Simultaneous presentation of IgG4-related chronic peri-aortitis and coeliac disease in a patient with Marfan’s Syndrome David Lindsay, Mediola Ismajli, Roger Bucknall, George Lipscomb, Joseph J. Boyle, Justin C. [scilit.net]

Simultaneous presentation of IgG4-related chronic peri-aortitis and coeliac disease in a patient with Marfan's Syndrome Title: Simultaneous presentation of IgG4-related chronic peri-aortitis and coeliac disease in a patient with Marfan's Syndrome Authors [spiral.imperial.ac.uk]

Storiform fibrosis was also present. Obliterative phlebitis, depicted in this figure, was shown in a vein running adjacent to an artery (top of figure). [em-consulte.com]

Developed by 30 distinguished contributors, the book consists of six parts and 16 chapters, with each chapter presenting two cases. [books.google.de]

• HELLP Syndrome

  The pregnancy wascomplicated by diabetes mellitus, fetal cardiac abnormality, and HELLP syndrome (hemolysis, elevated liver enzymes, and lowplatelets), necessitating emergency delivery at 34 weeks. [dokumen.tips]

  The pregnancy was complicated by diabetes mellitus, fetal cardiac abnormality, and HELLP syndrome (hemolysis, elevated liver enzymes, and low platelets), necessitating emergency delivery at 34 weeks. [docplayer.net]

• Inguinal Mass

  Khoan Vu, Richa Gupta, John Frater, John Atkinson and Prabha Ranganathan, A 55‐Year‐Old Man With Periorbital and Inguinal Masses, Pericarditis, and Pleuritis, Arthritis Care & Research, 69, 5, (730-736), (2017). [doi.org]

• Mediastinal Lymphadenopathy

  Four years before the diagnosis of his aortic dissection, the patient had been found to have mediastinal lymphadenopathy, with lymph nodes up to 3 cm in diameter. The patient had undergone biopsy of a subcarinal lymph node via mediastinoscopy. [docplayer.net]

• Respiratory Disorders

  It is now widely believed that IgG4-RD characteristically manifests as Mikulicz’s disease [ 4 ], respiratory disorders [ 5 ], sclerosing cholangitis [ 6 ], retroperitoneal fibrosis [ 3 ], tubulointerstitial nephritis [ 7 ], and prostatitis [ 8 ]. [ncbi.nlm.nih.gov]

• Anosmia

  In this article, we report two patients of IgG4 syndrome: a 60-year-old male with complaints of nasal congestion, rhinitis, anosmia and hearing loss, and a 28-year-old female with bilateral orbital and parotid gland swelling. [scinapse.io]

• Jaw Claudication

  However, there was no clinical evidence of cranial involvement, ie headaches, vision changes, or jaw claudication. Thus, immediate glucocorticoid therapy to prevent vision loss was not essential. [uscapknowledgehub.org]

  She denied fevers, chills, night sweats, visual changes, jaw claudication, joint pain, or focal neurologic symptoms. Her medications included aspirin and captopril. [jrheum.org]

  He denied having head-aches, vision changes, jaw claudication, rash, weakness, orsymptoms of polymyalgia rheumatica.Physical examination on the sixth postoperativeday revealed an irregularly irregular heart rhythm. [dokumen.tips]

  He denied having headaches, vision changes, jaw claudication, rash, weakness, or symptoms of polymyalgia rheumatica. Physical examination on the sixth postoperative day revealed an irregularly irregular heart rhythm. [docplayer.net]

• Irregular Heart Rhythm

  He denied having head-aches, vision changes, jaw claudication, rash, weakness, orsymptoms of polymyalgia rheumatica.Physical examination on the sixth postoperativeday revealed an irregularly irregular heart rhythm. [dokumen.tips]

  Physical examination on the sixth postoperative day revealed an irregularly irregular heart rhythm. The rate ranged from 80 to 123 beats per minute. [docplayer.net]

• Irregularly Irregular Heart Rhythm

  He denied having head-aches, vision changes, jaw claudication, rash, weakness, orsymptoms of polymyalgia rheumatica.Physical examination on the sixth postoperativeday revealed an irregularly irregular heart rhythm. [dokumen.tips]

  Physical examination on the sixth postoperative day revealed an irregularly irregular heart rhythm. The rate ranged from 80 to 123 beats per minute. [docplayer.net]

• Ankle Pain

  Between week 20of gestation and delivery, physical examination, laboratory testing, plain radiography, and magnetic resonance imaging (MRI) wereperformed to investigate the cause of the ankle pain. [dokumen.tips]

  J Invest Dermatol 2003;120: DOI /art Clinical Images: Transient regional osteoporosis The patient, a 33-year-old woman, developed left ankle pain at week 20 of gestation during her first pregnancy. [docplayer.net]

