Otosclerosis is a common cause of hearing impairment.
Hearing loss is the primary sign of otosclerosis. In the preliminary stages, the individuals suffer from partial hear loss which gets worse over time and results in complete deafness. In addition to it, the condition presents itself with the following signs and symptoms:
Entire Body System
- Surgical Procedure
Advances in cochlear implant technology and coding strategies have led to developments in different surgical procedures to manage cochlear ossification. [ncbi.nlm.nih.gov]
Treatments The hearing can be restored with a surgical procedure called stapedectomy. Hearing aids can be helpful in patients who do not desire surgical treatment. [texasearcenter.com]
Morphological investigations of the otosclerotic focus show all three phases of a chronic inflammation with bone resorption, formation of new bone and finally eburnation. Various hypotheses about the cause of inflammation were proposed in the past. [ncbi.nlm.nih.gov]
Nervous System Puts the Brakes on Inflammation March 1, 2018 Cells in the nervous system can “put the brakes” on the immune response to infections in the gut and lungs to prevent excessive inflammation, according to research by Weill Cornell Medicine [nycornell.org]
Learn More About Topic Swimmer's Ear Swimmer’s ear (also called acute otitis externa) is a painful condition that affects the outer ear and ear canal that is caused by infection, inflammation, or irritation. [entnet.org]
CONCLUSION: There is weak evidence from one study with significant limitations that deterioration of hearing loss in otosclerosis patients receiving sodium fluoride treatment is less than in patients treated with a placebo. [ncbi.nlm.nih.gov]
Weakness of the Face A very rare complication of stapedectomy is temporary weakness of the face. This may occur as the result of an abnormality or swelling of the facial nerve. [michiganear.com]
In a series of 700 stapedectomies, only 2 patients had facial weakness; both were of delayed onset (around postoperative day [POD] 5), and both completely resolved within 2 weeks with steroid administration. [emedicine.medscape.com]
Notify our office immediately if any of the following occurs: Sudden hearing loss Intense pain Prolonged or intense dizziness Facial weakness Packing is placed in the ear at the time of surgery, so hearing improvement will not be noticed until it is removed [dariuskohanmd.com]
Learn more about arthritis and other health issues in our Women's Health Center. Comprehensive women's health information provided by MerckSource.com. Learn more about arthritis and other health issues in our Women's Health Center. [web.archive.org]
Patients with chronic rheumatoid arthritis 3. Patient who are pregnant / lactating 4. In children before skeletal growth has been completed 5. Patients who show allergy for the drug 6. [drtbalu.co.in]
People with stomach problems, significant arthritis, and kidney disease should not take fluorical. Pregnant women and children should not take fluorides. [earcentergreensboro.com]
There are numerous side-effects to these Medical treatments, including occasional stomach upset, allergic itching, and increased joint pains which can lead to arthritis.  Famous patients Edit The renowned German composer Beethoven was theorized to [psychology.wikia.com]
Molecular genetic testing is useful to differentiate otosclerosis from syndromic stapes ankylosis. Congenital stapes ankylosis is genetically heterogeneous. [ncbi.nlm.nih.gov]
Pathological condition of the bony labyrinth of the ear, in which there is formation of spongy bone; may cause bony ankylosis of the stapes, resulting in conductive hearing loss; cochlear otosclerosis may also develop, resulting in sensorineural hearing [icd9data.com]
The otosclerotic focus may be asymptomatic, or if present in the area of foot plate of stapes it may give rise to ankylosis of foot plate with resultant conductive deafness. [drtbalu.co.in]
OBJECTIVE: Otosclerosis and osteoporosis are metabolic bone diseases. In this paper, we investigated presence of osteoporosis with bone mineral density test in patients who had surgery for otosclerosis. [ncbi.nlm.nih.gov]
NIH Consensus Development Panel on Osteoporosis Prevention, Diagnosis, and Therapy. Osteoporosis prevention, diagnosis, and therapy. 2001. JAMA. 285:785-95. [dizziness-and-balance.com]
