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Pericardial Anomaly

Pericardium Defect


Presentation

  • Abstract Ebstein's anomaly is known for its varied presentations and exceptionally long survival in some cases.[ncbi.nlm.nih.gov]
  • […] as pain or heaviness in chest, difficulty in breathing or cough. 4,5 We present a case in a middle-aged man who presented with feeling of heaviness in chest.[pjms.com.pk]
  • Here the authors describe a case of previously undiagnosed Ebstein's anomaly in a patient who presented with massive pericardial effusion. Over the next 6 months, the patient was hospitalised twice for pericardiocentesis.[casereports.bmj.com]
  • The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly.[books.google.de]
Mediastinal Lymphadenopathy
  • There was no evidence of either hilar or mediastinal lymphadenopathy and no mass or consolidation was seen in both lungs (Fig-2).[pjms.com.pk]
Ascitic Fluid
  • Analysis of the ascitic fluid indicated that portal hypertension had caused the ascites. Although RHF could have caused it, we first had to ensure that it was not due to cirrhosis.[revespcardiol.org]
  • Ascites (fluid in abdomen) Pleural effusion (fluid in the pleural cavity, the fluid-filled space that surrounds the lungs) Pericardial effusion (fluid in the pericardial sac, covering that surrounds the heart) In addition, hydrops fetalis is frequently[perinatology.com]
  • Segmental hepatic dysfunction is thought to ooze out the ascitic fluid from the surface of liver .Ultimately severe raise of hepatic venous pressure results in congestive hepatomegaly and could result in now obsolete, cardiac cirrhosis.[drsvenkatesan.com]
Sepsis
  • He then had severe pulmonary sepsis that triggered death of the patient 1 week after the second procedure.[revespcardiol.org]
  • It has been reported in literature that such cysts can cause right main stem bronchus obstruction, pulmonary artery stenosis, ventricular outflow tract obstruction, sepsis, atrial fibrillation and cardiac temponade, all of which can prove to be fatal.[pjms.com.pk]
  • Acidosis Pediatric Metabolic Alkalosis Pediatric Respiratory Acidosis Pediatric Respiratory Alkalosis Pediatric Respiratory Failure Pediatric Status Epilepticus Pulmonary Infarction Shock in Pediatrics Traumatic Brain Injury in Children Treatment of Sepsis[klikdokterjantung.wordpress.com]
Pathologist
  • All clinicians and scientists interested in birth defects, including pediatricians, geneticists, genetic counselors, obstetricians, and pediatric pathologists, will find this book to be an invaluable source of information.[books.google.de]
Intermittent Fever
  • It was associated with low-grade intermittent fever and nonproductive cough for the last 20 days. The child's birth history was uneventful, with a birth weight of 2.8 kg, and he was fully immunized as per the schedule.[annalspc.com]
Flank Mass
  • The abdomen was of normal shape with no visceromegaly or flank masses.[pjms.com.pk]
Painful Cough
  • The child presented with chest pain, cough and fever. The preoperative diagnosis of pericardial cyst was suggestive on echocardiography and CT scan. It was confirmed on histopathology after successful surgical excision.[annalspc.com]
Jaundice
  • Shock in Pediatrics Traumatic Brain Injury in Children Treatment of Sepsis and Septic Shock in Children Neonatology Anemia of Prematurity Apnea of Prematurity Benign Neonatal Sleep Myoclonus Birth Trauma Bowel Obstruction in the Newborn Breast Milk Jaundice[klikdokterjantung.wordpress.com]

Workup

  • […] histological features of lung specimens from nine patients in whom no extrathoracic lesions were identified, which they termed "diffuse pulmonary lymphangiomatosis" (DPL). [4] Recognition of the disease requires a high index of suspicion and an extensive workup[en.wikipedia.org]
Left Pleural Effusion
  • A chest radiograph showed the presence of a left pleural effusion (Figure 1A) and the lateral view demonstrated a sharp line of pericardial calcification, indicating pericardial constriction (Figure 1B, arrow). Figure 1. Thoracic radiographs.[revespcardiol.org]
Pericardial Calcification
  • A chest radiograph showed the presence of a left pleural effusion (Figure 1A) and the lateral view demonstrated a sharp line of pericardial calcification, indicating pericardial constriction (Figure 1B, arrow). Figure 1. Thoracic radiographs.[revespcardiol.org]
Visceromegaly
  • The abdomen was of normal shape with no visceromegaly or flank masses.[pjms.com.pk]
Liver Biopsy

