Symptoma

Lymphatic Malformation

In this study, we present a case report of a pediatric lymphatic malformation of the sphenoid sinus. [ncbi.nlm.nih.gov]

  • Soft Tissue Mass

    However, there are congenital and acquired, as well as benign and malignant, soft-tissue masses that can mimic them clinically and at imaging. [ncbi.nlm.nih.gov]

    Figure 1 (a) T1-weighted coronal view showing an intracoronal large serpiginous soft tissue mass involving the superior aspect of the right orbit (black arrow). [nature.com]

    From Wikipedia, the free encyclopedia Jump to navigation Jump to search Cystic lymphatic malformation Specialty Dermatology A Cystic lymphatic malformation is a deep-seated, typically multilocular, ill-defined soft-tissue mass that is painless and covered [en.wikipedia.org]

    The radiologic evaluation of a magnetic resonance imaging scan showed weighted MR images of the lumbar spine show a large soft tissue mass composed of large cysts that was most compatible with a lymphatic malformation.. [pediatriceducation.org]

  • Inguinal Hernia

    At birth the child was noted to have a right inguinal hernia with two palpable testicles. Plan for partial resection and hernia repair with postoperative sclerotherapy was made. [ncbi.nlm.nih.gov]

  • Pharyngitis

    To the authors' knowledge this is the first description of a submucosal coblation technique being used as treatment for pharyngeal LMs. Copyright 2013 Elsevier Ireland Ltd. All rights reserved. [ncbi.nlm.nih.gov]

    Pharyngeal cleft cysts should be carefully excluded. LMs of the floor of the mouth and tongue are usually microcystic and diffuse, and they usually have minimal or no contrast enhancement. [birthmarks.us]

  • Steatorrhea

    She did not have common symptoms of intestinal vascular and lymphatic malformation, such as gastrointestinal bleeding, steatorrhea, and hypoalbuminemia. [ncbi.nlm.nih.gov]

  • Pelvic Mass

    This case is different from the 3 cases reported before, for it is only presented with a palpable pelvic mass and the lesion did not penetrate full thickness of bladder. [ncbi.nlm.nih.gov]

  • Subcutaneous Mass

    Abstract OBJECTIVE: Palpable subcutaneous masses present in various shapes and sizes in the pediatric population and, accordingly, represent a variety of underlying causes. [ncbi.nlm.nih.gov]

  • Petechiae

    Examination under anesthesia and vaginoscopy showed a congested appearance of the hymen and vaginal petechiae. [ncbi.nlm.nih.gov]

  • Blepharoptosis

    All of the patients had excellent aesthetic improvement and corrected blepharoptosis. [ncbi.nlm.nih.gov]

    The extensive lesions typically cause swelling, intraorbital hemorrhage, ocular proptosis, blepharoptosis, and cellulitis. [ajnr.org]

  • Strabismus

    Amblyopia, astigmatism, and strabismus were not improved after treatment. All of the patients had excellent aesthetic improvement and corrected blepharoptosis. [ncbi.nlm.nih.gov]

    If it is localized around the eye, it may cause proptosis (push the eye forward), increased intraocular pressure, strabismus, diplopia and even vision loss. [texaschildrens.org]

    […] typically fluctuate in size with upper respiratory infections, and expand suddenly due to intralesional hemorrhage and infection. 3 – 7 Ocular complications include astigmatism, corneal exposure, hyperopia secondary to pressure on the posterior globe, strabismus [ajnr.org]

  • Miosis

    Twenty-one weeks after initial treatment, ophthalmic examination showed complete resolution of the blepharoptosis and pupillary miosis. [ncbi.nlm.nih.gov]

  • Chemosis

    OBJECTIVES: Periorbital microcystic lymphatic malformations (LM) can cause severe symptoms, such as blepharoptosis, amblyopia, chemosis, strabismus, diminished vision, and blindness. [ncbi.nlm.nih.gov]

    Selective arteriograms in 2 patients in our series with acute proptosis and chemosis showed direct filling of irregularly shaped cystic spaces from tiny branches of the ophthalmic artery ( Fig 7 ) at the sites where MR imaging revealed intensely enhancing [ajnr.org]

  • Unilateral Proptosis

    Prenatal ultrasound revealed prominence of the left orbital soft tissue, and at birth, the patient was noted to have unilateral proptosis, tortuous retinal vessels, and intraretinal hemorrhages in all 4 quadrants in the left eye. [ncbi.nlm.nih.gov]

  • Abnormal Gait

    We report two cases of giant LM with occasional high fever and pain or abnormal gait. To overcome dose limitation and to prevent systematic toxicities, we performed both injection of absolute ethanol and aspiration of it after 5 min exposure to LM. [ncbi.nlm.nih.gov]

  • Vaginal Bleeding

    Premenarchal vaginal bleeding can present a diagnostic challenge and has not been previously reported in association with congenital venous lymphatic malformation. A 3-year-old girl presented with intermittent vaginal bleeding since birth. [ncbi.nlm.nih.gov]

