Presentation
A literature review of the disease, including its controversial histiogenesis, treatment, and survival, is presented. In view of the rarity of the disease, only by studying more patients can we better understand the disease. [ncbi.nlm.nih.gov]
These people present with various skin lesions and rashes - most commonly on the thighs. Treatment aimed at the underlying condition hastens the resolution of the lesions. [en.wikipedia.org]
Histological and immunohistological investigations of the malignant form of AEPS are presented: In a 69-year-old woman cutaneous lesions appeared 5 months before the diagnosis of B-immunoblastic lymphoma. [unboundmedicine.com]
Entire Body System
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Lymphedema
Angiosarcoma arising in chronic lymphedema (syndrome of Stewart and Treves) may be histologically indistinguishable from Kaposi's sarcoma, but may also present with large pleo-morphic cells occluding the vessel lumina and resembling the cases described [docslide.net]
Epithelioid hemangioendothelioma Angiosarcoma Idiopathic (head and neck) Associated with chronic lymphedema (Stewart-Treves) Postirradiation Epithelioid 6. [slideshare.net]
Keywords: Lymphedema; Synovitis; Aspiration 1. Introduction Various dermatoses are associated with rheumatoid arthritis (RA), including rheumatoid nodules, rheumatoid vasculitis, and neutrophilic dermatoses. [file.scirp.org]
[…] homozygous familial hypercholesterolemia, hyperapobetalipoproteinemia, myxedema, obstructive liver d. xanthoma, tuberous hyperlipoproteinemia type II & III xanthomas atherosclerosis, biliary disease, CTCL, diabetes mellitus, hypothyroidism, leukemia, lymphedema [dermadvocate.net]
The diagnosis is massive localized lymphedema of the morbidly obese (and not liposarcoma). FIgure 4a. [orthopaedicsone.com]
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Turkish
Modern Hebrew Hindi Hungarian Icelandic Indonesian Kinyarwanda Korean Latin Latvian Lithuanian Macedonian Malayalam Maori Malay Multiple languages Norwegian Persian Polish Portuguese Pushto Romanian Sanskrit Serbian Croatian Slovak Slovenian Swedish Thai Turkish [entityextraction.net]
New Orleans, Louisiana 1999 Faculty, Fifth Annual Midwest Dermatopathology Workshop, Northwestern University, Chicago, Illinois 1999 Invited speaker, IIIrd Regional Clinicopathological Colloquium of the International and Turkish Societies of Dermatopathology [skinsurgerycenter.net]
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Vietnamese
Indonesian Kinyarwanda Korean Latin Latvian Lithuanian Macedonian Malayalam Maori Malay Multiple languages Norwegian Persian Polish Portuguese Pushto Romanian Sanskrit Serbian Croatian Slovak Slovenian Swedish Thai Turkish Ukrainian Undetermined Urdu Vietnamese [entityextraction.net]
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Collapse
MeSH term, type words from the biomedical concept you have in mind here: [transliterated title] And for this query matching the title in original language: [PMID] Show me only articles for these PMIDs (PubMed IDs): [shown] Results per page: [expand/collapse [entityextraction.net]
Cardiovascular
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Vascular Disease
In the case reported, there are three distinctive features which imply that this rare syndrome should be recognized as a pattern of vascular disease. (1) There was focal proliferation of cells, similar to neoplastic reticular cells, associated with the [academic.naver.com]
Cholesterol emboli Arteriovenous shunts Chronic lymphatic leukemia Monoclonal gammopathy Angiosarcoma The “diffuse dermal angiomatosis” variant of cutaneous reactive angiomatosis is usually associated with peripheral vascular disease / atherosclerosis [dermatologyadvisor.com]
Illustrated here from a biopsy of a patient with an unclassified collagen vascular disease presenting with nodules and livedo reticularis is a muscular vessel (artery) whose endothelium is disrupted by lymphocytes (endothelialitis) and media and adventia [vgrd.org]
