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Renal Malrotation

Kidney Malrotation


Presentation

  • Presentation Young boy presenting with features of right pyeronephritis (right loin pain, fevers. Urine cultures were negative. A right renal mass was suspected on initial ultrasound (not shown).[radiopaedia.org]
  • Elsevier Health Sciences, ٣١‏/٠١‏/٢٠١٤ - 992 من الصفحات Acclaimed for its unsurpassed readability and manageable scope, Ashcraft’s Pediatric Surgery presents authoritative, practical guidance on treating the entire range of general surgical and urological[books.google.com]
  • Two vena cavae, one on each side of the aorta, are present below the level of the renal veins. 8 Several imaging techniques used in the evaluation and differentiation of pelvic cystic masses include excretory urography, ultrasound,CT and magnetic resonance[appliedradiology.com]
  • In the present case, a similar congenital anomaly in the form of the left ectopic (left iliac fossa) and malrotated kidney was present.[medical-dictionary.thefreedictionary.com]
  • […] from Altmetric.com Description A 60-year-old man was presented with colicky upper left abdominal pain and vomiting.[casereports.bmj.com]
Recurrent Infection
  • infection) Acute pyelonephritis (and urosepsis) Pyonephrosis and perinephric abscess Chronic pyelonephritis Epididymitis and orchitis Prostatitis Bladder pain syndrome Parasitic infections Phimosis and paraphimosis Neoplasia Wilm’s tumour and neuroblastoma[dundeemedstudentnotes.wordpress.com]
  • Obstruction and severe reflux may be corrected surgically when indicated (if causing hypertension, recurrent infections, or renal growth retardation).[merckmanuals.com]
  • The majority of patients with ectopic kidneys are asymptomatic but those affected by obstruction, recurrent infection, or renal calculi, the anatomical position and associated anomalies should dictate the plan of management.[casereports.in]
  • For those patients affected by obstruction, recurrent infection, or renal calculi, renal function should dictate management, though blood supply and position need to be considered when surgery is planned.[pediatricurologybook.com]
  • The most common pathologic conditions include renal calculi, pelviureteric junction (PUJ) obstruction, hydronephrosis and recurrent infections.[omicsonline.org]
Fever
  • Presentation Young boy presenting with features of right pyeronephritis (right loin pain, fevers. Urine cultures were negative. A right renal mass was suspected on initial ultrasound (not shown).[radiopaedia.org]
  • Other symptoms of malrotation may include: Frequent vomiting, often green or yellow-green in color A swollen, firm abdomen Pale color Poor appetite Little or no urine (due to fluid loss) Infrequent bowel movements Blood in the stools Fever Lethargy (showing[my.clevelandclinic.org]
  • He had a history of fever on and off since the last 7 months. An ultrasound showed a calculus of 2 Χ 1 cm in the lower calyx of left kidney and bilateral mild hydronephrotic changes.[sjkdt.org]
  • The abnormality may be clinically silent until adulthood, when hematuria, flank pain, fever, or, rarely, hypertension cause the patient to seek medical attention.[radiologykey.com]
Infertility
  • Others include dysuria, urinary frequency, hematuria, urinary tract infections, infertility, hemospermia and, rarely, enuresis.[appliedradiology.com]
  • Male infertility Varicocele Sexual health Erectile dysfunction Peyronie’s disease Priapism Retrograde ejaculation Premature Ejaculation Late-onset hypogonadism Hypogonadism and male hormone replacement Urethritis Gonorrhoea Chlamydia Non-specific urethritis[dundeemedstudentnotes.wordpress.com]
  • Patients are usually shorter than average (even with growth hormone therapy) and almost all are infertile (although assisted fertility may be successful).[patient.info]
  • ., Mulholland, S.G. et al. (1987) Ureteral ectopia presenting as epididymitis and infertility. Urology 30, 67–69. CrossRef PubMed Google Scholar Sripathi, V., King, P.A., Thompson, M.R., Bogle, M.S. (1991) Primary obstructive megaureter. J. Pediat.[link.springer.com]
Recurrent Urinary Tract Infection