• Osteopenia

  Plain radiography revealed generalized osteopenia of the bones of the left foot. MRI showedextensive bone marrow edema within the left talus, with similar patchy changes present in adjacent bones. [dokumen.tips]

  Plain radiography revealed generalized osteopenia of the bones of the left foot. MRI showed extensive bone marrow edema within the left talus, with similar patchy changes present in adjacent bones. [docplayer.net]

• Thigh Pain

  A 54-year-old man presented with right lower abdominal and upper thigh pain. Cross-sectional imaging of the abdomen revealed right hydronephrosis caused by a mass adjacent to the bladder. [em-consulte.com]

• Severe Osteoporosis

  Given concomitant severe osteoporosis, steroid-sparing agents in the form of weekly methotrexate and intravenous rituximab (1000 mg twice, 2 weeks apart) were administered 3 and 6 months from the time of diagnosis, respectively. [jrheum.org]

• Paresthesia

  The patient reported a 20-pound weight lossin the year that preceded the aortic surgery, as well as aworsening of distal paresthesias in his feet, which wasattributed to diabetic neuropathy. [dokumen.tips]

  The patient reported a 20-pound weight loss in the year that preceded the aortic surgery, as well as a worsening of distal paresthesias in his feet, which was attributed to diabetic neuropathy. [docplayer.net]

• Forgetful

  Chiara Tioni, Marco Antonutti, Concetta Di Nora and Alessandro Proclemer, Never forget the aorta: a case report of IgG4-related disease causing aortitis, European Heart Journal - Case Reports, 10.1093/ehjcr/yty111, (2018) . [doi.org]

• Dysuria

  Other presenting signs or symptoms include leg edema, varicocele, testicular pain, claudication, dysuria, frequency and, in cases with advanced bilateral ureteral stenosis, oligo-anuria. Thrombophlebitis or deep vein thrombosis may also occur. [omicsonline.org]

• Anuria

  Other presenting signs or symptoms include leg edema, varicocele, testicular pain, claudication, dysuria, frequency and, in cases with advanced bilateral ureteral stenosis, oligo-anuria. Thrombophlebitis or deep vein thrombosis may also occur. [omicsonline.org]

Despite extensive workup, no … View Full Text Request Permissions If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. [heart.bmj.com]

If the pathologic workup for this case had ceased with only two cassettes of aortic wall, then the aortitis would have been misclassified as lymphoplasmacytic, and would raise suspicion for IgG4-related aortitis [ 13 ]. [uscapknowledgehub.org]

[…] infiltration of IgG4-positive plasma cells, storiform fibrosis, obliterative phlebitis, and elevated concentration serum IgG4. 2 Tissue biopsy is the gold standard for diagnosis of IgG4-related disease; however, imaging is an important part of the diagnostic workup [circimaging.ahajournals.org]

Diagnostic workup for IgG4-RD requires a high index of suspicion, and further workup often includes the results of serological testing for elevated levels of IgG4. [readbyqxmd.com]

[…] fibrosis. [14] Chronic periaortitis had been recognized as a common manifestation of IgG4RD, and it commonly affects abdominal aorta; it often coexists with autoimmune pancreatitis, another prototype manifestation of this disease. [15] In the diagnostic workup [indianjrheumatol.com]

• Normocytic Anemia

  Prior to surgery, the patient hadhad mild normochromic, normocytic anemia, with ahematocrit value of 37.4% (normal 4153) and a meancorpuscular volume of 77 fl (normal 80100). The serumcreatinine level was 1.5 mg/dl (normal 0.81.2). [dokumen.tips]

  Prior to surgery, the patient had had mild normochromic, normocytic anemia, with a hematocrit value of 37.4% (normal 41 53) and a mean corpuscular volume of 77 fl (normal ). The serum creatinine level was 1.5 mg/dl (normal ). Other Figure 3. [docplayer.net]

• Polyps

  […] hyperplasia with sinushistiocytosis, considered a normal finding.The patients earlier medical history was signifi-cant for diabetes mellitus, hypertension, coronary arterydisease, chronic obstructive pulmonary disease, chronicrhinosinusitis with nasal polyps [dokumen.tips]

  The patient s earlier medical history was significant for diabetes mellitus, hypertension, coronary artery disease, chronic obstructive pulmonary disease, chronic rhinosinusitis with nasal polyps, hypothyroidism, obstructive sleep apnea, and chronic renal [docplayer.net]

  Presentation includes allergic rhinitis, nasal polyps, chronic sinusitis, nasal obstruction, and rhinorrhea. Mild to moderate peripheral eosinophilia and elevated serum IgE levels are common. [rarediseasesjournal.com]

• Granulomatous Arthritis

  Rheumatic disorders may be categorized by their propensity to involve the aorta: conditions with a prevale... more A syndrome of granulomatous arthritis-uveitis-rash has been described in children. [scinapse.io]

