Our patient presented all the clinical manifestations corresponding to the severe form of the disease. [elsevier.es]

• Recurrent Bacterial Infection

  Possible diagnosis: patients with important leucocytosis >25,000cells/mm3 and one of the following: - Recurrent bacterial infections. - Deep-seated and severe infection. - Absence of pus at the sites of infection. [elsevier.es]

Regarding aetiological treatment, HLA typing of the patient was started, together with the search for a haematopoietic precursor cell donor. [elsevier.es]

If transplantation is performed before serious infections develop, the resulting prognosis is very good. [elsevier.es]

Correct oral hygiene is important for the control of periodontitis and for preventing infections. These patients can receive all vaccines, including those involving live viruses. [elsevier.es]