  • Gun S, Ciantelli GL, Takahashi MAU, Brabo AA, Morais LA (2012) Complete renal fusion in a child with recurrent urinary tract infection. Radiol Bras. 45: 233-234.[omicsonline.org]
  • Clinical (symptomatic) success was defined as an absence of recurrent flank pain or other clinical condition attributable to UPJ obstruction (e.g. recurrent urinary tract infections or recurrent renal calculi).[brazjurol.com.br]
Enuresis
  • Page 365 - The genetics of enuresis. In: Kolvin I, MacKeith RC, Meadow SR (eds): Bladder control and enuresis. ‎[books.google.com]
  • Others include dysuria, urinary frequency, hematuria, urinary tract infections, infertility, hemospermia and, rarely, enuresis.[appliedradiology.com]
Aspiration
  • The presence of spermatozoa in the cystic aspirate differentiates the seminal vesicle cysts from the müllerianduct cysts.[appliedradiology.com]
  • Although an upper GI series provides definitive diagnosis, it must be done carefully by a radiologist experienced with doing this procedure on children to avoid aspiration and is not typically necessary if surgery is to be done immediately.[msdmanuals.com]
  • Although the final diagnosis is made by biopsy with fine-needle aspiration, we should take into account the risk of bleeding, which is increased due to the high vascularity of the tumor.[frontiersin.org]
Pelvic Mass
  • The mesonephric duct differentiates into the appendix of the epididymis, paradidymis, vas deferens, ejaculatory duct, seminal vesicles and hemitrigone. 6 The differential diagnosis of cystic pelvic masses in the male includes müllerian duct and ejaculatory[appliedradiology.com]
Hematuria
  • Others include dysuria, urinary frequency, hematuria, urinary tract infections, infertility, hemospermia and, rarely, enuresis.[appliedradiology.com]
  • A 30-year-old male visited our hospital with the chief complaints of abdominal pain and microscopic hematuria.[webview.isho.jp]
  • The abnormality may be clinically silent until adulthood, when hematuria, flank pain, fever, or, rarely, hypertension cause the patient to seek medical attention.[radiologykey.com]
Renal Stone
  • stone formation; (iii) accessory renal arteries or abnormal arterial supply, e.g. from the mesenteric artery.[academic.oup.com]
  • The radio opaque shadow seen in plain X-ray was found to be a renal stone and it was lying in the lower calyx. The kidneys were in normal anatomical positions.[sjkdt.org]
  • Renal stone-associated squamous cell carcinoma and pyelo-colo-duodenal fistula. Urology . 2008;72(5):1013. Article PubMed Guraya SY, Murshid KR. Malignant duodenocolic fistula. Various therapeutic surgical modalities.[acgcasereports.gi.org]
Dysuria
  • Others include dysuria, urinary frequency, hematuria, urinary tract infections, infertility, hemospermia and, rarely, enuresis.[appliedradiology.com]
  • Basic Sciences Anatomy of the urinary tract Male Female Micturition Kidney physiology Water homeostasis Core clinical Problems/Presenting Complaint Haematuria Lower Urinary Tract Symptoms Dysuria Oliguria/Anuria Polyuria Nocturia/nocturnal polyuria Urinary[dundeemedstudentnotes.wordpress.com]
  • We present here a 36-year-old male with bilateral flank pain and dysuria for 3 days. He had a history of fever on and off since the last 7 months.[sjkdt.org]
Urinary Incontinence
  • Basic Sciences Anatomy of the urinary tract Male Female Micturition Kidney physiology Water homeostasis Core clinical Problems/Presenting Complaint Haematuria Lower Urinary Tract Symptoms Dysuria Oliguria/Anuria Polyuria Nocturia/nocturnal polyuria Urinary[dundeemedstudentnotes.wordpress.com]
  • PubMed Google Scholar Freedman, E.R., Rickwood, A.M.K. (1994) Urinary incontinence due to unilateral vaginally ectopic single ureter. Br. J. Urol. 73, 716–717.[link.springer.com]
  • In females, the common symptom is dribbling urinary incontinence [ 136 ]. Other presenting symptoms can include urinary tract infection, abdominal pain, and renal failure [ 137 ].[transbiomedicine.com]
Hemospermia
  • Others include dysuria, urinary frequency, hematuria, urinary tract infections, infertility, hemospermia and, rarely, enuresis.[appliedradiology.com]

