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Interstitial Pulmonary Fibrosis of the Newborn

Interstitial Pulmonary Fibrosis of Fetus or Newborn


Presentation

  • Neonatal respiratory distress is a common presenting symptom, although childhood interstitial lung disease and pulmonary fibrosis can also be presenting diagnoses..[hopkinsmedicine.org]
  • Six were symptomatic at birth with 10 of the 11 presenting at or before 3 months of age. The most common presenting sign was tachypnoea associated with rib indrawing, occurring in nine cases.[adc.bmj.com]
  • In the present report, we reviewed our experience with 10 infants during a 10-year period. In 9 patients, onset of symptoms occurred before the age of 2 months and included tachypnea, cough, and inadequate weight gain.[ncbi.nlm.nih.gov]
  • Occasionally, patients present withbegan.[slideshare.net]
Pain
  • […] or itchy Reduced sweating Fox-Fordyce disease Toe-web intertrigo (athlete's foot) Common in people wearing tight fitting shoes Bacterial infection sometimes due to Pseudomonas aeruginosa Mild form presents with erythema and scaling May cause burning pain[dermnetnz.org]
  • , discomfort, or difficulty performing daily activities problems in the joints, such as swelling or pain Inverse psoriasis and intertrigo are two skin conditions that affect areas where the skin folds, such as the armpits, groin, and abdomen, causing[medicalnewstoday.com]
  • Signs and symptoms of intertrigo Intertrigo usually is chronic with an insidious onset of itching, burning, pain, and stinging in the skin folds. Intertrigo initially presents as mild erythematous patches on both sides of the skinfold.[emedicine.medscape.com]
  • The rash can be itchy or painful, but it’s not contagious. Bacteria, fungus, and yeast can easily grow in this warm and moist environment and worsen the rash.[healthline.com]
Camping
  • Courageous Kids Summer Camp A unique 4-day annual event providing an opportunity for children and teens who have experienced a death in their families.[app.peacehealth.org]
Surgical Procedure
  • The approach of the surgical procedure should always be coded. True or False It is not necessary to code closure of a routine surgical incision.True or False.[quizlet.com]
Vomiting
  • […] conditions due to chemicals, gases, fumes and vapors J688Other respiratory conditions due to chemicals, gases, fumes and vapors J689Unspecified respiratory condition due to chemicals, gases, fumes and vapors J690Pneumonitis due to inhalation of food and vomit[cms.gov]
  • In people with diabetes, infectious intertrigo may result in cellulitis, a potentially serious infection that can cause red streaks, fever, nausea, and vomiting.[verywellhealth.com]
Hematochezia
  • A patient presents to the Emergency Room (ER) with hematochezia and hematemesis.[quizlet.com]
Dysphagia
  • Dysphagia increases the risk of silent and nonsilent aspirations and lung infections [ 23 ]. Although lung involvement in Niemann–Pick disease is frequently reported, its prevalence is unknown.[err.ersjournals.com]
Nausea
  • In people with diabetes, infectious intertrigo may result in cellulitis, a potentially serious infection that can cause red streaks, fever, nausea, and vomiting.[verywellhealth.com]
Hypertension
  • Lastly, patients with idiopathic pulmonary fibrosis often have pulmonary hypertension as their disease progresses.[medicinenet.com]
  • Pulmonary hypertension may be seen in non-ketotic hyperglycaemia [ 4 ], and was described in glycogenoses type I [ 5, 6 ], inborn errors of intracellular cobalamin metabolism [ 7 ], HUPRA (hyperuricaemia, pulmonary hypertension, renal failure and alkalosis[err.ersjournals.com]
  • Hypertension and chronic renal insufficiency 403.90, 585.9 The patient has hypertension and kidney disease so it is hypertensive kidney disease category 403.[quizlet.com]
  • Pulmonary hypertension – Unlike systemic hypertension , this condition occurs only in the pulmonary arteries.[doctortipster.com]
  • Some complications may include: Pulmonary hypertension : Increased blood pressure in the pulmonary blood vessels (pulmonary hypertension) Cor pulmonale : Heart failure involving the right side of the heart (most of the time heart failure means left heart[verywell.com]
Heart Failure
  • (congestive) and diastolic (congestive) heart failure I50810Right heart failure, unspecified I50811Acute right heart failure I50812Chronic right heart failure I50813Acute on chronic right heart failure I50814Right heart failure due to left heart failure[cms.gov]
  • Some complications may include: Pulmonary hypertension : Increased blood pressure in the pulmonary blood vessels (pulmonary hypertension) Cor pulmonale : Heart failure involving the right side of the heart (most of the time heart failure means left heart[verywell.com]
  • Heart failure often develops. The median survival for people with IPF is five years.[columbiasurgery.org]
  • The most common were: sepsis, heart failure, acute kidney failure, asphyxia and prematurity.[jped.com.br]
  • One form is caused by heart failure and back pressure in the lungs' blood vessels; in another form, direct injury to the lung causes the leak of fluid. Lung Cancer has many forms, and may develop in any part of the lungs.[ejgh.org]
Chest Pain
  • Other, but less common symptoms may include: A dry cough Chest pain Palpitations Weight loss Fatigue Muscle and joint aches Clubbing (a condition in which the end of the fingers take on the look of an inverted spoon) Causes There are many possible causes[verywell.com]
  • Substernal or pleuritic chest pain is rare.[archbronconeumol.org]
  • (You would not code the chest pain because it is an integral part of angina.) Patient has a gastronomy tube and receives tube feedings. This requires 2 codes. One code indicates the presence of the gastrostomy tube.[quizlet.com]
Tachycardia
  • (See index entry: Failure, heart, congestive) 427.1 VT stands for ventricular tachycardia. See Index for Tachycardia, paroxysmal, ventricular. This is confirmed in the Tabular Listing.[quizlet.com]
Thrombosis
  • The endothelial lesions induced by lipids infused with the parenteral nutrition can encourage both thrombosis and colonization by microorganisms.[jped.com.br]
Grieving
  • Surviving the Holidays Educational series for persons grieving the death of a loved one. Test[app.peacehealth.org]
Stroke
  • Stroke 2009; 40: 9: 3045-3050. // p. 61[mediasphera.ru]
  • Lyden, MD Chair, Department of Neurology Director, Cedars-Sinai Stroke Center Carmen and Louis Warschaw Chair in Neurology Research Profile The research of Patrick D. Lyden, MD, focuses on translational stroke research.[careers.cedars-sinai.edu]
  • IPF can raise your odds of getting other conditions, including: High blood pressure in the lungs, called pulmonary hypertension Heart attack Stroke Blood clots in your lungs Lung cancer Lung infections Ask your doctor what you can do to lower your chances[webmd.com]
  • A CVA is also known as a cerebrovascular accident or stroke, which is considered a cerebrovascular disease. Use the ICD-9 Alphabetic Index and Tabular List to find the correct diagnosis code(s).[quizlet.com]

