Presentation
Abstract Ebstein's anomaly is known for its varied presentations and exceptionally long survival in some cases. [ncbi.nlm.nih.gov]
[…] as pain or heaviness in chest, difficulty in breathing or cough. 4,5 We present a case in a middle-aged man who presented with feeling of heaviness in chest. [pjms.com.pk]
The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly. [books.google.de]
Here the authors describe a case of previously undiagnosed Ebstein's anomaly in a patient who presented with massive pericardial effusion. Over the next 6 months, the patient was hospitalised twice for pericardiocentesis. [casereports.bmj.com]
Symptoms, if present, are usually because of compression by the cystic mass. [annalspc.com]
Cardiovascular
- Thrombosis
Case Report The patient is a 22-year-old African-American woman Gravida 3 Para 2 at 29 weeks gestation with past medical history significant for EA, ASD with right to left (R→L) shunting, protein S deficiency, previous history of deep venous thrombosis [ispub.com]
Coronary aneurysms, thrombosis or occlusions may occur. The risk of occlusion is 8% for >9mm aneurysms. Myocarditis, pericarditis, valvulitis or AV node conduction anomalies may also occur. Treatment is with gamma globulin and aspirin. [radiology.vlahos.org]
Thrombosis can occur, with occlusion of the parent artery or embolism downstream. They are also liable to rupture. Clinically: systolic & diastolic murmurs may be found. Symptomatic cases need CABG. [cardiologyforyou.blogspot.com]
Pulmonary thrombosis was suspected, but was not confirmed at autopsy, when the heart was found in the left pleura. The number of fatalities is high. Diagnosis This is difficult, but does not seem impossible. [embryology.med.unsw.edu.au]
Liver, Gall & Pancreas
- Jaundice
Shock in Pediatrics Traumatic Brain Injury in Children Treatment of Sepsis and Septic Shock in Children Neonatology Anemia of Prematurity Apnea of Prematurity Benign Neonatal Sleep Myoclonus Birth Trauma Bowel Obstruction in the Newborn Breast Milk Jaundice [klikdokterjantung.wordpress.com]
Workup
[…] histological features of lung specimens from nine patients in whom no extrathoracic lesions were identified, which they termed "diffuse pulmonary lymphangiomatosis" (DPL). [4] Recognition of the disease requires a high index of suspicion and an extensive workup [en.wikipedia.org]
Treatment
Nonsteroidal anti-inflammatory drug treatment for postoperative pericardial effusion: a multicenter randomized, double-blind trial. [clinicaltrials.gov]
Initial treatment shortly after birth may be necessary to treat a baby's cyanosis because of inadequate pulmonary artery blood flow. [pted.org]
[…] of Infections of the Lung, Pleura, and Mediastinum Surgical Treatment of Pediatric Hypoplastic Left Heart Syndrome Systemic to Pulmonary Artery Shunting for Palliation Tetralogy of Fallot With Pulmonary Stenosis The Fontan Procedure for Pediatric Tricuspid [klikdokterjantung.wordpress.com]
The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly. [books.google.de]
Organellar and miscellaneous neurodegenerative disorders 413 Lysosomal enzyme deficiencies 414 mucopolysaccharidoses 420 Mitochondrial disorders 425 Peroxisomal diseases 430 Miscellaneous metabolic disorders 434 Metabolic dysplasias susceptible to dietary treatment [books.google.com]
Prognosis
Treatment and prognosis As the anomaly is of variable severity, so is the prognosis. Severity is related to the amount of RVOT dysfunction and tricuspid regurgitation. Sudden death from arrhythmia may occur. [radiopaedia.org]
Morbidity after cardiovascular surgery is much higher if the patient has cirrhosis, and the prognosis is influenced by the functional state of the liver disease. [revespcardiol.org]
When only the left coronary artery is anomalous, prognosis is relatively better. Again early death usually occurs from CHF & arrhythmia. Anomalous origin of the right coronary artery only carries the best prognosis. [cardiologyforyou.blogspot.com]
McElhinney DB, Silverman N (1999) Left ventricular aneurysm inthe fetus: a diagnosis with a mixed prognosis. Cardiol Young9: 123-126. [criticalcare.imedpub.com]
Etiology
CT chest is used as a diagnostic tool to establish the etiology. In our patient the pericardial cavity was large; the sternal wound had grown Acinetobacter baumannii. [elynsgroup.com]
The etiological study found no other causes in addition to those proposed a priori (alcohol and congestion), and the clinical, histopathological, and laboratory data indicated that congestion was the primary cause. 1 The echocardiogram still indicated [revespcardiol.org]
The etiology of these two t^^pes of congenital dextrocardia differs widely. [embryology.med.unsw.edu.au]
The pericardial effusion in our case was acquired and was tubercular in etiology. [heartviews.org]
Epidemiology
The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly. [books.google.de]
Epidemiology [ edit ] Lymphangiomatosis can occur at any age, but the incidence is highest in children and teenagers. [en.wikipedia.org]
Pathophysiology
However, as all that glitters is not gold.. all restrictive pathophysiology is not a restrictive-infiltrative cardiomyopathy.. let’s understand why! [escardio.org]
Pathophysiology: During fetal life: while PA pressure is higher than AO pressure, the anomalous coronary artery gets anterograde flow from PA. [cardiologyforyou.blogspot.com]
Based on this case report the clinical, pathophysiological and diagnostic features of this condition are described Pulmonary and systemic venous flow patterns assessed by transesophageal Doppler echocardiography in congenital absence of the pericardium [rwjms1.umdnj.edu]
Prevention
The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly. [books.google.de]
[…] intervention Most authors advise leaving incidental defects untreated Symptomatic foraminal defect may require surgery because of herniation and strangulation of left atrial appendage or herniation of LA/LV Surgery can be enlargement of the defect to prevent [learningradiology.com]
Techniques to prevent arrhythmias and sudden death should be considered in some cases when large amounts of adjacent structures are removed during surgery. Acknowledgements None. [jtd.amegroups.com]
The indications for resection of pericardial cysts include large size, symptoms, patient concern, uncertainty of malignant potential, and prevention of the life threatening emergencies. [ctsnet.org]
The indications for resection of pericardial cysts are large size, symptoms, uncertainty of malignant potential and prevention of life-threatening emergencies. [annalspc.com]