Workup

  • Sometimes, ascertaining the diagnosis on the basis of IVU alone is difficult, and further workup—using CT scanning, MRI, or scintigraphy—may be necessary.[emedicine.medscape.com]

Treatment

  • Prompt recognition and treatment is essential to arrest haemorrhage which may be life threatening. A patient with chronic aortic dissection and malrotated right kidney underwent PCNL for right renal calculus. He developed delayed gross haematuria.[ncbi.nlm.nih.gov]
  • Focus on evidence-based treatments and outcomes to apply today’s best practices.[books.google.com]
  • Czaplicki M, Krzeski T, Borkowski A, et al: Surgical treatment of stenosis of the pyeloureteral junction in pelvic kidney. Eur Urol 1984;10:377–379. Donahoe PK, Hendren WH: Pelvic Kidney in infants and children: Experience with 16 cases.[karger.com]
  • […] ruled out as it significantly impair successful treatment. [4] For stones that are less than 1.5 cm, ureteroscopy and shockwave lithotripsy can be first utilized. [4] For stones larger than 1.5 cm or when previous treatment has failed, the stones can[en.wikipedia.org]
  • Surgical. treatment of atypical metastasis from renal cell carcinoma (RCC). BJU Int 2012;110: 559-563. 21. Sadler GJ, Anderson MR, Moss MS, Wilson PG.[ijp.iranpath.org]

Prognosis

  • , Prevention, and Complications Prognosis full recovery is expected after surgical correction Prevention no preventive measures are available at this time Complications without treatment, condition is lethal Please rate topic.[step2.medbullets.com]
  • Prognosis The overall prognosis is good. Patients are usually shorter than average (even with growth hormone therapy) and almost all are infertile (although assisted fertility may be successful).[patient.info]
  • In recent years, with the advent of target therapies, the prognosis of patients with metastatic RCC has improved ( 10 ).[frontiersin.org]
  • Cleveland Clinic, including causes, signs, symptoms, diagnosis, treatment, and prognosis. This paper talks about cases of adults. SPECTCT Scan InsideRadiology Situs inversus abdominus and malrotation in an adult with.[light-factor.cf]
  • DISCUSSION The biological behavior of RCC is characteristically variable and the prognosis is unpredictable 8 ) . The clinical course of the disease ranges from months to several decades and even spontaneous regression has been documented 9 ) .[kjim.org]

Etiology

  • Gleason PE, Kelalis PP, Husmann DA, Kramer SA: Hydronephrosis in renal ectopia: Incidence, etiology and significance. J Urol 1994;151:1660–1661.[karger.com]
  • M F Right (67%) ETIOLOGY / PATHOPHYSIOLOGY Due to abnormal ascent of the kidneys, resulting in abnormalities in renal position, rotation and fusion. Renal ectopic by definition refers to abnormal position of the kidneys.[fetalultrasound.com]
  • A review of the literature on extrarenal calyces was presented and etiology was discussed. We emphasized the necessity of further investigation in surgical treatments of these patients aside from ne-phrectomy. Copyright 1978, Igaku-Shoin Ltd.[webview.isho.jp]
  • Introduction Congenital failure of the duodenal lumen to completely recanalize Etiology unknown but thought to occur during weeks 8-10 of development Results in stenosis of the duodenal passageway between the stomach and intestinal tract leads to gastric[step2.medbullets.com]
  • Duodenocolic fistulas are classified into primary and secondary groups; primary fistulas can be due to infectious etiology, Crohn’s disease, peptic ulcer disease, or active malignancies without any prior surgeries. 1,2 Secondary fistulas can develop as[acgcasereports.gi.org]

