As michel's aplasia is associated with LAMM syndrome there will be Microtia and microdontia present (small sized teeth). [en.wikipedia.org]

In his summary he describes "a case of complete absence of the inner ear (Michel deformity) is presented," while in the preceding case description (page 603), he says "the vestibule and lateral semicircular canal made up one large [jamanetwork.com]

• Disability

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• Ear Deformity

  Michel inner ear deformity is a rare developmental anomaly refers to the total aplasia of the inner ear. It is caused by developmental arrest of otic placode early during the third week of gestational age. [semanticscholar.org]

  Common cavity inner ear deformity. Kavanagh KT, Magill HL. Kavanagh KT, et al. Pediatr Radiol. 1989;19(5):343-5. doi: 10.1007/BF02467313. Pediatr Radiol. 1989. PMID: 2755750 Review of congenital inner ear abnormalities on CT temporal bone. [pubmed.ncbi.nlm.nih.gov]

Treatment[edit] enrollment in appropriate early intervention programs for the deaf and hard of hearing. consideration of vibrotactile hearing devices or brain stem implants for individuals with Congenital labyrinthine aplasia Evaluation for cochlear implantation [en.wikipedia.org]

Appropriate Imaging Modality for the Etiologic Diagnosis of Congenital Single-Sided Deafness in Children. Lee SY, Kim SH, Bae YJ, Kim EH, Koo JW, Choi BY. Lee SY, et al. J Clin Med. 2018 Dec 4;7(12):515. doi: 10.3390/jcm7120515. J Clin Med. 2018. [pubmed.ncbi.nlm.nih.gov]

Epidemiology[edit] Michel aplasia is a rare disease. It was first described by P. Michel in the year 1863. [en.wikipedia.org]

Prevention (of secondary complications)[edit] Presence of inner ear abnormalities lead to Delayed gross development of child because of balance impairment and profound deafness which increases the risk of trauma and accidents. [en.wikipedia.org]