Presentation
The time is definitely right for a comprehensive presentation of these new diagnostic modalities and the way in which they will influence the field of congenital heart management. * First and only volume on the market presenting all the pre- and post-operative [books.google.de]
If patent ductus arteriosus are present, a difference in color and clubbing in the arms might be evident. [astrocyte.in]
The patient presented to us in the early second decade. The diagnosis was suspected with echocardiography and confirmed with cardiac catheterization. The patient underwent successful surgical correction of the anomaly. [pesquisa.bvsalud.org]
All studies on humans described in the present manuscript were carried out with the approval of the responsible eth-ics committee and in accordance with national law and the Helsinki Declaration of 1975 (in its current, re-vised form). [docslide.com.br]
Entire Body System
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Anemia
Stay current on the developments and research surrounding neonatal anemia from the entirely new chapter on Blood and Hematopoietic System highlights. [books.google.de]
Therapeutic Phlebotomy Indications for therapeutic phlebotomy are hemoglobin greater than 20 g per dL and hematocrit greater than 65%, associated with headache, increasing fatigue, or other symptoms of hyperviscosity in the absence of dehydration or anemia [slideplayer.com]
Therapeutic Phlebotomy Indications for therapeutic phlebotomy are hemoglobin greater than 20 g per dL and hematocrit greater than 65, associated with headache, increasing fatigue, or other symptoms of hyperviscosity in the absence of dehydration or anemia [powershow.com]
[…] effusion in osteoarthritis with correlation to radiographic findings. 24166054 Sonographic classification of draining pathways of obstructed hepatic veins in Budd-Chiari syndrome. 24166013 Transcranial Doppler ultrasonography in children with sickle cell anemia [nlm.life]
Hematologic Problems Indications for therapeutic phlebotomy are hemoglobin greater than 20 g per dL and hematocrit greater than 65%, associated with headache, increasing fatigue, or other symptoms of hyperviscosity in the absence of dehydration or anemia [slideshare.net]
Respiratoric
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Pneumonia
Clinical symptoms (tachypnea, recurrent pneumonia, heart failure, etc.) present in most patients during infancy [ 5 ]. Without receiving surgical correction, the patients have less chance to survive to adulthood. [cardiothoracicsurgery.biomedcentral.com]
A preliminary study. 28940421 Changes in pulmonary artery systolic pressure correlate with radiographic severity and peripheral oxygenation in adults with community-acquired pneumonia. 28881023 Double-outlet left ventricle with a bicuspid pulmonary valve [nlm.life]
Cardiovascular
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Heart Disease
Every topic and chapter has been revised and updated to reflect the latest medical and surgical treatments for all congenital and acquired heart diseases. New surgical approaches, including hybrid procedures, have been updated. [books.google.com]
There is no doubt that these techniques will be particularly helpful for older children and adults with congenital heart disease in assessing the late impact of a congenital heart malformation and the surgical repair or palliation which may have been [books.google.de]
Anomalous right or left pulmonary artery arising from the aorta are relatively rare congenital heart disease entities. [astrocyte.in]
disease dextrocardia double aortic arch double outlet right ventricle ebstein anomaly eisenmenger syndrome endocardial cushion defect familial arrhythmia family history heart disease fetal arrhythmia fetal cardiomyopathy fetal congenital heart disease [washington.providence.org]
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Vascular Disease
Report of a case with special reference to pulmonary vascular disease in the left and right lungs. Chest 1983 ; 3 : 575 – 578. 10. Weintraub, RA, Fabian, CE, Adams, DF. Ectopic origin of one pulmonary artery from the ascending aorta. [cambridge.org]
In some cases, there is an absence of cardiac failure or a very short period of failure followed by the development of pulmonary vascular disease. [astrocyte.in]
Although early recognition and surgical treatment of this condition are mandatory to prevent the onset of irreversible pulmonary vascular disease, the presence of severe pulmonary hypertension did not contraindicate surgical correction in our patient. [ncbi.nlm.nih.gov]
To avoid pulmonary vascular disease and improve the outcome, AORPA must be repaired as early in life as possible [ 10 – 12 ]. [cardiothoracicsurgery.biomedcentral.com]
Heath-Edwards classification A histopathologic classification useful in assessing the potential for reversibility of pulmonary vascular disease. (Heath D, Edwards JE. [cachnet.org]
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Hypotension
Intravenous fluids or sympathomimetics may be required to treat hypotension. Other anesthetic agents can depress the sympathetic drive, with similar hemodynamic effects 18. [ejca.eg.net]
Workup
[…] measurements. 22730008 Granular cell tumor in a male breast: mammographic, sonographic, and pathologic features. 22729971 Unusual motion detected on real-time sonography inside a glomus tumor in the thigh. 22729945 Role of sonography in the diagnostic workup [nlm.life]
Hypertrophy
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Ventricular Hypertrophy
An electrocardiogram showed right ventricular hypertrophy with … View Full Text Request Permissions If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. [heart.bmj.com]
hypertrophy septal defect sick sinus syndrome single ventricle defect subaortic stenosis supraventricular tachycardia syncope tachycardia tetralogy of fallot transposition of great vessels truncus arteriosus truncus arteriosus communis tufted angioma [washington.providence.org]
