Presentation
Patients may present with sepsis or metastatic spread of septic emboli, most commonly occurring in the lung. This presentation may appear as acute respiratory distress syndrome (ARDS). [emedicine.medscape.com]
The spleen may be missing (asplenia), or be present as multiple small spleens, rather than a single (polyspenia). [rarediseases.org]
Neurologic
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Trigeminal Neuralgia
Rarely, they may have pain similar to that of trigeminal neuralgia. Spontaneous rupture of a carotid-cavernous aneurysm leads to an abrupt onset of a direct C-C fistula. [emedicine.medscape.com]
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Neuralgia
Rarely, they may have pain similar to that of trigeminal neuralgia. Spontaneous rupture of a carotid-cavernous aneurysm leads to an abrupt onset of a direct C-C fistula. [emedicine.medscape.com]
Treatment
Standard Therapies Treatment No curative treatment is currently available for Meckel syndrome which has a constantly fatal outcome due to renal failure and lung hypoplasia. Treatment is symptomatic and supportive. [rarediseases.org]