Presentation
The time is definitely right for a comprehensive presentation of these new diagnostic modalities and the way in which they will influence the field of congenital heart management. * First and only volume on the market presenting all the pre- and post-operative [books.google.de]
Most patients present with this anom-aly during infancy and do not survive to adulthood without treatment. However, the present case describes a patient who presented as an adult. [docslide.com.br]
If patent ductus arteriosus are present, a difference in color and clubbing in the arms might be evident. [astrocyte.in]
It is present in 1% to 4% of patients with congenital heart defects, and male and female children are equally affected. [musculoskeletalkey.com]
At the present time, mortality is virtually nonexistent. [revespcardiol.org]
Entire Body System
- Asymptomatic
AVR is not indicated in asymptomatic patients with AR who have normal LV size and function. [slideplayer.com]
Implantation of Cardiac Pacemakers 56 Arrhythmia Diagnosis and Management Asymptomatic Adult Patients Pacemaker implantation may be beneficial for asymptomatic adult patients with resting heart rates of less than 40 beats per minute or abrupt pauses in [powershow.com]
Similar articles [Hemitruncus arteriosus in an asymptomatic young man--diagnostic value of transesophageal echocardiography]. Völker H, Köhler E. Völker H, et al. Z Kardiol. 1994 Sep;83(9):610-4. Z Kardiol. 1994. PMID: 7801662 German. [pubmed.ncbi.nlm.nih.gov]
CT • Case Study By: Philips CT Clinical Science On: Jul 21, 2005 Rating: 1 2 3 4 5 (0) Views: 957 Asymptomatic assessment of coronary artery disease This Mx8000 IDT case study presents images from a scan of a 76 year-old man with mild hypertension and [netforum.healthcare.philips.com]
- Surgical Procedure
To make the department as the destination of choice for advanced surgical procedure. [neigrihms.gov.in]
Arch Anomalous branch Associated anomaly Surgical procedure Additional surgical procedure CPB Post-op complication Outcome Follow-up (months) Group I Type 1a 1 4/12 Male 3.5 + + 95 55/30 30 (FU no PAH) Left RPA PDA Direct implantation PDA ligation No [icvts.oxfordjournals.org]
Transesophageal echography showed adequate surgical procedure results, with no acceleration through the anastomosis and good biventricular function. After 24 hours, the patient was extubated. [ctsnet.org]
Neurological outcome of a patient with hemitruncus arteriosus after the surgical procedure is a major point of interest for both the surgeon and the anaesthesiologist. [turkiyeklinikleri.com]
Personnel performing such procedures should work as part of a team with expertise in the surgical and transcatheter management of patients with CHD. 26 Anesthesia and Sedation Access to Care Anesthesia and Sedation Surgical procedures that require general [slideplayer.com]
Cardiovascular
- Heart Disease
Letture consigliate Eichhorn JG, Long FR, Hill SL et al (2006) Assessment of in-stent stenosis in small children with congenital heart disease using multi-detector computed tomography: a validation study. [link.springer.com]
[…] fetal congenital heart disease giant cell myocarditis heart anomaly heart murmur heart problems heart racing hemitruncus hypoplastic left heart syndrome infiltrative disorders of the heart interrupted aortic arch kawasaki syndrome maternal valvular disease [washington.providence.org]
Truncus arteriosus is a congenital heart disease characterized by a single great artery that leaves the base of the heart, giving rise to the coronary, pulmonary, and systemic arteries. [emedicine.medscape.com]
Complex Congenital Heart Disease Patients with the following conditions should be seen regularly at adult congenital heart disease centers: Conduits, valved or nonvalved Cyanotic congenital heart (all forms) Double-outlet ventricle Eisenmenger syndrome [emoryhealthcare.org]
Every topic and chapter has been revised and updated to reflect the latest medical and surgical treatments for all congenital and acquired heart diseases. New surgical approaches, including hybrid procedures, have been updated. [books.google.com]
- Hypertension