Workup

Pulmonary Infiltrate
  • . - Pulmonary infiltrates in immunodeficient patients. Pulmonary infiltrates in patients with lowered immunity, primarily those caused by opportunistic pathogens, produce interstitial patterns in chest radiographs.[archbronconeumol.org]
  • infiltrates with eosinophiliaPulmonary infiltrates with eosinophilia  Pulmonary Interstial glycogenosis (PIG )Pulmonary Interstial glycogenosis (PIG ) 15.[slideshare.net]
Hypercapnia
  • […] with hypercapnia J9620Acute and chronic respiratory failure, unspecified whether with hypoxia or hypercapnia J9621Acute and chronic respiratory failure with hypoxia J9622Acute and chronic respiratory failure with hypercapnia J9690Respiratory failure,[cms.gov]
  • M ellies et al. [ 128 ] applied noninvasive ventilation to eight adults with late-onset Pompe disease and respiratory failure apparent from severe restrictive lung disease, nocturnal hypoxaemia and daytime hypercapnia.[err.ersjournals.com]
  • Arterial hypoxemia only becomes evident in the advanced stages of the disease, and hypercapnia in the final stages. Exercise testing reveals a low exercise tolerance because of the dyspnea associated with hypoxemia caused by the exercise.[archbronconeumol.org]
ST Elevation
  • (There is no mention of left heart, systolic, or diastolic heart failure so these conditions should not be coded. ) NSTEMI (Note: Assume this is the initial episode of care) 410.71 NSTEMI is a non-ST elevation MI, one type of Acute Myocardial Infarction[quizlet.com]

Treatment

  • […] of ILD The causes of ILD are not well understood—and this sometimes makes diagnosis and treatment difficult.[brighamandwomens.org]
  • Conditions that improve with immune suppressive treatment probably are not idiopathic pulmonary fibrosis. The toxicity and side effects of treatments can be serious.[medicinenet.com]

Prognosis

  • The prognosis in infancy is thought to be poor 2-4 ; a recent case series 2 recorded nine deaths out of ten patients. The authors suggested that a delay in diagnosis might have contributed to the poor prognosis.[adc.bmj.com]
  • Prognosis. In the case of pneumonitis with a good response to treatment, the prognosis is favorable. The prognosis for fibrosis is variable.[archbronconeumol.org]
  • Natural histories differ depending upon the genes involved and a specific diagnosis is important to provide accurate information concerning prognosis and mode of inheritance.[jhu.pure.elsevier.com]
  • The prognosis of pulmonary fibrosis also depends on the particular cause.[verywell.com]