Its basis is usually atherosclerotic vascular disease, cholesterol emboli, mural thrombi and rarely, fragmentation of intracardiac tumors. [docslide.us]
Skin
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Cutaneous Manifestation
[Systemic proliferative angioendotheliomatosis: a cutaneous manifestation of malignant B-cell lymphomas. Histologic and immunohistologic studies of two cases]. [unboundmedicine.com]
Seminars in Diagnostic Pathology 4(1): 18-27, 1987 Angioendotheliomatosis proliferans systemisata a cutaneous manifestation of malignant b cell lymphoma. Hautarzt 42(6): 384-390, 1991 Malignant systemic angioendotheliomatosis. [eurekamag.com]
manifestation of Hughes syndrome. 61 Nikam B...Jamale V 26231975 2015 7 Recurrent reactive angioendotheliomatosis in pregnancy: a case report. 61 Bin Saif GA...Sangueza OP 26228728 2015 8 Intravascular/Intralymphatic Histiocytosis: A Report of 3 Cases [malacards.org]
Reactive angioendotheliomatosis as a presenting cutaneous manifestation of Hughes syndrome. Lupus. 2015 Dec. 24 (14):1557-61. [Medline]. Lomater C, Gerloni V, Gattinara M, Mazzotti J, Cimaz R, Fantini F. [emedicine.medscape.com]
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Dry Skin
Other side effects include dry skin and itching, epistaxis, chilitis and psychiatric disorders, including severe depression and suicide idealization. [gs.amegroups.com]
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Skin Thickening
thickening, tendinous xanthoma, thrush, vitiligo, Werner’s s., xanthoma disseminatum, yellow skin infectious ; botryomycosis, chronic mucocutaneous candidiasis, chronic paronychia, crusted scabies, erosa interdigitalis blastomycetica, Fournier’s gangrene [dermadvocate.net]
Face, Head & Neck
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Aged Face
451 The Archaeology of Joint Disease 463 Topical Retinoids in the Treatment of Aging of the Skin 477 Carbon Dioxide Laser Resurfacing of the Aged Face 483 Melasma 491 Skin Tumours in Prematurely Photoaged Skin after LongTerm 501 Surface Evaluation of [books.google.com]
Workup
A thorough diagnostic workup and subsequent 3-year clinical follow-up revealed no sign of an underlying infectious or neoplastic disorder. [karger.com]
The usual workup utilized brain CT which is inadequate tool to evaluate nonhemorrhagic brain lesions. 3. Conclusion Intravascular lymphoma is a rare and fatal disease that presents with a myriad of nonspecific symptoms. [hindawi.com]
Serum
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Hyperviscosity
[…] organ 造血器 hematopoietic stem cell造血幹細胞 hemolytic uremic syndrome (HUS)溶血性尿毒性症候群 hemophagocytic syndrome (HPS)血球貪食症候群 hemophilia血友病 hereditary hemorrhagic telangiectasia遺伝性出血性末梢血管拡張症(オスラー病) hereditary spherocytosis (HS)遺伝性球状赤血球症 hiatus leukemicus白血病裂孔 hyperviscosity [tokyo-med.ac.jp]
Colonoscopy
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Colonic Ulcer
ulcers Microscopic (histologic) description Intravascular proliferation of endothelial cells resembling glomeruloid hemangioma Differential diagnosis Angiosarcoma Intravascular papillary endothelial hyperplasia Intravascular pyogenic granuloma Kaposi [pathologyoutlines.com]
Treatment
[…] type – Intravascular large B-cell lymphoma Treatment[edit] This section is empty. [en.wikipedia.org]
A literature review of the disease, including its controversial histiogenesis, treatment, and survival, is presented. In view of the rarity of the disease, only by studying more patients can we better understand the disease. [ncbi.nlm.nih.gov]
In a few cases treatment with palliative chemotherapy has been effective. [wiki30.com]
Fully revised and expanded, this new edition now includes full colour photographs and illustrations throughout to aid recognition and diagnosis, and covers the latest developments and treatment modalities. [books.google.com]
Prognosis
(Outcomes/Resolutions) The prognosis of Reactive Angioendotheliomatosis is linked to the prognosis of the underlying condition it is associated with. [dovemed.com]