Biphosphonates such as Didronel (Etidronate Diaxodium), used for osteoporosis, has been utilized by some to regulate bone metabolism in the medical management of otospongiosis. [newyorkear.com]
CONCLUSION: Low pitch tinnitus is more likely to be resolved after stapedotomy for patients with otosclerosis. High pitch tinnitus may not resolve even after closure of the Air-Bone Gap at tinnitus frequencies. [ncbi.nlm.nih.gov]
Also, see eMedicineHealth's patient education article Tinnitus. [emedicine.medscape.com]
- Hearing Impairment
Hearing Impairment from Otosclerosis If we were able to examine the inner ear bone under a microscope before a hearing impairment developed, we would see minute areas of both softening and hardening of the bone. [epichearing.com]
If you feel a significant degree of hearing impairment following stapedectomy, revision surgery can be performed with good odds of success. [hillsent.com.au]
Types of Hearing Impairment The external ear and the middle ear conduct sound; the inner ear receives it. If there is some difficulty in the external or middle ear, a conductive hearing impairment occurs. [michiganear.com]
Otosclerosis is caused by an abnormal bone homeostasis of the otic capsule and represents a frequent cause of hearing impairment. [ncbi.nlm.nih.gov]
- Progressive Hearing Loss
This far-advanced otosclerosis often presents with a family history of hearing loss or a gradually progressive hearing loss that starts early in adult life. [emedicine.medscape.com]
Patients complain on progressive hearing loss and tinnitus. The diagnosis is made clinically by conventional audiologic evaluation and radiologically by x-ray mastoid Schuller's view and CT scan. [ncbi.nlm.nih.gov]
- Hearing Problem
The condition may not need to be treated until you have more serious hearing problems. Using some medicines such as fluoride, calcium, or vitamin D may help to slow the hearing loss. [nlm.nih.gov]
Extensive hearing tests will confirm the diagnosis. Treatment People with otosclerosis often benefit from a properly fitted hearing aid. The surgical replacement of the stapes has become a common procedure to improve conductive hearing problems. [encyclopedia.com]
With over 16 years of experience serving patients in the Orange County and Long Beach area, we are proud to offer all of our patients a complete, all-in-one solution to any hearing problem or medical related ear condition. [eardoctor.org]
Hearing Loss Genetic Hearing Loss Noise Induced Hearing Loss Bilateral Hearing Loss Unilateral Hearing Loss Conductive Hearing Loss High Frequency Hearing Loss Low Frequency Hearing Loss Sensorineural Hearing Loss Hearing Problems Fungal Ear Infections [hiddenhearing.co.uk]
Bedside: The otologic clinician should confirm audiological testing suggesting a conductive hearing loss with bedside examination. [dizziness-and-balance.com]
Suggested mechanisms include end-organ or neural degeneration or biochemical derangement in the perilymph by contact of the disease process. [emedicine.medscape.com]
Some authors have suggested an inflammatory etiology for otosclerosis resulting from persistent measles virus infection involving the otic capsule. [ncbi.nlm.nih.gov]
Patients sometimes experience dizziness and nausea after stapedectomy surgery. Some mild unsteadiness and brief dizziness with head turning is not uncommon. If dizziness is marked, do not get up without assistance. [tampabayhearing.com]
[…] have hearing loss You develop fever, ear pain, dizziness, or other symptoms after surgery Otospongiosis; Hearing loss - otosclerosis House JW, Cunningham CD. [nlm.nih.gov]
The post-operative course was uneventful in 12 of 14 cases with no EH in the vestibule, and the other two cases had a short period of dizziness, but two cases with EH in the vestibule had a long period of dizziness. [ncbi.nlm.nih.gov]
METHODS: Fifty otosclerosis patients comprising 27 patients with vertigo (Group A) and 23 patients without vertigo/dizziness (Group B) were enrolled. [ncbi.nlm.nih.gov]
The study, of 140 patients with otosclerosis who underwent stapedial surgery, found that, while 12 patients [8.6%] reported having vertigo prior to surgery and no vertigo after the operation, 36 patients [25.7%] who had no vertigo before surgery reported [emedicine.medscape.com]
Ossification may occur as a consequence of the pathology of meningitis, chronic otitis media, severe otosclerosis, autoimmune inner ear diseases, temporal bone traumas, and other diseases. [ncbi.nlm.nih.gov]
