Presentation
CONCLUSIONS: Myotonic dystrophy type 1 presents several particularities to the anesthesiologist. [cyberleninka.org]
Cardiovascular
- Tachycardia
Cardiac involvement: It is represented mainly by deterioration of the conduction system of the heart, tachycardias, cardiomyopathy, and valve diseases7. [cyberleninka.org]
- Heart Disease
They are multisystemic diseases clinically characterized by a combination of myotonia and other muscular symptoms (muscle weakness, wasting and myalgia) together with the involvement of other organs and systems (cataract, diabetes, heart diseases, hormone [ncbi.nlm.nih.gov]
Musculoskeletal
- Myalgia
They are multisystemic diseases clinically characterized by a combination of myotonia and other muscular symptoms (muscle weakness, wasting and myalgia) together with the involvement of other organs and systems (cataract, diabetes, heart diseases, hormone [ncbi.nlm.nih.gov]
Ears
- Hearing Impairment
Rev-Neurol-(Paris). 2001 Feb; 157(2): 209-18 Bonsch,-D; Scheer,-P; Neumann,-C; Lang-Roth,-R; Seifert,-E; Storch,-P; Weiller,-C; Lamprecht-Dinnesen,-A; Deufel,-T A novel locus for autosomal dominant, non-syndromic hearing impairment (DFNA18) maps to chromosome [malattierare.regione.veneto.it]
Neurologic
- Apathy
Obsessive-compulsive and passive-aggressive behaviors, as well as apathy and depression, are common in patients with MD. Mental retardation can be seen in 60% of the congenital types of MD, affecting severely all measures of general intelligence. [cyberleninka.org]
Treatment
Therefore, those patients should be followed continuously, paying special attention for cardiovascular manifestations to make the best treatment decisions, and especially for the choice of anesthetic technique and drugs. [cyberleninka.org]
Prognosis
Prognosis depends mainly on the cardiac and respiratory repercussions. Muscular involvement: Myotonia can be seen in several neuromuscular disorders. [cyberleninka.org]
Prevention
Besides, sedation is required to prevent the discomfort of the tracheal tube. This can prolong the recovery time of the respiratory function. [cyberleninka.org]