This lifelong systemic volume flow to the left lung caused progressive worsening of pulmonary hypertension and right ventricular hypertrophy. [ncbi.nlm.nih.gov]
A special focus has been placed on noninvasive imaging techniques, normative blood pressure standards, suggested approaches to pediatric hypertension, detection and management of lipid abnormalities as recommended by the Expert Panel, pediatric arrhythmias [books.google.com]
Management and treatment Early diagnosis and surgical treatment are mandatory in order to prevent cardiac failure and pulmonary hypertension. [orpha.net]
This may be a response to heart failure, pulmonary hypertension, or relative hypovolemia linked to fluid restriction or diuretics. [ejca.eg.net]
In the intensive care unit, elective nitric oxide was started in the usual doses in view of severe pulmonary arterial hypertension. [annalspc.com]
- Vascular Disease
Report of a case with special reference to pulmonary vascular disease in the left and right lungs. Chest 1983 ; 3 : 575 – 578. 10. Weintraub, RA, Fabian, CE, Adams, DF. Ectopic origin of one pulmonary artery from the ascending aorta. [cambridge.org]
Heath-Edwards classification A histopathologic classification useful in assessing the potential for reversibility of pulmonary vascular disease. (Heath D, Edwards JE. [cachnet.org]
In some cases, there is an absence of cardiac failure or a very short period of failure followed by the development of pulmonary vascular disease. [astrocyte.in]
DISEASE AT THIRD MONTH :PULMONARY BLOOD FLOW, CIRCULATING VASOCONSTRICTOR, NEUROGENIC CROSSOVER FROM UNPROTECTED LUNG AND LEFT VENTRICULAR FAILURE 4. [slideshare.net]
- Continuous Murmur
Cardiac auscultation revealed a grade II/VI continuous murmur. Peripheral pulses were palpable. On abdominal examination, the liver span was increased on palpitation and generalized edema was obvious. [dovepress.com]
Musculoskeletal
- Osteoporosis
Diffusemarrowdeposition j generalized osteoporosis ri coarsetrabecular pattern(DDx: sarcoidosis) r/ pathologic collapseof vertebralbody may occur 3. [dokumen.tips]
Neurologic
- Hemianesthesia
hemianesthesia. hemiseptum (hem-e-sep′tum) A lateral half of any septum. hemispasm (hem′e-spazm) A spasm affecting one or more muscles of one side of the face or body. hemisphere (hem′i-sfer) [TA] Half of a spherical structure. [theodora.com]
Workup
[…] measurements. 22730008 Granular cell tumor in a male breast: mammographic, sonographic, and pathologic features. 22729971 Unusual motion detected on real-time sonography inside a glomus tumor in the thigh. 22729945 Role of sonography in the diagnostic workup [nlm.life]
Treatment
details of surgical treatment, potential complications and literature references. [books.google.de]
and which forms of treatment currently in use provide the best outcomes to date [books.google.com]
Management and treatment Early diagnosis and surgical treatment are mandatory in order to prevent cardiac failure and pulmonary hypertension. [orpha.net]
Prognosis
NATURAL HISTORY INCREASE PBF SEVERE PAH SURVIVAL BEYOND 1 YR IS NOT POSSIBLE ASSOCIATED CARDIAC ANOMALIES MAY WORSEN THE PROGNOSIS EVEN FURTHER THE PREVALENCE OF HEMITRUNCUS BEYOND INFANCY IS NOT KNOWN AS MAJORITY OF THE SERIES HAVE PATIENTS [slideshare.net]
Prognosis Patients treated early in life have good short and long-term outcome. If left untreated, the disease may lead to congestive cardiac failure and pulmonary hypertension, with 30% of infants dying within 3 months. [orpha.net]
Barlowpositive i/ slightincreasein femoralanteversion in cartilage r/ mild marginalabnormalities acetabular { early labraleversion Prognosis: 60ohwill become stable after 1 week; 88% will becomestableby age of 2 months HIP SUBLUXED 4. [dokumen.tips]
Treatment and prognosis Due to parallel fetal circulation, truncus arteriosus does not cause any hemodynamic problem in utero. [radiopaedia.org]
Other types of hemivertebra, especially those involving unbalanced congenital scoliosis, usually progress markedly with growth and have a relatively poor prognosis unless early spinal fusion prevents further spinal curvature. [medical-dictionary.thefreedictionary.com]
Etiology
