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Proliferating Angioendotheliomatosis

Prolif Angioendotheliomatosis


Presentation

  • A literature review of the disease, including its controversial histiogenesis, treatment, and survival, is presented. In view of the rarity of the disease, only by studying more patients can we better understand the disease.[ncbi.nlm.nih.gov]
  • Patients present with various skin lesions and rashes - mostly commonly on the thighs. Treatment aimed at the underlying condition hastens the resolution of the lesions.[en.wikipedia.org]
  • Histological and immunohistological investigations of the malignant form of AEPS are presented: In a 69-year-old woman cutaneous lesions appeared 5 months before the diagnosis of B-immunoblastic lymphoma.[unboundmedicine.com]
Italian
  • Pronunciation Italian Pronunciation Italian Pronunciation Italian Pronunciation Japanese Pronunciation Japanese Pronunciation Japanese Pronunciation Korean Pronunciation Norwegian Pronunciation Norwegian Pronunciation Polish Pronunciation Polish Pronunciation[pronouncekiwi.com]
  • [subject] Find articles for the above query (if any), plus for... all these words: this exact wording or phrase: one or more of these words: OR OR but not having any of these unwanted words: [language] And with languages: English French German Italian[entityextraction.net]
  • Benign reactive proliferating angioendotheliomatosis [in Italian]. G Ital Dermatol Venereol. 1 988;123(5):245248. (71.) McMenamin ME, Fletcher CDM. Reactiveangioendotheliomatosis: a study of 15 cases demonstrating a wide clinicopathologic spectrum.[thefreelibrary.com]
  • Waterborn zoonotic helminthiase in an Italian diver: a case report of a cutaneous Sparganum infection and a review of European cases. Pathog Glob Health. 2015;109(8):383-6. Epub 2016 Jan 9. PMID: 26751512 195. Ahn CS, Guerra A, Sangüeza OP.[skinsurgerycenter.net]
Lymphedema
  • Angiosarcoma arising in chronic lymphedema (syndrome of Stewart and Treves) may be histologically indistinguishable from Kaposi's sarcoma, but may also present with large pleo-morphic cells occluding the vessel lumina and resembling the cases described[docslide.net]
  • Epithelioid hemangioendothelioma Angiosarcoma Idiopathic (head and neck) Associated with chronic lymphedema (Stewart-Treves) Postirradiation Epithelioid 6.[slideshare.net]
  • Keywords: Lymphedema; Synovitis; Aspiration 1. Introduction Various dermatoses are associated with rheumatoid arthritis (RA), including rheumatoid nodules, rheumatoid vasculitis, and neutrophilic dermatoses.[file.scirp.org]
  • […] homozygous familial hypercholesterolemia, hyperapobetalipoproteinemia, myxedema, obstructive liver d. xanthoma, tuberous hyperlipoproteinemia type II & III xanthomas atherosclerosis, biliary disease, CTCL, diabetes mellitus, hypothyroidism, leukemia, lymphedema[dermadvocate.net]
  • The diagnosis is massive localized lymphedema of the morbidly obese (and not liposarcoma). FIgure 4a.[orthopaedicsone.com]
Turkish
  • Castilian) Pronunciation Spanish (Castilian) Pronunciation Spanish (Spain) Pronunciation Spanish (Spain) Pronunciation Spanish (Spain) Pronunciation Spanish (Spain) Pronunciation Spanish (Mexico) Pronunciation Swedish Pronunciation Swedish Pronunciation Turkish[pronouncekiwi.com]
  • Modern Hebrew Hindi Hungarian Icelandic Indonesian Kinyarwanda Korean Latin Latvian Lithuanian Macedonian Malayalam Maori Malay Multiple languages Norwegian Persian Polish Portuguese Pushto Romanian Sanskrit Serbian Croatian Slovak Slovenian Swedish Thai Turkish[entityextraction.net]
  • New Orleans, Louisiana 1999 Faculty, Fifth Annual Midwest Dermatopathology Workshop, Northwestern University, Chicago, Illinois 1999 Invited speaker, IIIrd Regional Clinicopathological Colloquium of the International and Turkish Societies of Dermatopathology[skinsurgerycenter.net]
Vietnamese
