Good sources of potassium include: bananas vegetables pulses nuts and seeds milk fish shellfish beef chicken turkey bread Always tell medical staff that you have long QT syndrome. [nhs.uk]

Circulation. 1995;92:3381-3386 [34] Kannankeril PJ, Roden DM, and Fish FA. Suppression of bidirectional ventricular tachycardia and unmasking of prolonged QT interval with verapamil in Andersen’s syndrome. J Cardiovasc Electrophysiol. 2004;15:119. [geneticheartdisease.org]

View Article PubMed Google Scholar Plaster NM, Tawil R, Tristani-Firouzi M, Canun S, Bendahhou S, Tsunoda A, Donaldson MR, Iannaccone ST, Brunt E, Barohn R, Clark J, Deymeer F, George AL, Fish FA, Hahn A, Nitu A, Ozdemir C, Serdaroglu P, Subramony SH, [ojrd.biomedcentral.com]

Viskin S, Fish R, Zeltser D, Belhassen B, Heller K, Brosh D, et al. Arrhythmias in the congenital long QT syndrome: how often is torsade de pointes pause dependent? Heart. 2000;83:661-6. 59. Walker BD, Krahn AD, Klein GJ, Skanes AC, Yee R. [revespcardiol.org]

Even though the clinical diagnosis of J-LN is rather straightforward, it is important to genotype all these patients because it has been shown by Schwartz et al. [ 3 ] that the smaller group with KCNE1 mutations has a markedly less severe clinical course [ojrd.biomedcentral.com]

LQTS8 Also known as Timothy syndrome (TS), patients show severe QT prolongation on their ECGs, which is combined with syndactyly, baldness at birth, and small teeth in 100% of cases and less penetrant cardiac structural malformations, mental retardation [frontiersin.org]

Clinical Topics: Arrhythmias and Clinical EP, Congenital Heart Disease and Pediatric Cardiology, Dyslipidemia, Prevention, Implantable Devices, EP Basic Science, Genetic Arrhythmic Conditions, SCD/Ventricular Arrhythmias, Atrial Fibrillation/Supraventricular [acc.org]

Sub-type Frequency Gene Mutation Effect ECG finding LQTS 1 30-35% KVLQT1 K Efflux Broad, late-inset, T wave LQTS 2 25-30% HERG K Efflux Widely-split, low-amplitude, T wave LQTS 3 5-10% SCN5A Prolonged Na influx Biphasic or peaked, late-onset, T wave LQTS [geneticheartdisease.org]

Sub-type Frequency Gene Mutation Effect ECG finding LQTS 1 30-35% KVLQT1 K Efflux Broad, late-inset, T wave LQTS 2 25-30% HERG K Efflux Widely-split, low-amplitude, T wave LQTS 3 5-10% SCN5A Prolonged Na influx Biphasic or peaked, late-onset, T wave LQTS [geneticheartdisease.org]

The electrocardiogram of these patients has a prominent U wave and a normal or modestly prolonged QT interval. Although LQT7 is currently included among the sub-types of congenital long-QT syndrome, this inclusion is controversial. [geneticheartdisease.org]

The electrocardiogram of these patients has a prominent U wave and a normal or modestly prolonged QT interval. Although LQT7 is currently included among the sub-types of congenital long-QT syndrome, this inclusion is controversial. [geneticheartdisease.org]