Epidemiology

  • […] during weeks 8-10 of development Results in stenosis of the duodenal passageway between the stomach and intestinal tract leads to gastric outlet syndrome Associated with Down syndrome (20-30% of DS cases) and other birth defects as with biliary atresia Epidemiology[step2.medbullets.com]
  • Abbreviations TS: Turner syndrome RCC: Renal cell carcinoma SEER: Surveillance, epidemiology, and end results OS: Overall survival.[bmcresnotes.biomedcentral.com]
  • Epidemiology, clinical features, and diagnosis of mechanical small bowel obstruction in adults. Of malrotation and intestinal volvulus. Malrotation is a birth defect that occurs during the 10th week of pregnancy.[light-factor.cf]
  • Epidemiology [ 2 ] Turner syndrome occurs in approximately 1 in every 2,000 live female births. The condition is much more common in utero and it has been estimated that 1-2% of all conceptuses are affected, of whom only 1% will survive to term.[patient.info]
  • […] imaging before any abdominal surgery as the vascular supply to the abnormal kidney can be highly variable between patients. [1] Additionally, the horseshoe kidneys can have a close association with colon which can increase risk of bowel injury. [1] Epidemiology[en.wikipedia.org]
Sex distribution
Age distribution

Pathophysiology

  • M F Right (67%) ETIOLOGY / PATHOPHYSIOLOGY Due to abnormal ascent of the kidneys, resulting in abnormalities in renal position, rotation and fusion. Renal ectopic by definition refers to abnormal position of the kidneys.[fetalultrasound.com]
  • CrossRef PubMed Google Scholar Koff, S.A. (1990) Pathophysiology of ureteropelvic junction obstructions. Urol. Clin. North. Am. 17, 263–272.[link.springer.com]
  • Pathophysiology [ edit ] Kidneys are normally located in the retroperitoneal space between the T12 and L3 vertebrae after ascending from the pelvis during development to rest underneath the adrenal glands. [1] In patients with this condition, the horseshoe[en.wikipedia.org]
  • Eight were male, 89% had left sided UPJ obstruction, and 78% had crossing vessel pathophysiology. Eight patients had a primary UPJ obstruction, while one patient’s obstruction was thought to be secondary to stone disease (Table-1).[brazjurol.com.br]
  • Williams B, Tareen B, Resnick MI (2007) Pathophysiology and treatment of ureteropelvic junction obstruction. Curr Urol Rep 8: 111-117.[transbiomedicine.com]

Prevention

  • Prevention of neural tube defects: results of the Medical Research Council Vitamin Study. ‎[books.google.com]
  • , and Complications Prognosis full recovery is expected after surgical correction Prevention no preventive measures are available at this time Complications without treatment, condition is lethal Please rate topic.[step2.medbullets.com]
  • Antibiotic prophylaxis to prevent subacute bacterial endocarditis is now less likely to be necessary (see the separate article on Prevention of Endocarditis ). Orthopaedics: regular review is usually unnecessary.[patient.info]
  • Is chronic lung disease in low birth weight infants preventable? A survey of eight centers. ‎ Página 84 - Tanner JM, Whitehouse RH, Marubini E, Resele LF. The adolescent growth spurt of boys and girls of the Harpenden growth study. ‎[books.google.es]
  • A volvulus is a disorder that causes an obstruction in the intestine, preventing food from being digested normally. The blood supply to the twisted part of the intestine can also be cut off, leading to the death of that segment of the intestine.[my.clevelandclinic.org]

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