  • Indonesian Kinyarwanda Korean Latin Latvian Lithuanian Macedonian Malayalam Maori Malay Multiple languages Norwegian Persian Polish Portuguese Pushto Romanian Sanskrit Serbian Croatian Slovak Slovenian Swedish Thai Turkish Ukrainian Undetermined Urdu Vietnamese[entityextraction.net]
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  • MeSH term, type words from the biomedical concept you have in mind here: [transliterated title] And for this query matching the title in original language: [PMID] Show me only articles for these PMIDs (PubMed IDs): [shown] Results per page: [expand/collapse[entityextraction.net]
Vascular Disease
  • In the case reported, there are three distinctive features which imply that this rare syndrome should be recognized as a pattern of vascular disease. (1) There was focal proliferation of cells, similar to neoplastic reticular cells, associated with the[academic.naver.com]
  • Cholesterol emboli Arteriovenous shunts Chronic lymphatic leukemia Monoclonal gammopathy Angiosarcoma The “diffuse dermal angiomatosis” variant of cutaneous reactive angiomatosis is usually associated with peripheral vascular disease / atherosclerosis[dermatologyadvisor.com]
  • Illustrated here from a biopsy of a patient with an unclassified collagen vascular disease presenting with nodules and livedo reticularis is a muscular vessel (artery) whose endothelium is disrupted by lymphocytes (endothelialitis) and media and adventia[vgrd.org]
  • Its basis is usually atherosclerotic vascular disease, cholesterol emboli, mural thrombi and rarely, fragmentation of intracardiac tumors.[kundoc.com]
Osteoporosis
  • […] and Continuation of Aurotherapy in Patients with 367 Discoid Lupus Erythematosus Lesions Treated with Cryosurgery 375 A Current and Future Problem 387 Newer Concepts in Antimicrobial Therapy 397 Anecdotal Therapies 407 The Inverse Relationship between Osteoporosis[books.google.com]
  • Kuriyama M, Fujiyama J, Kubota R, Nakagawa M, Osame M: Osteoporosis and increased bone fractures in cerebrotendinous xanthomatosis. Metabolism 42:1497-8,1993.[orthopaedicsone.com]
  • […] epithelioma, dermatomyositis, inflammatory diseases, intradermal nevi, mixed tumor of the skin, primary from childhood, scars, scleroderma osteomyelitis congenital syphilis, diabetic foot ulcer, mycetoma (Madura foot), secondary syphilis, tertiary lues osteoporosis[dermadvocate.net]
Cutaneous Manifestation
  • Seminars in Diagnostic Pathology 4(1): 18-27, 1987 Angioendotheliomatosis proliferans systemisata a cutaneous manifestation of malignant b cell lymphoma . Hautarzt 42(6): 384-390, 1991 Malignant systemic angioendotheliomatosis.[eurekamag.com]
  • manifestation of malignant B-cell lymphomas.[unboundmedicine.com]
  • Reactive angioendotheliomatosis as a presenting cutaneous manifestation of Hughes syndrome. Lupus. 2015 Dec. 24 (14):1557-61. [Medline]. Lomater C, Gerloni V, Gattinara M, Mazzotti J, Cimaz R, Fantini F.[emedicine.medscape.com]
  • Cutaneous manifestations are also common and often consist of hyperpigmented or hemorrhagic lesions on the thighs and abdomen ( 31 ).[nature.com]
Skin Thickening
  • thickening, tendinous xanthoma, thrush, vitiligo, Werner’s s., xanthoma disseminatum, yellow skin infectious ; botryomycosis, chronic mucocutaneous candidiasis, chronic paronychia, crusted scabies, erosa interdigitalis blastomycetica, Fournier’s gangrene[dermadvocate.net]
Dry Skin
  • Other side effects include dry skin and itching, epistaxis, chilitis and psychiatric disorders, including severe depression and suicide idealization.[gs.amegroups.com]
Aged Face
  • 451 The Archaeology of Joint Disease 463 Topical Retinoids in the Treatment of Aging of the Skin 477 Carbon Dioxide Laser Resurfacing of the Aged Face 483 Melasma 491 Skin Tumours in Prematurely Photoaged Skin after LongTerm 501 Surface Evaluation of[books.google.com]
Epistaxis
  • Other side effects include dry skin and itching, epistaxis, chilitis and psychiatric disorders, including severe depression and suicide idealization.[gs.amegroups.com]