Reactive angioendotheliomatosis has a good prognosis and usually regresses when the underlying disease, if discovered, is successfully treated. The disease sometimes regresses spontaneously. The prognosis depends on the underlying cause. [emedicine.medscape.com]
Prognosis Extremely poor; short survival is the norm despite aggressive chemotherapy. [medical-dictionary.thefreedictionary.com]
[…] from our specialty having an attentive and current awareness of the disease pathogenesis, since the radiologist is in the unique position of being able to identify etiology early in the course of disease, allowing for prompt treatment that may alter prognosis [applied-radiology.vmhost1.publishwithagility.com]
Etiology
A brain magnetic resonance imaging (MRI) was completed to exclude a cerebrovascular etiology of her acute symptoms. The MRI was reported as abnormal due to the presence of “white matter disease”. [hindawi.com]
Because the patient had no laboratory signs of infection, another etiology was considered. [quiz.jbjs.org]
Patients with SVCS will benefit from our specialty having an attentive and current awareness of the disease pathogenesis, since the radiologist is in the unique position of being able to identify etiology early in the course of disease, allowing for prompt [applied-radiology.vmhost1.publishwithagility.com]
Classification of these conditions often presents many nosological challenges, since underlying etiologies and pathogenetics are often not known. [doctors-hospitals-medical-cape-town-south-africa.blaauwberg.net]
(Etiology) The exact cause of Reactive Angioendotheliomatosis is unknown They are thought to occur as a reactive process to an existing underlying health condition. [dovemed.com]
Epidemiology
Definition / general Intravascular proliferation of endothelial cells Epidemiology Typically seen in skin; extremely rare in colon, with only one case reported Clinical features Only reported patient experienced massive gastrointestinal bleeding Gross [pathologyoutlines.com]
Generally, AL occurs in adults, but to date, no distinctive epidemiological features have been identified, owing to the small number of cases that have been reported in the literature (3). [path.upmc.edu]
Society ERS European Respiratory Society ESTS European Society of Thoracic Surgeons IASLC International Association for the Study of Lung Cancer IMIG International Mesothelioma Interest Group NCCN National Comprehensive Cancer Network SEER Surveillance, Epidemiology [haigan.gr.jp]
Epidemiology Frequency About 100 cases of malignant angioendotheliomatosis and about 40 cases of the reactive form have been described worldwide. [emedicine.medscape.com]
Pathophysiology
Pathophysiology The pathophysiology is not fully understood, but occlusion of blood vessel lumens appears to be common to all variants of the disease. [dermatologyadvisor.com]
Pathophysiology The pathogenesis of reactive angioendotheliomatosis is still not fully elucidated. [emedicine.medscape.com]
Although there appears to be a possible association between intravascular lymphoma and nodal NHL, the pathophysiologic relationships are poorly understood. [hematologyandoncology.net]
Prevention
Current medical research have not established a method of preventing Reactive Angioendotheliomatosis Regular medical screening at periodic intervals with blood tests, scans, and physical examinations, may be advised for those who have this condition What [dovemed.com]
PRISMS (Prevention of Relapses and Disability by Interferon b-1a Subcutaneously in Multiple Sclerosis). Randomised double-blind placebo-controlled study of interferon beta-1a in relapsing/remitting multiple sclerosis. [ge-bu.nl]
All female patients who can become pregnant must be enrolled in the iPLEDGE program, which is designed to prevent pregnancy while using this medication. [gs.amegroups.com]
The service-connected disabilities must be sufficient to prevent the veteran from performing the mental or physical tasks required to obtain or keep employment. [veterans.perkinslawtalk.com]