Infection is rare and must be identified and treated early to avoid profound sensorineural hearing loss, meningitis, and a prolonged hospital course. [emedicine.medscape.com]
Infection: Luckily rare, a post-operative infection after stapedotomy can lead to profound hearing loss and, in rare cases, meningitis. The latter occurs when bacteria transgress the vestibule to enter the CSF-containing subarachnoid space. E. [audiologyonline.com]
1878– Kessel—first successful stapes surgery 1890– Miot reported a series of 200 stapes mobilization surgery 1900 Politzer and Siebenmann condemned stapes surgery because of potential risk to cause meningitis 1916-- Gunnar Holmgren Father [slideshare.net]
A normal examination of the ear using auriscope would usually not show any abnormalities. Individuals should therefore visit an ENT specialist to get a differential diagnosis done. Specialized instruments such as tympanometer would help to evaluate the movement of the bones inside the middle ear. This is usually a painless procedure and yields quick results.
In certain conditions, imaging studies of the head may also be required, such as temporal bone computed tomography . Temporal bone computed tomography can further be enhance with the use of 18F-fluoride positron emission tomography to elucidate bone metabolism of the inner ear . The relative hypodensity in otosclerosis of the round window during CT scan can help surgeons in counselling and in deciding whether to proceed for surgical stapedectomy .
In the preliminary stages, the hearing loss is mild and does not require any treatment. However, over a time of time, the condition can worsen and individuals are then immediately put on treatment. The following are the several methods employed for treating otosclerosis:
- Hearing aids are meant for treating moderate hearing loss. But, when the condition turns severe then hearing aids are not of much help.
- Supplements of fluoride, calcium and vitamin D can be of some help in slowing down the progression of the disease . However, not enough research has been conducted in this regard and efficacy of nutritional supplements is yet to be proved.
- Surgery is often the treatment of choice to restore hearing ability. In this, the part of the ear known as stapes is replaced by prosthesis which can restore hearing function. In many cases, a total replacement may be required and such a procedure is known as stapedectomy . Operative intervention of the middle ear may require local or general anesthesia with sedation . Individuals often recover well with surgery and hearing ability is restored . This is however a very delicate operative procedure and in certain cases can even damage the neighboring nerves calling for complications. The risk though small, can contribute towards development of unpleasant conditions.
- Advances in ear surgery has implored the use of endoscopic surgery to significantly lower risk and morbidity .
If prompt treatment is not initiated then the condition may worsen over a period. Individuals can suffer from total deafness for the rest of the life. Surgical procedures can be carried out to restore the hearing function to certain extent; but may not always be successful.
Possible complications of otosclerosis include the following conditions:
The exact cause that triggers such an abnormal bone remodeling mechanism is unknown. However, there have been some pieces of evidence suggesting that otosclerosis is an inherited condition and can be passed from one generation to other. In otosclerosis the bone remodeling function is disrupted as a result of which the sound waves are unable to travel to the inner ear from the middle ear. Such a condition causes hearing loss.
Some other theories point towards the fact that otosclerosis develops as a result of measles virus. The exact theory states that individuals may be born with certain kind of genetic defect and a viral infection may further trigger the onset of the disorder. In addition to this, low levels of fluoride can also have some kind of link with development of otosclerosis.
Otosclerosis is a common condition affecting about 3 million Americans. Women are more prone to contract this condition than males. This condition is often diagnosed in mid adulthood and is a common cause of hearing loss amongst the young adult population. It has also been estimated that Caucasians are more affected by this disease condition than individuals of other regions.