Treatment

  • The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly.[books.google.de]
  • Organellar and miscellaneous neurodegenerative disorders 413 Lysosomal enzyme deficiencies 414 mucopolysaccharidoses 420 Mitochondrial disorders 425 Peroxisomal diseases 430 Miscellaneous metabolic disorders 434 Metabolic dysplasias susceptible to dietary treatment[books.google.com]
  • […] hemidiaphragm Increased distance between sternum and heart 2 absence of sternopericardial ligament Lung may interpose between aorta and main pulmonary artery on axial CT scans Levoposition of heart Pneumopericardium may occur following pneumothorax Treatment[learningradiology.com]
  • The patient was counseled to get the cyst excised at the earliest but the patient refused surgical treatment due to personal reasons.[pjms.com.pk]
  • The various treatment modalities include percutaneous aspiration of cyst, ethanol sclerosis, surgical resection or video-assisted thoracoscopic surgery (VATS). [1], [4], [5] Currently, VATS is the approach most commonly used in practice. [4] It has many[annalspc.com]

Prognosis

  • Morbidity after cardiovascular surgery is much higher if the patient has cirrhosis, and the prognosis is influenced by the functional state of the liver disease.[revespcardiol.org]
  • Treatment and prognosis As the anomaly is of variable severity, so is the prognosis. Severity is related to the amount of RVOT dysfunction and tricuspid regurgitation. Sudden death from arrhythmia may occur.[radiopaedia.org]
  • When only the left coronary artery is anomalous, prognosis is relatively better. Again early death usually occurs from CHF & arrhythmia. Anomalous origin of the right coronary artery only carries the best prognosis.[cardiologyforyou.blogspot.com]
  • McElhinney DB, Silverman N (1999) Left ventricular aneurysm inthe fetus: a diagnosis with a mixed prognosis. Cardiol Young9: 123-126.[criticalcare.imedpub.com]

Etiology

  • The etiological study found no other causes in addition to those proposed a priori (alcohol and congestion), and the clinical, histopathological, and laboratory data indicated that congestion was the primary cause. 1 The echocardiogram still indicated[revespcardiol.org]
  • CT chest is used as a diagnostic tool to establish the etiology. In our patient the pericardial cavity was large; the sternal wound had grown Acinetobacter baumannii.[elynsgroup.com]
  • The etiology of these two t pes of congenital dextrocardia differs widely.[embryology.med.unsw.edu.au]
  • The pericardial effusion in our case was acquired and was tubercular in etiology.[heartviews.org]

Epidemiology

  • The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly.[books.google.de]
  • Epidemiology [ edit ] Lymphangiomatosis can occur at any age, but the incidence is highest in children and teenagers.[en.wikipedia.org]
Sex distribution
Age distribution

Pathophysiology

  • However, as all that glitters is not gold.. all restrictive pathophysiology is not a restrictive-infiltrative cardiomyopathy.. let’s understand why![escardio.org]
  • Pathophysiology: During fetal life: while PA pressure is higher than AO pressure, the anomalous coronary artery gets anterograde flow from PA.[cardiologyforyou.blogspot.com]
  • Based on this case report the clinical, pathophysiological and diagnostic features of this condition are described Pulmonary and systemic venous flow patterns assessed by transesophageal Doppler echocardiography in congenital absence of the pericardium[rwjms1.umdnj.edu]

Prevention

  • The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly.[books.google.de]
  • […] intervention Most authors advise leaving incidental defects untreated Symptomatic foraminal defect may require surgery because of herniation and strangulation of left atrial appendage or herniation of LA/LV Surgery can be enlargement of the defect to prevent[learningradiology.com]
  • The indications for resection of pericardial cysts are large size, symptoms, uncertainty of malignant potential and prevention of life-threatening emergencies.[annalspc.com]
  • Techniques to prevent arrhythmias and sudden death should be considered in some cases when large amounts of adjacent structures are removed during surgery. Acknowledgements None.[jtd.amegroups.com]
  • The indications for resection of pericardial cysts include large size, symptoms, patient concern, uncertainty of malignant potential, and prevention of the life threatening emergencies.[ctsnet.org]

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