hypertrophy secondary to systemic hypertension. 23124825 Sonographic diagnosis of a viable abdominal pregnancy with planned delivery after fetal lung maturation. 23124800 Echogenic splenic lesions in a child with type B Niemann-Pick disease. 23124724 [nlm.life]
Treatment
and which forms of treatment currently in use provide the best outcomes to date [books.google.com]
Walsh, along with a multi-disciplinary team of contributors guide you through the sweeping developments in diagnosis and treatment of the mother fetus, and neonate. [books.google.de]
Patients with AORPA who experienced surgical treatment early in life have excellent short-and long-term outcome [ 18 ]. However, the most common late complication after surgical treatment is stenosis at the anastomotic site. [cardiothoracicsurgery.biomedcentral.com]
Management and treatment Early diagnosis and surgical treatment are mandatory in order to prevent cardiac failure and pulmonary hypertension. [orpha.net]
Prognosis
NATURAL HISTORY INCREASE PBF SEVERE PAH SURVIVAL BEYOND 1 YR IS NOT POSSIBLE ASSOCIATED CARDIAC ANOMALIES MAY WORSEN THE PROGNOSIS EVEN FURTHER THE PREVALENCE OF HEMITRUNCUS BEYOND INFANCY IS NOT KNOWN AS MAJORITY OF THE SERIES HAVE PATIENTS [slideshare.net]
Prognosis Patients treated early in life have good short and long-term outcome. If left untreated, the disease may lead to congestive cardiac failure and pulmonary hypertension, with 30% of infants dying within 3 months. [orpha.net]
Treatment and prognosis Due to parallel fetal circulation, truncus arteriosus does not cause any hemodynamic problem in utero. [radiopaedia.org]
Other types of hemivertebra, especially those involving unbalanced congenital scoliosis, usually progress markedly with growth and have a relatively poor prognosis unless early spinal fusion prevents further spinal curvature. [medical-dictionary.thefreedictionary.com]
Associated cardiac anomalies may worsen the prognosis even further. [annalspc.com]
Etiology
Etiology The pathogenesis still remains unknown, although an association has been suggested with the 22q11.2 deletion syndrome (see this term). [orpha.net]
Candida parapsilosis was known to be occasionally responsible for pathological lesions of the nails [5] but is now emerging as one of the important etiological agents of onychomycosis. [docksci.com]
In our review of the literature; although both lesions involve abnormal development of the region of the aortic and pulmonary roots and the aortic arch, they seem to have different embryologic etiologies. [studyres.com]
Irrespective of the etiology, right heart failure will result in inadequate systemic perfusion, exacerbating the original problem. [ejca.eg.net]
[…] primary pancreatic Burkitt's lymphoma in a 4-year-old child. 27224638 Presence of a high-flow-mediated constriction phenomenon prior to flow-mediated dilatation in normal weight, overweight, and obese children and adolescents. 27220064 The chorionic bump: Etiologic [nlm.life]
Epidemiology
Summary Epidemiology The incidence is estimated at 0.1% of all congenital cardiac anomalies and around 200 cases have been described in the world literature. [orpha.net]
An epidemiological survey in Israel,” Mycoses, vol. 43, no. 9-10, pp. 349–353, 2000. [2] H. C. Williams, “The epidemiology of onychomycosis in Britain,” British Journal of Dermatology, vol. 129, no. 2, pp. 101– 109, 1993. [3] S. Perea, M. J. [docksci.com]
JFW [email protected] 16:07, 4 September 2014 (UTC) I will be adding a section title "Caregiving for a Child with CHD" between the treatment and epidemiology sections. [en.wikipedia.org]
We present the results of a literature review of the epidemiological, physiopathological, clinical, diagnostic, and surgical characteristics of this rare condition. [revespcardiol.org]
Pathophysiology
It provides complete, authoritative information on the biology of the newborn and the pathophysiology and management of diseases during the neonatal period. [books.google.com]
PATHOPHYSIOLOGY • FIRST DESCRIBED BY FRAENTZEL IN 1868 • RPA FROM AORTA MOST COMMON(X4-8 TIMES) • AFFECTED LUNG IS PERFUSED AT SYSTEMIC PRESSURE AND THE REMAINING LUNG IS EXPOSED TO THE ENTIRE OUTPUT OF THE RIGHT VENTRICLE • PULMONARY CIRCULATION OF BOTH [slideshare.net]
The last 20 years have brought about rapid developments in technology, emphasis on a multidisciplinary approach to treatment, and a more thorough understanding of both the anatomy and pathophysiology of congenital heart disease, leading to the improved [accessmedicine.mhmedical.com]
The pathophysiological characteristic change of AORPA is early and rapid development of pulmonary hypertension, and which the several mechanisms involve in. [cardiothoracicsurgery.biomedcentral.com]
The pathophysiology involves external vascular compression, which leads directly to a reduced luminal cross-sectional area, as well as cartilage breakdown, tracheomalacia, and stenosis as a result of chronic, pulsatile mechanical compression. [radiologykey.com]
Prevention
Although early recognition and surgical treatment of this condition are mandatory to prevent the onset of irreversible pulmonary vascular disease, the presence of severe pulmonary hypertension did not contraindicate surgical correction in our patient. [ncbi.nlm.nih.gov]
Second, financial constraints prevent referral of patients with AORPA to a better hospital. [cardiothoracicsurgery.biomedcentral.com]
Reference Parker SE, Mai CT, Canfield MA, et al; for the National Birth Defects Prevention Network. Updated national birth prevalence estimates for selected birth defects in the United States, 2004-2006. [cdc.gov]
Management and treatment Early diagnosis and surgical treatment are mandatory in order to prevent cardiac failure and pulmonary hypertension. [orpha.net]
Other types of hemivertebra, especially those involving unbalanced congenital scoliosis, usually progress markedly with growth and have a relatively poor prognosis unless early spinal fusion prevents further spinal curvature. [medical-dictionary.thefreedictionary.com]