Generally presents at birth or within the first few years of life, but may affect any age group. There is no evidence of familial predisposition1. [jemds.com]

Nasal obstruction, cerebrospinal fluid rhinorrhoea and meningitis are the usual presentations in nasal location [2] while extranasal masses have a less predictable presentation. [neurologyindia.com]

Gliomas are locally aggressive lesions usually presented at birth, and 90% of cases are diagnosed by age of 2 years. [jpss.eu]

Extranasal gliomas clinically present in early infancy or childhood as a firm, red to bluish skin-covered mass. [radiopaedia.org]

A 25-day-old baby boy presented to our hospital with a midline swelling over his nose and upper lip. The swelling had been present since birth but did not cause any nasal obstruction or epistaxis. [jiaps.com]

• Pathologist

  College of American Pathologists 2000 Sponsored Video Citing articles via Latest Most Read Most Cited Validating Whole Slide Imaging Systems for Diagnostic Purposes in Pathology: Guideline Update From the College of American Pathologists in Collaboration [meridian.allenpress.com]

  […] interdisciplinary approach to the diagnosis, treatment, and management of head and neck diseases, including the incidence, etiology, clinical presentation, pathology, differential diagnosis, and prognosis for each disorder-promoting clear communication between pathologists [books.google.it]

  ‘Nasal gliomas’ and related brain heterotopias: a pathologist's perspective. Pediatr Pathol 1986 ; 5 : 353 –62 29 Rahbar, R, Resto, VA, Robson, CD, Perez-Atayde, AR, Goumnerova, LC, McGill, TJ et al. [cambridge.org]

• Swelling

  CASE 2: A 6 months old girl presented with swelling over root of nose .Clinically diagnosed as nasal dermoid or hamartoma. X-ray revealed a soft tissue swelling over the root of the nose with no calcification. Underlying bone appeared normal. [jemds.com]

  A 25-day-old baby boy presented to our hospital with a midline swelling over his nose and upper lip. The swelling had been present since birth but did not cause any nasal obstruction or epistaxis. [jiaps.com]

  This swelling was covered by bluish red colored skin. The swelling gradually increased to attain the size of about 5 x3cms at the time of presentation. The other biochemical investigations were within normal limits. [ijri.org]

  A 2-year-old male child was brought to our hospital with a history of swellings on both sides of the nasal bridge since birth. The swellings were said to be increasing in size gradually, but there was no associated change in size with crying. [ojoonline.org]

• Crying

  Because they have an intracranial connection, there is pulsation and expansion of the mass with crying, straining, or compression of the jugular vein (Furstenberg test).[3] In our patient, the mass showed no pulsation and expansion during crying or straining [jcasonline.com]

  The mass exhibited no pulsation and expansion during crying or straining. The patient's nasal passages were patent. [journals.lww.com]

  This mass showed no growth or change in size during crying or jugular vein compression… CONTINUE READING [semanticscholar.org]

  The mass does not increase in size with crying and does not transilluminate(2,6). [jemds.com]

• Surgical Procedure

  We suspected that the force of the surgical procedure was transmitted intracranially, causing the frontal lobe cerebral hemorrhage, near the bone defect. He recovered from the cerebral hemorrhage without dyskinesia. [hindawi.com]

  Unlike surgical approaches, evaluation with imaging methods is necessary for the differentiation before the excision procedure of the mass. [jpedres.org]

• Inflammation

  LYMPHOPLASMCYTIC inflitrate, dense hyaline fibrosis, atrophy of background parenchyma, infiltration of surrounding tissue can mimic something worse, marked PERIDUCTAL inflammation and duct stenosis, seen here, vascular thrombi, eos, and many IgG4 positive [pinterest.es]

  The underlying etiology may be inflammation, chronic fungal sinusitis, benign neoplasm, inverted papilloma, or malignant tumor. A radiological evaluation is mandatory to assess the site, extent, and enhancement effect of the lesion. [hindawi.com]

• Skin Disease

  Explore a range of neoplastic and non-neoplastic disorders of the skin. Access well-rounded, comprehensive coverage and detailed discussions of metabolic, systemic, allergic, infectious, and inflammatory skin diseases and cutaneous neoplasms. [books.google.it]

• Strabismus

  B 26455258 2015 30 Nasal heterotopia versus pilocytic astrocytoma: A narrow border. 62 Ellouze N...Piette C 26072230 2015 31 A case of nasal glial heterotopia with complete excision. 62 On HR...Chung KY 25771835 2015 32 Nasal glioma presenting with strabismus [malacards.org]

  The leading symptom was nasal congestion (41% of all NGH cases) although it can also appear in form of rhinorrhoea, epistaxis, meningitis, chronic rhinosinusitis and strabismus (8%). [actaitalica.it]

• Epistaxis

  A 37-year-old man was seen with right nasal obstruction, epistaxis, and headache. Imaging showed a radiologically malignant mass lesion. Biopsy and subsequent resection were performed in the evaluation and treatment of this lesion. [experts.umich.edu]

  They can cause: obstruction of the nasal passage respiratory compromise in infants obstruction of the nasolacrimal duct, with resultant epiphora cerebrospinal rhinorrhea meningitis epistaxis Nasal gliomas are composed of dysplastic glial tissue and are [radiopaedia.org]