Under normal conditions, for individuals to be able to hear, sound waves must travel from the middle ear to the inner ear. Such sequence of events does not take place in otosclerosis due to an abnormal bone growth in the middle ear.
Bone remodeling is an ongoing process wherein the bone tissues are periodically renewed by replacing the old with new. However, due to abnormal remodeling such an activity does not take place and the sound waves are unable to travel to the inner ear. There is an observable fixation of stapes ossicle to the oval window causing a disruption in the sound transmission . Otosclerosis can affect one or both ears.
It is not possible to prevent otosclerosis. It is a genetic defect that occurs spontaneously thus making it difficult to prevent the development of such a disease condition. However, there have been small pieces of evidence suggesting fluoride tablets and measles vaccination as preventive measures against otosclerosis. There is still dearth of information in this regard, and more research needs to be carried out.
Otosclerosis is a condition characterized by abnormal development of bone in the middle ear. Such a condition can contribute to hearing loss and other associated abnormalities. It is a serious condition demanding prompt diagnosis. Otosclerosis develops due to abnormal remodeling of the bone. Such an event interrupts the travelling of the sound waves from the middle ear to inner ear contributing to hearing loss. It is not an uncommon condition and affects millions of individuals across the globe.
Otosclerosis is a condition characterized by abnormal growth of bone in the middle ear region. This causes gradual ear loss which can lead to complete deafness over a period of time.
The exact cause that triggers the development of otosclerosis is unknown. However heredity and genetic factors are known to play foul. Researchers also believe that measles virus and low fluoride can also cause otosclerosis.
Diagnosis of otosclerosis is done using specialized instruments that can measure the activity of the bone inside the middle ear. Individuals need to consult an ENT specialist for appropriate diagnosis of the condition. In addition to this, CT scan of the head may also be required.
Individuals with mild hear loss do not usually require any treatment. Those with moderate hear loss require hearing aids to deal with the problem. However, in severe cases, hearing aids are of no help and surgical procedures are the only resort.
- Toynbee J. Pathological and surgical observations of the diseases of the ear. Trans Med Chir Soc Lond. 1841; 24:190-196.
- Jack FL. Remarkable improvement of hearing by removal of the stapes. Trans Am Otol Soc. 1893; 284:474-89.
- Virk JS, Singh A, Lingam RK. The role of imaging in the diagnosis and management of otosclerosis. Otol Neurotol. Sep 2013; 34(7):e55-60.
- Waterval JJ, Vallinga M, Brans B, Winkens B, Stokroos RJ. 18F-fluoride PET/CT scan for quantification of bone metabolism in the inner ear in patients with otosclerosis--a pilot study. Clin Nucl Med. 2013; 38(9):677-85
- Mansour S, Nicolas K, Ahmad HH. Round window otosclerosis: radiologic classification and clinical correlations. Otol Neurotol. 2011; 32(3):384-92
- Liktor B, Szekanecz Z, Batta TJ, Sziklai I, Karosi T. Perspectives of pharmacological treatment in otosclerosis. Eur Arch Otorhinolaryngol. 2013; 270(3):793-804
- Jack FL. Remarkable improvement of hearing by removal of the stapes. Trans Am Otol Soc. 1893; 284:474-89.
- Lempert J. Improvement in hearing in cases of otosclerosis: A new, one-stage surgical technic. Arch Otolaryngol. 1938; 28:42-97.
- Thomeer HG, Kunst HP, Cremers CW. Congenital stapes ankylosis associated with another ossicular chain anomaly: surgical results in 30 ears. Arch Otolaryngol Head Neck Surg. Sep 2011; 137(9):935-41.
- Kojima H, Komori M, Chikazawa S, Yaguchi Y, Yamamoto K, Chujo K, et al. Comparison between endoscopic and microscopic stapes surgery. Laryngoscope. May 13 2013.