Examination and radiologic workup were consistent with a veno-lymphatic malformation, including demonstration of cystic fluid-fluid levels on imaging. [ncbi.nlm.nih.gov]

Genioplasty Indications horizontal mandibular excess or asymmetry, need for mandibular advancement Contraindications co-morbidities increasing surgical risk Setup supine, nasal intubation, general anesthesia, Inferior alveolar nerve block Preoperative Workup [csurgeries.com]

Click here to go to a related article (Appropriate Diagnostic Workup for Birthmarks). [birthmarks.us]

[…] histological features of lung specimens from nine patients in whom no extrathoracic lesions were identified, which they termed “diffuse pulmonary lymphangiomatosis” (DPL). 3 Recognition of the disease requires a high index of suspicion and an extensive workup [lgdalliance.org]

  • Multilocular Cyst

    They present with either generalized edema and poorly defined borders (microcystic) or a localized area of multilocular cysts (macrocystic). [ncbi.nlm.nih.gov]

It is very rare at birth and its treatment remains controversial. [ncbi.nlm.nih.gov]

Surgical excision is ideal to treat LM, and the prognosis is good. Although asymptomatic horseshoe kidney need not be treated, it is important for patients to receive regular follow-up because of the propensity for various complications. [ncbi.nlm.nih.gov]

Generally, as the stage increases the prognosis for cure decreases. It is also generally true that facial and oropharyngeal involvement are associated with a worse prognosis. [childrensenthouston.com]

The prognosis of primary lymphedema of the lower limbs. Arch Surg. 1981. Google Scholar 15. Williams WH, McNeill GC, Witte MH, et al. Evaluation of peripheral lymphedema by longitudinal lymphangioscintigraphy. Lymphology. 2002;35. Google Scholar 16. [link.springer.com]

It is also generally true that facial and oropharyngeal involvement are associated with a poor prognosis. [edmondsmd.com]

Stridor in a neonate evokes a series of prompt evaluations to determine the etiology. Common etiologies include inherent structural defects (such as laryngomalacia), vocal fold paralysis, acquired infectious etiologies, or extrinsic compressions. [ncbi.nlm.nih.gov]

A short review of epidemiology, clinical manifestation and treatment is given. [ncbi.nlm.nih.gov]

Summary Epidemiology Prevalence is unknown. [orpha.net]

Epidemiology Frequency Lymphatic VMs are the most common bases for macrocheilia, macroglossia, macrotia, and macromelia. [3] Combined lymphaticovenous malformation (LVM) occurs particularly in the craniofacial region. [4] Etiology The vascular system [emedicine.medscape.com]

Neurofibroma Lymphoproliferative Lymphoma Langherhans cell histiocytosis Xanthogranuloma Mesenchymal Rhabdomyosarcoma Fibrous histiocytoma Meningioma Optic nerve glioma Neurofibroma Metastasis Lung, Breast, Prostate Neuroblastoma Leukemia Summary Chart Epidemiology [eyerounds.org]

Discussion Epidemiology Lymphangiomas account for about 5% of benign tumors seen in infants and children. 1,2 The sites most commonly involved are the neck (75%) and axillae (20%). 3,4 Less than 1% of lymphangiomas are found in the gastrointestinal tract [gastroenterologyandhepatology.net]

The purpose of this study was to determine the natural progression of LMs to facilitate patient counseling, gain insight into pathophysiology, and guide therapy. [ncbi.nlm.nih.gov]

An analysis of thirty cases of orbital lymphangioma: pathophysiologic considerations and management recommendations. Ophthalmology 1990; 97 : 1583–1592. 4. Suzuki Y, Obana A, Gohto Y, Miki T, Otuka H, Inoue Y. [nature.com]

The pathophysiology of lymphedema. Cancer. 1998. Google Scholar 13. Papendieck CM. Lymphangiomatosis and dermoepidermal disturbances of lymphangioadenodysplasias. Lymphology. 2002;35. Google Scholar 14. Wolfe JH, Kinmonth JB. [link.springer.com]

A study by Yan et al found a significant increase in VEGF-C and neuropilin 2 in patients with recurrent lymphatic VM microcystic lesions, compared with individuals with nonrecurrent lesions. [8] Pathophysiology See Etiology section above. [emedicine.medscape.com]

Pathophysiologic considerations and management recommendations. Ophthalmology. 1990 Dec;97(12):1583-92. PubMed PMID: 2087290. Sires BS, Goins CR, Anderson RL, Holds JB. Systemic corticosteroid use in orbital lymphangioma. [eyerounds.org]

To overcome dose limitation and to prevent systematic toxicities, we performed both injection of absolute ethanol and aspiration of it after 5 min exposure to LM. [ncbi.nlm.nih.gov]

Since a lymphatic malformation will never go away on its own, expert treatment is required to heal this condition, prevent infection and prevent complications. [spectrumhealth.org]