  The intranasal glioma may present with nasal obstruction, epistaxis or nasal deformity and usually arise from the lateral nasal wall (on examination an intranasal encephalocele arises medially). [jemds.com]

  The swelling had been present since birth but did not cause any nasal obstruction or epistaxis. The baby also had an associated cleft palate [Figure 1]. He was born at full-term and had a normal vaginal delivery. [jiaps.com]

• Suggestibility

  Even laminated cerebral cortex with neurones and ependymal canals, suggestive of encephalocele, were found in heterotopias. Distinction required radiological and surgical evidence. [tandfonline.com]

  Histopathology revealed mature glial tissue with multinucleate glial cells in the dermis suggesting a diagnosis of glial heterotopia. [jemds.com]

  Suggested Reading Fletcher et al (2013) WHO classification of tumours of soft tissue and bone, 4th ednGoogle Scholar Copyright information © The Editor(s) (if applicable) and The Author(s), under exclusive license to Springer Nature Switzerland AG 2021 [link.springer.com]

  The presence of these findings highly suggests an encephalocele. Treatment is complete resection of the lesion. Incomplete resection results in recurrence of the lesion. [brown.edu]

  The MRI performed at 6 weeks of life suggested glial heterotopia. This diagnosis was confirmed by the pathological analysis. Congenital hemangiomas and nasal glial heterotopies have similar clinical presentations. [em-consulte.com]

• Meningism

  Any of these lesions can be associated with a cerebrospinal fluid (CSF) leak so that the biopsy must be avoided because of meningitis risk. [jpss.eu]

  Nasal obstruction, cerebrospinal fluid rhinorrhoea and meningitis are the usual presentations in nasal location [2] while extranasal masses have a less predictable presentation. [neurologyindia.com]

  8 days, developed delayed postoperative bacterial meningitis at 9 months. [casereports.bmj.com]

  However, they are different and have to be differentially diagnosed because the patients with encephalocele have the potential risk for meningitis. [jemds.com]

The preoperative workup as well as perioperative steps for excision are documented, with the hope that this will assist other practitioners with this approach... [read.qxmd.com]

The preferred treatment for NGH is complete surgical excision. [journals.lww.com]

The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. [orpha.net]

Surgical treatment is the best choice and should be performed on clinically stable patients. [humpath.com]

Scrupulous preoperative evaluation and sufficient diagnostic modalities must be pursued in order to arrive a correct diagnosis, treatment plan and prevent possible complications especially those related to intracranial communication. [pjohns.pso-hns.org]

Treatment and prognosis Once the diagnosis of a nasal glioma is established, early surgical resection is advocated to prevent local recurrence, nasal deformity, and secondary visual involvement 3. Surgical resection is often curative 1. [radiopaedia.org]

[…] this highly lauded three-volume reference provides an interdisciplinary approach to the diagnosis, treatment, and management of head and neck diseases, including the incidence, etiology, clinical presentation, pathology, differential diagnosis, and prognosis [books.google.it]

[…] displaced normal, mature glial tissue (choristomas) Continuity with intracranial component usually obliterated Encephalocele represents herniation of brain tissue and leptomeninges through defect of skull Continuity with cranial cavity is maintained ETIOLOGY [basicmedicalkey.com]

Updated, reorganized, and revised throughout, this highly lauded three-volume reference provides an interdisciplinary approach to the diagnosis, treatment, and management of head and neck diseases, including the incidence, etiology, clinical presentation [books.google.it]

Recurrences or more correctly persistence may be seen in up to 30% of patients if not completely excised.[2] Epidemiology[edit] Nasal glial heterotopia is rare, while an encephalocele is uncommon. [en.wikipedia.org]

Nasal encephaloceles: a review of etiology, pathophysiology, clinical presentations, diagnosis, treatment, and complications. Childs Nerv Syst 2013;29:739-44. DOI: https://doi.org/10.1007/s00381-012-1998-z Van Wyhe RD, Chamata ES, Hollier LH. [pediatrmedchir.org]

Pathophysiology Cutaneous ectopic brain (CEB) may be an isolated embryonic rest or a congenital herniation through the skull with an eventual loss of connection. [emedicine.medscape.com]

Nasal encephaloceles: a review of etiology, pathophysiology, clinical presentations, diagnosis, treatment, and complications. Childs Nerv Syst 2013;29:739–44. [14]. McDonald WS, Zagzag D, Thorne CH. [journals.lww.com]

Nasal encephaloceles: A review of etiology, pathophysiology, clinical presentations, diagnosis, treatment, and complications. Childs Nerv Syst. 2013;29:739-744. 11. McDonald WS, Zagzag D, Thorne CH. [mednexus.org]

They emphasize the importance of detailed prenatal investigation as most important in preventing birth trauma and consequent complications. [nel.edu]

The authors emphasize the importance of preoperative assessment in order to prevent the intracranial complications. The authors report the case of 25 days-old girl with a mass on the dorsum and left wall of the nose, presented since birth. [jpss.eu]

Treatment and prognosis Once the diagnosis of a nasal glioma is established, early surgical resection is advocated to prevent local recurrence, nasal deformity, and secondary visual involvement 3. Surgical resection is often curative 1. [radiopaedia.org]

Scrupulous preoperative evaluation and sufficient diagnostic modalities must be pursued in order to arrive a correct diagnosis, treatment plan and prevent possible complications especially those related to intracranial communication. [pjohns.pso-hns.org]