At 1 month following treatment, her IgG4 levels had fallen to 31 mg/dL. [mdedge.com]

Treatment of the aortitis may prevent progression of the IgG4-related systemic disease to involvement of other organs. IgG4-related systemic disease should be considered in all patients with aortitis judged to be of unknown etiology. [ncbi.nlm.nih.gov]

[…] of IgG4-Related Disease Abstract 1 Introduction 2 Diagnosis 2.1 Epidemiology 2.2 Clinical Symptoms 2.3 Laboratory Tests 2.4 Imaging 2.5 Histopathology 2.6 Steroid Responsiveness 2.7 Diagnostic Criteria 3 Treatment 3.1 Indication of Treatment 3.2 Induction [library.wur.nl]

Textbook of Systemic Vasculitis is an up-to-date and forward looking guide to the condition, featuring potential future developments, as well as reviewing advances in treatment over the past half-century. [books.google.com]

Further studies into diagnostic criteria, disease prevalence, prognosis, therapeutic interventions, and differentiating possible localized hypersensitivity reactions from systemic disease are areas of active investigation. [ncbi.nlm.nih.gov]

[…] of chapters throughout allows readers to easily scan through for the information required Useful summary boxes outline the main points of each condition including aetiology, pathology, epidemiology, clinical features, investigations, management and prognosis [books.google.com]

In conclusion the data show a rather good overall prognosis of CP and they question a central role of IgG4 in the pathogenesis of periaortitis. [rheuma-schweiz.ch]

Retroperitoneal fibrosis Periaortic and aortic inflammation associated with retroperitoneal and mediastinal fibrosis Behcet's disease Genital and oral aphthous ulcers, uveitis Sarcoidosis Interstitial lung diseases Relationship between postoperative prognosis [freethesaurus.com]

Symptoms 2.3 Laboratory Tests 2.4 Imaging 2.5 Histopathology 2.6 Steroid Responsiveness 2.7 Diagnostic Criteria 3 Treatment 3.1 Indication of Treatment 3.2 Induction of Remission 3.3 Relapse and Maintenance Therapy 3.4 Treatment-Related Side Effects4 Prognosis [library.wur.nl]

IgG4-related systemic disease should be considered in all patients with aortitis judged to be of unknown etiology. [Indexed for MEDLINE] Free full text [ncbi.nlm.nih.gov]

Their etiology varies greatly based on patient’s age and other clinicopathologic determinants. [ijcep.com]

A small subset of patients have predominantly plasmacytic aortitis of uncertain etiology. [docksci.com]

The secondary headaches include a diverse and fascinating array of etiologies which can mimic primary headache disorders ranging from the rare to the mundane and from the well established to the highly controversial. [books.google.com]

The patient's symptoms, the unusual appearance on computed tomography, the presence of popliteal aneurysms in a woman, and the normal WBC scan were indicative of an inflammatory etiology. [arizona.pure.elsevier.com]

Management of Acute Hemorrhage Platelets Plasma and Specialized Coagulation Concentrate New Approaches for the Therapy of Bleeding Disorders Overview of Venous Thromboembolism Thrombophilia Genetics Epidemiology and Risk Factors for Venous Clinical Manifestations [books.google.de]

Textbook of Systemic Vasculitis is an in-depth guide to the epidemiology, classification and genetics of systemic vasculitis as well as imaging, symptoms and management of the disease. [books.google.com]

Manifestations and Diagnosis of Venous Venous Thrombosis in Unusual Sites Victor J Marder Hylton V Joffe and Sam Schulman Prevention of Venous Thromboembolic Disease Treatment of Venous Thromboembolic Disease Overview of Arterial Thrombotic Disorders Pathophysiology [books.google.de]

Mediterr J Rheumatol 2016;27(4):191-3 58-year-old patient with IgG4-related thoracic aortitis Authors Information Department of Pathophysiology, Medical School, University of Athens, Athens, Greece Abstract We report a 58-year-old male with a one-month [mjrheum.org]

CONCLUSIONS: The results of this retrospective multicenter study highlight three important points: (1) the possibility of latent existence and progression of periaortic/periarterial lesions, (2) the efficacy of corticosteroid therapy in preventing new [ncbi.nlm.nih.gov]

[…] of Venous Thromboembolic Disease Treatment of Venous Thromboembolic Disease Overview of Arterial Thrombotic Disorders Pathophysiology of Atherothrombosis Prevention of Thromboembolic Stroke in Patients with Acute Thrombolytic Therapy Unusual Sites of [books.google.de]

Conclusions : The results of this retrospective multicenter study highlight three important points: (1) the possibility of latent existence and progression of periaortic/periarterial lesions, (2) the efficacy of corticosteroid therapy in preventing new [pubfacts.com]