Etiology

  • [Etiology of intertrigo in adults: A prospective study of 103 cases]. J Mycol Med. 2017 Mar;27(1):28-32. [PubMed: 27554869] 8. Kalkan G, Duygu F, Bas Y.[ncbi.nlm.nih.gov]
  • INTERSTIAL LUNG DISEASES OF KNOWN ETIOLOGY Aspiration syndromes Chronic infection Bronchopulmonary dysplasia Hypersensitivity pneumonitis ( drugs, environment or occupation associated ) Surfactant B or C deficiency 13.[slideshare.net]
  • Etiology of intertrigo Intertrigo develops from mechanical factors and secondary infection. Heat and maceration are central to the process. Opposing skin surfaces rub against each other, at times causing erosions that become inflamed.[emedicine.medscape.com]
  • Myofibroblasts are considered to be an important determinant in the etiology of fibrosis and inhibiting myofibroblast differentiation has become an important target for therapy.[albany.edu]
  • […] and Classification The etiology of DILD is extremely varied.[archbronconeumol.org]

Epidemiology

  • Neurology and Neurosurgery Czech and Slovak Ophthalmology Czech and Slovak Psychiatry Czech Geriatric Review Czech Gynaecology Czech Rheumatology Czech Dental Journal Czech Urology Czech-Slovak Dermatology Czecho-Slovak Pathology Czech-Slovak Pediatrics Epidemiology[prolekare.cz]
  • [Clinical aspects, epidemiology and economic impact of foot epidermomycosis in an industrial milieu]. Ann Dermatol Venereol. 1986;113(6-7):521-33. [PubMed: 2949683] 10. Del Rosso JQ.[ncbi.nlm.nih.gov]
  • Epidemiology Epidemiological data on DILD are sparse. The incidence and prevalence reported in the literature are highly variable because the epidemiological methods used differ from one study to another.[archbronconeumol.org]
  • Epidemiology ILD is rare in children. Cases tend to cluster in infancy, and 10-16% appear to be familial.[slideshare.net]
  • Epidemiological research on the prevalence of interstitial disease in adults from the United States suggests that the condition is more common in the general population 10 than previous estimates based on hospital records would suggest. 11 There is evidence[adc.bmj.com]
Sex distribution
Age distribution

Pathophysiology

  • Lindsey Zehr Internship Title: Idiopathic Pulmonary Fibrosis (IPF): A comprehensive evaluation of disease pathophysiology, biomedical research, and clinical observation Internship Mentor: R.[albany.edu]
  • Pathophysiology [ edit ] In disorders that are intrinsic to the lung parenchyma, the underlying process is usually pulmonary fibrosis (scarring of the lung). [5] As the disease progresses, the normal lung tissue is gradually replaced by scar tissue interspersed[en.wikipedia.org]
  • Pathophysiology The pathophysiologyThe pathophysiology is more complexis more complex than adult diseasethan adult disease because the injurybecause the injury occurs during theoccurs during the process of lungprocess of lung growth andgrowth and differentiation.differentiation[slideshare.net]
  • Pathophysiology Environmental factors and genetic causes play a leading role in the development of intertrigo. One of these factors is the friction caused by adjacent skin surfaces causing inflammation of the epidermis.[ncbi.nlm.nih.gov]
  • Stroke: Pathophysiology, Diagnosis, and Management 5th ed. Philadelphia: Elsevier Inc 2011; 750-752. Greenberg J., Skubick D., Shenkin H. Acute hydrocephalus in cerebellar infarct and hemorrhage. Neurology 1979; 29: 409-413. Klugkist H., McCarthy J.[mediasphera.ru]

Prevention

  • Additionally, preventative measures to reduce skin-on-skin friction and moisture can help in the management of current intertrigo and prevent future episodes.[emedicine.medscape.com]
  • Prevention Prevention is key. Once intertrigo sets in, it can be difficult to cure unless the root causes (such as obesity) are addressed.[verywellhealth.com]
  • - 0% Emergent - ED Care Needed - Preventable/Avoidable - 0% Emergent - ED Care Needed - Not Preventable/Avoidable - 0% Primary diagnosis of injury 0% Primary diagnosis of mental health problems 0% Primary diagnosis of substance abuse 0% Primary diagnosis[medicbind.com]
  • Is it possible to prevent intertrigo? It's possible to prevent simple intertrigo by liberally applying a lubricating ointment like petrolatum directly into the intertriginous skin fold predisposed to irritation prior to any physical activity.[rxlist.com]

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