Etiology The pathogenesis still remains unknown, although an association has been suggested with the 22q11.2 deletion syndrome (see this term). [orpha.net]
Candida parapsilosis was known to be occasionally responsible for pathological lesions of the nails [5] but is now emerging as one of the important etiological agents of onychomycosis. [docksci.com]
In our review of the literature; although both lesions involve abnormal development of the region of the aortic and pulmonary roots and the aortic arch, they seem to have different embryologic etiologies. [studyres.com]
[…] expansion { oftenmultiple after Prognosis; tendencyto recurafter localexcision; pulmonary metastases severalrecurrences may develoP related) DDx: fibrousdysplasia(possibly A IN H U M D IS E A S E = DACTYLOLYSIS SPONTANEA = fissure, saw,sword] [ainhum Etiology [dokumen.tips]
I recommend referencing the latest articles on the genetic basis for and noninherited risk factors for CHD from the American Heart Association as etiologies of CHD. Circulation. 2007 Jun 12;115(23):3015-38. Epub 2007 May 22. [en.wikipedia.org]
Epidemiology
Summary Epidemiology The incidence is estimated at 0.1% of all congenital cardiac anomalies and around 200 cases have been described in the world literature. [orpha.net]
Ekko 12:39, 24 August 2007 (UTC) Sources for epidemiology section? [ edit ] The figures given in the epidemiology section appear to be based on the US alone, but do not state this. (Nothing about the source of these numbers is given.) [en.wikipedia.org]
An epidemiological survey in Israel,” Mycoses, vol. 43, no. 9-10, pp. 349–353, 2000. [2] H. C. Williams, “The epidemiology of onychomycosis in Britain,” British Journal of Dermatology, vol. 129, no. 2, pp. 101– 109, 1993. [3] S. Perea, M. J. [docksci.com]
We present the results of a literature review of the epidemiological, physiopathological, clinical, diagnostic, and surgical characteristics of this rare condition. [revespcardiol.org]
Pathophysiology
The Congenital Heart Defects are presented with each chapter devoted to a single malformation, with incidence, morphology, associated anomalies, pathophysiology, diagnosis (including clinical pattern, electrocardiogram, chest X-ray, echocardiogram, cardiac [books.google.de]
It provides complete, authoritative information on the biology of the newborn and the pathophysiology and management of diseases during the neonatal period. [books.google.com]
PATHOPHYSIOLOGY • FIRST DESCRIBED BY FRAENTZEL IN 1868 • RPA FROM AORTA MOST COMMON(X4-8 TIMES) • AFFECTED LUNG IS PERFUSED AT SYSTEMIC PRESSURE AND THE REMAINING LUNG IS EXPOSED TO THE ENTIRE OUTPUT OF THE RIGHT VENTRICLE • PULMONARY CIRCULATION OF BOTH [slideshare.net]
The last 20 years have brought about rapid developments in technology, emphasis on a multidisciplinary approach to treatment, and a more thorough understanding of both the anatomy and pathophysiology of congenital heart disease, leading to the improved [accessmedicine.mhmedical.com]
The pathophysiology involves external vascular compression, which leads directly to a reduced luminal cross-sectional area, as well as cartilage breakdown, tracheomalacia, and stenosis as a result of chronic, pulsatile mechanical compression. [radiologykey.com]
Prevention
Reference Parker SE, Mai CT, Canfield MA, et al; for the National Birth Defects Prevention Network. Updated national birth prevalence estimates for selected birth defects in the United States, 2004-2006. [cdc.gov]
Management and treatment Early diagnosis and surgical treatment are mandatory in order to prevent cardiac failure and pulmonary hypertension. [orpha.net]
4 The surgical repair should be done within the first six months to prevent severe pulmonary vasculature disease. [dovepress.com]
Other types of hemivertebra, especially those involving unbalanced congenital scoliosis, usually progress markedly with growth and have a relatively poor prognosis unless early spinal fusion prevents further spinal curvature. [medical-dictionary.thefreedictionary.com]
Before commencing the cardiopulmonary bypass, a tourniquet was applied to the anomalous pulmonary artery in order to prevent pulmonary overflow and organ malperfusion during the bypass. [ctsnet.org]