different pathophysiological entities, specifically idiopathic retroperito... more Ref 78 Download PDF Cite this paper An elevated IgG4 response in chronic infectious aortitis is associated with [scinapse.io]

CONCLUSIONS: The results of this retrospective multicenter study highlight three important points: (1) the possibility of latent existence and progression of periaortic/periarterial lesions, (2) the efficacy of corticosteroid therapy in preventing new [ncbi.nlm.nih.gov]

[…] of Venous Thromboembolic Disease Treatment of Venous Thromboembolic Disease Overview of Arterial Thrombotic Disorders Pathophysiology of Atherothrombosis Prevention of Thromboembolic Stroke in Patients with Acute Thrombolytic Therapy Unusual Sites of [books.google.de]

Conclusions : The results of this retrospective multicenter study highlight three important points: (1) the possibility of latent existence and progression of periaortic/periarterial lesions, (2) the efficacy of corticosteroid therapy in preventing new [pubfacts.com]