Workup

  • A thorough diagnostic workup and subsequent 3-year clinical follow-up revealed no sign of an underlying infectious or neoplastic disorder.[karger.com]
Dyslipidemia
  • Note the red and purple reticular pattern with associated ulcerations The patient’s past medical history included dyslipidemia, hypertension, chronic obstructive pulmonary disease, and a previous cerebrovascular accident.[gs.amegroups.com]

Treatment

  • Treatment aimed at the underlying condition hastens the resolution of the lesions. The malignant type is an intravascular lymphoma, usually of the diffuse B-cell type.[en.wikipedia.org]
  • A literature review of the disease, including its controversial histiogenesis, treatment, and survival, is presented. In view of the rarity of the disease, only by studying more patients can we better understand the disease.[ncbi.nlm.nih.gov]
  • In a few cases treatment with palliative chemotherapy has been effective.[wiki30.com]
  • Stay at the forefront of your field with updated treatment methods throughout, as well as an increased focus on patients with skin of color.[books.google.com]

Prognosis

  • (Outcomes/Resolutions) The prognosis of Reactive Angioendotheliomatosis is linked to the prognosis of the underlying condition it is associated with.[dovemed.com]
  • Prognosis Extremely poor; short survival is the norm despite aggressive chemotherapy.[medical-dictionary.thefreedictionary.com]
  • Reactive angioendotheliomatosis has a good prognosis and usually regresses when the underlying disease, if discovered, is successfully treated. The disease sometimes regresses spontaneously. The prognosis depends on the underlying cause.[emedicine.medscape.com]
  • […] from our specialty having an attentive and current awareness of the disease pathogenesis, since the radiologist is in the unique position of being able to identify etiology early in the course of disease, allowing for prompt treatment that may alter prognosis[applied-radiology.vmhost1.publishwithagility.com]
  • Can rituximab change the usually dismal prognosis of patients with intravascular large B-cell lymphoma? J Clin Oncol . 2008;26:5134-5136. 4. atz DA, Miller IJ, Gregory SA.[hematologyandoncology.net]

Etiology

  • Because the patient had no laboratory signs of infection, another etiology was considered.[quiz.jbjs.org]
  • Classification of these conditions often presents many nosological challenges, since underlying etiologies and pathogenetics are often not known.[doctors-hospitals-medical-cape-town-south-africa.blaauwberg.net]
  • Patients with SVCS will benefit from our specialty having an attentive and current awareness of the disease pathogenesis, since the radiologist is in the unique position of being able to identify etiology early in the course of disease, allowing for prompt[applied-radiology.vmhost1.publishwithagility.com]
  • (Etiology) The exact cause of Reactive Angioendotheliomatosis is unknown They are thought to occur as a reactive process to an existing underlying health condition.[dovemed.com]
  • Miscellaneous causes such as primary skin disorders are less commonly the etiology. In this case report, we described the rare finding of breast DDA in a patient who was successfully treated with isoretinoin.[gs.amegroups.com]

Epidemiology

  • Generally, AL occurs in adults, but to date, no distinctive epidemiological features have been identified, owing to the small number of cases that have been reported in the literature (3).[path.upmc.edu]
  • Society ERS European Respiratory Society ESTS European Society of Thoracic Surgeons IASLC International Association for the Study of Lung Cancer IMIG International Mesothelioma Interest Group NCCN National Comprehensive Cancer Network SEER Surveillance, Epidemiology[haigan.gr.jp]
  • Epidemiology Frequency About 100 cases of malignant angioendotheliomatosis and about 40 cases of the reactive form have been described worldwide.[emedicine.medscape.com]
  • Epidemiology and clinical characteristics of classic Kaposi's sarcoma, seroprevalence and variants of human herpesvirus 8 in South America: a critical review of an old disease. Int J Infect Dis. 2005;9(5):239-250. (61.) Pfleger L, Tappeiner J.[thefreelibrary.com]
  • A new classification of Mucocutaneous Leishmaniasis based on epidemiological, clinical, histopathological and immunological parameters: A retrospective analysis of 75 Bolivian cases. Clin Res 1992; 40, 671 A. 10.[skinsurgerycenter.net]
Sex distribution
Age distribution

Pathophysiology

  • Pathophysiology The pathophysiology is not fully understood, but occlusion of blood vessel lumens appears to be common to all variants of the disease.[dermatologyadvisor.com]
  • Pathophysiology The pathogenesis of reactive angioendotheliomatosis is still not fully elucidated.[emedicine.medscape.com]
  • Although there appears to be a possible association between intravascular lymphoma and nodal NHL, the pathophysiologic relationships are poorly understood.[hematologyandoncology.net]
  • Thalassemia Intermedia Liver, spleen, lymph node, paravertebral, intrathoracic, pelvic locations Incidence in up to 20% of pts Peak age incidence 21-30 yrs Paraspinal location occurs in 11-15% of cases 80% asymptomatic Can present as tumor-like masses M:F 5:1 Pathophysiology[orthopaedicsone.com]

Prevention

  • Current medical research have not established a method of preventing Reactive Angioendotheliomatosis Regular medical screening at periodic intervals with blood tests, scans, and physical examinations, may be advised for those who have this condition What[dovemed.com]
  • All female patients who can become pregnant must be enrolled in the iPLEDGE program, which is designed to prevent pregnancy while using this medication.[gs.amegroups.com]
  • The service-connected disabilities must be sufficient to prevent the veteran from performing the mental or physical tasks required to obtain or keep employment.[veterans.perkinslawtalk.com]
  • Author Robert A Schwartz, MD, MPH Professor and Head of Dermatology, Professor of Pathology, Pediatrics, Medicine, and Preventive Medicine and Community Health, Rutgers New Jersey Medical School; Visiting Professor, Rutgers University School of Public[emedicine.medscape.com]
  • Pathogenesis and rationale of prevention and treatment. J Bone Joint Surg 49A:1-30,1967.[orthopaedicsone.com]

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