We present three cases of orbital lymphangioma that were treated with sclerotherapy. Case 1: A 6-month-old boy was presented in 2010 with right ptosis and proptosis. [ncbi.nlm.nih.gov]

Presents as cutaneous vesicles. [dermpedia.org]

• Axillary Lesion

  She underwent wide excision of the right breast and axillary lesion and the lesion pathologic finding is lymphangioma of the breast. [ncbi.nlm.nih.gov]

• Tonsillar Hypertrophy

  Radiofrequency treatment for obstructive tonsillar hypertrophy. Arch Otolaryngol Head Neck Surg 2000 ;126: 736 – 40. Google Scholar | Crossref | Medline 44. Mann, W. What is the value of somnoplasty? Facelift from the inside for snorers. [doi.org]

• Inspiratory Stridor

  We present the case of a four month old male who presented with chief complaint of inspiratory stridor after a single episode of pneumonia. [ncbi.nlm.nih.gov]

• Painful Cough

  Patients with lymphangioma of the neck and mediastinum are usually asymptomatic but they may present chest pain, cough, dyspnea, dysphagia, or vascular compression syndromes if the lesion reaches dimensions large enough to cause compression of adjacent [qims.amegroups.com]

• Macroglossia

  Key words :Cystic hygroma, Lymphangioma, Macroglossia Lymphangioma is a benign, harmatomatous tumour of lymphatic vessels with a marked predilection for the head and neck region. [arabmedmag.com]

  Isolated tongue involvement can lead to macroglossia with dysphagia and airway obstruction. [ncbi.nlm.nih.gov]

  Oral lymphangiomas occur more commonly in the anterior two-third of the tongue, resulting in macroglossia. Various other sites such as lip, palate, and buccal mucosa have been reported. [jofs.in]

• Lacrimation

  Lacrimal Gland Lymphangioma: Report of a Case and Review of Literature. Orbit. 2012 Feb 16. [Medline]. Shah A, Meacock L, More B, Chandran H. Lymphangioma of the penis: a rare anomaly. Pediatr Surg Int. 2005 Apr. 21(4):329-30. [Medline]. [emedicine.medscape.com]

• Pterygium Colli

  They are known to be associated with Turner's syndrome, Noonan's syndrome, Trisomies, Cardiac anomalies, Fetal hydrops, Fetal alcohol syndrome, and Familial pterygium colli. [ghorayeb.com]

• Vesicular Rash

  Lymphangiomas are most commonly described as a small painless mass in the neck or a vesicular rash in an infant patient. Ninety per cent of cases are diagnosed before the age of 2. Treatment usually involves surgical resection. [ncbi.nlm.nih.gov]

• Neck Swelling

  Conversely, the breasts shrunk remarkably while the upper chest and neck swellings became worse when she lay down [Figure 2]. [afrjpaedsurg.org]

• Gait Ataxia

  An 83-year-old woman presented with progressive gait ataxia, bilateral lower extremity weakness, and a band-like sensation in the middle and lower thoracic dermatomes. [ncbi.nlm.nih.gov]

The clinical presentation is usually subacute and diagnosis made incidentally during a workup of chronic gastrointestinal symptoms. [ncbi.nlm.nih.gov]

• Ovarian Mass

  Even though most cystic masses are of ovarian origin, non-ovarian causes can mimic ovarian masses and should be considered as differential diagnoses. Surgical exploration may be necessary to exclude malignant causes. [ncbi.nlm.nih.gov]

• Karyotype Abnormal

  Etiology Karyotypic abnormalities are present in 25-70% of children with LM. [emedicine.com]

199 Downloads 43 Citations Purpose: To determine the efficacy of OK-432 sclerotherapy in the treatment of lymphangiomas. Methods: The treatment was begun for 14 patients with lymphangioma. [doi.org]

For a lymphangioma with a large vascular component, consider experimental treatment with propranolol. It is now an established treatment to decrease the size of capillary hemangiomas. [aao.org]

This report outlines our approach to workup and treatment of this rare lesion. Case report of presentation, diagnosis and treatment is presented. [ncbi.nlm.nih.gov]

OK-432 is therefore proposed as a first line option for treatment of lymphangiomas. [adc.bmj.com]

Tanrıverdi HA, Hendrik HJ, Ertan K, Axt R, Schmidt W (2001) Hygroma colli cysticum: prenatal diagnosis and prognosis. Am J Perinatol 18:415–420 PubMed CrossRef Google Scholar 13. [springerlink.com]

Prognosis The prognosis for cases of lymphangioma circumscriptum and cavernous lymphangioma is generally excellent. [knowcancer.com]

Prognosis/Outlook for Lymphangioma The prognosis for lymphangioma is excellent, but the outcome also depends on the size, type and the location of lymphangioma in the patient, some are as follows: Macrocystic lesions have the good prognosis for successful [epainassist.com]

Prognosis Excellent. lymphangioma A benign, often multiloculated lesion characterized by a localized proliferation of dilated lymphatics lined by benign endothelial cells Clinical May cause acute abdominal cysts, laryngeal masses, intraabdominal masses [medical-dictionary.thefreedictionary.com]

In these cases, the etiology is related to inadequate drainage of the lymphatic vessel into the venous system. Nuchal lymphangiomas are often associated with chromosome abnormalities. [nature.com]

The etiology is unknown, though some believe that it might be associated with developmental anomalies of the lymphatics. [ispub.com]

Descamps P, Jourain O, Paillet C et al (1997) Etiology, prognosis, counseling and management of nuchal cystic hygroma: 25 new cases and literature review. Eur J Obstet Gynecol Reprod Biol 71:3–10 PubMed CrossRef Google Scholar 15. [springerlink.com]

(Etiology) A Lymphangioma tumor develops when the lymphatic system gets obstructed due to various reasons, as the fetus grows The obstruction causes fluid to fill-up within the lymphatic channels, which then dilate. [dovemed.com]

[…] are also called lymphangiectasis Lymphangioma circumscriptum: the classic lesion appears at birth or in early years but most cases described in literature are postsurgery or radiation therapy See also Atypical or benign vascular lesion, postradiation Epidemiology [pathologyoutlines.com]

Well constructed epidemiologic studies determining the incidence of LC do not appear to exist, but lymphatic malformations occur in approximately 1.2 to 2.8 of every 1,000 live births in the United States. [clinicaladvisor.com]

Summary Epidemiology Prevalence is unknown. [orpha.net]

Epidemiology The incidence of LM is estimated to be one case per 6000-16,000 live births. Most LMs (50-65%) are evident at birth, and 80-90% of them present by age 2 years. [emedicine.com]

Etiology Pathophysiology Despite its superficial manifestations, LC is a problem of abnormal lymphatic vessels in the deep subcutaneous tissues. [clinicaladvisor.com]

Lymphangioma circumscriptum has a high recurrence rate after excision because of its deep component (see Pathophysiology ). Cavernous lymphangioma are also uncommon and usually arise during infancy. [emedicine.com]

Despite the rarity of breast cystic lymphangioma, its evaluation should be considered for prompt diagnosis and definitive treatment to prevent recurrence and complications. [ncbi.nlm.nih.gov]

Prevention of Lymphangioma There are no known preventive measures for lymphangioma as it is an infection that victims or patients are born with as such cannot be prevented, but can only be managed when discovered on time. [epainassist.com]