Presentation
The exclusion of a large akinetic RVOT area during reoperation of patients presenting with severe post-repair right ventricular dilatation was investigated. [ncbi.nlm.nih.gov]
Pediatric patients usually have no symptoms but patients over 40 years of age are symptomatic at presentation [ 5 ]. [omicsonline.org]
Cardiovascular
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Heart Disease
Idiopathic myocarditis associated with such unusual features is relatively rare, and may present problems in differentiation from other congenital heart diseases causing dilatation and dysfunction of the right ventricle. [ncbi.nlm.nih.gov]
Infants, children and adolescents with congenital heart disease (CHD) are a challenge to manage and an ever-increasing number are reaching adulthood. [books.google.de]
Causes of right chambers dilatation include pressure overload, volume overload, and myocardial dysfunction, which may be secondary to ischemic heart disease or to primary cardiomyopathies (mainly ARVC) (1). [escardio.org]
Workup
QRS Wave
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Poor R Wave Progression
Figure 3 shows atrial fibrillation, poor R wave progression, and diffuse ST-segment abnormalities in an ECG from a patient with ischemic cardiomyopathy. [clevelandclinicmeded.com]
Hypertrophy
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Right Ventricular Hypertrophy
Objective: To investigate the sympathovagal balance in PH associated with right ventricular hypertrophy or right ventricular dilation. [jscimedcentral.com]
Although right ventricular hypertension (consequent to pulmonary hypertension) leads to right ventricular hypertrophy and eventually right ventricular dilatation (RVD) with associated right atrial hypertension, or hypertrophy or dilatation, the eventual [academic.oup.com]
[…] case due to right ventricular hypertrophy. [lifeinthefastlane.com]
Hypertrphy may also shift the electrical axis (to the right in right ventricular hypertrophy, and to the left in left ventricular hypertrophy). ST-T segment Significant hypertrophy may result in abnormal depolarization of the ventricular myocardium. [ecgwaves.com]
In this study right ventricular hypertrophy was associated with LV hypertrophy in one- fifth of the patients. [medsci.org]
Treatment
A triad of circulatory collapse, right ventricular dilatation, and large alveolar dead space is proposed for the rapid diagnosis and treatment of massive pulmonary embolism. [ncbi.nlm.nih.gov]
Standard treatment of right ventricular outflow tract or pulmonary artery obstruction involves open chest surgery. [nice.org.uk]
The completely revamped interventional section includes new material on treatment of pediatric and adult congenital heart disease, as well as on coronary atherectomy, thrombectomy, distal embolic protection devices, bare metal and drug-eluting stents, [books.google.de]
Prognosis
Abstract The prognosis of multidetector computed tomography (MDCT) assessed right ventricular dilatation (RVD) is unclear in patients with pulmonary embolism (PE) and a simplified Pulmonary Embolism Severity Index (sPESI) of 0. [ncbi.nlm.nih.gov]
The prognosis of pulmonary hypertension (PH) depends upon the functional capacity of the right ventricle. [jscimedcentral.com]
Our outcome figures suggest a guarded prognosis be given during counseling of parents of fetuses with right heart dilatation. [link.springer.com]
The study of life prognosis in patients with 2 forms of DCM showed that 5-year mortality of patients was about 50%. [ijbm.org]
Etiology
Etiology Primary hypertrophic cardiomyopathy ( 60–90% of cases) Most common hereditary heart disease Most commonly due to mutations in genes encoding myosin heavy chain causes disorganized myocyte architecture characterized by myofibrillar disarray and [amboss.com]
[…] hypoplastic left heart syndrome interrupted aortic arch aortic coarctation ventricular septal defect 1 congenital pulmonary stenosis : tends to cause more wall hypertrophy rather than chamber dilatation dilated fetal cardiomyopathy more unusual cardiac etiologies [radiopaedia.org]
The left ventricular compromise in the proband and in his father may have two different etiologies (in the case of the proband’s father DCM could be secondary to hypertension and valvular disease), but it may also be possible that they have a familial [escardio.org]
A systematic approach to define the etiology is essential for determination of the most effective treatment strategy. [emedicine.medscape.com]
Other studies should be individualized depending upon the suspected etiology of RHF. [revespcardiol.org]
Epidemiology
Overview of major types of cardiomyopathy Dilated cardiomyopathy Epidemiology Most common cardiomyopathy Incidence : 6/100,000 per year Sex: (approx. 3:1) Etiology Idiopathic (approx. 50%) Secondary cause Coronary heart disease Arterial hypertension Peripartum [amboss.com]
Epidemiology The incidence of acute cor pulmonale depends on the underlying cause. [clinicaladvisor.com]
Differences in left ventricular structure between black and white hypertensive adults: the Hypertension Genetic Epidemiology Network Study. Hypertens 2004; 43:1182–1188 View Article Google Scholar 18. [journals.plos.org]
[…] corticosteroids; thus, timely diagnosis via EMB is prudent. [13, 14] Treatment with cyclosporine and corticosteroids is associated with a median transplant-free survival of 12.3 months compared to 3 months without immunosuppression. [15] The European Study of Epidemiology [emedicine.medscape.com]
Pathophysiology
atrial fibrillation ) Mnemonic for etiology of dilated cardiomyopathy : ABCCCD : A A lcohol use, B B eriberi, C C ocaine, C C oxsackie B virus, C C hagas, D D oxorubicin/ D aunorubicin Pathophysiology Structural damage to the myocardium or valves ; [amboss.com]
Right ventricular function in cardiovascular disease, part II: pathophysiology, clinical importance, and management of right ventricular failure. Circulation. 2008 Apr 1;117(13):1717-31. [escardio.org]
“Acute right ventricular failure — from pathophysiology to new treatments”. Intensive Care Med. vol. 30. 2004. pp. 185 Thorough review of all aspects of acute cor pulmonale, with an emphasis on pathophysiology and diagnosis. [clinicaladvisor.com]
Repaired tetralogy of Fallot: the roles of cardiovascular magnetic resonance in evaluating pathophysiology and for pulmonary valve replacement decision support. J Cardiovasc Magn Reson. 2011;13:9. [jcmr-online.biomedcentral.com]
When a clot lodges in the pulmonary arterial circulation, various pathophysiologic effects occur. [rwjms1.umdnj.edu]
Prevention
OBJECTIVES: We hypothesize that concomitant tricuspid annuloplasty in patients with tricuspid annular dilatation who undergo mitral valve repair could prevent progression of tricuspid regurgitation and right ventricular remodeling. [ncbi.nlm.nih.gov]
Objectives We hypothesize that concomitant tricuspid annuloplasty in patients with tricuspid annular dilatation who undergo mitral valve repair could prevent progression of tricuspid regurgitation and right ventricular remodeling. [hartlongcentrum.nl]
His research aims to find better ways to diagnose, treat and prevent people dying from this disease, and beat the heartbreak. Donate [bhf.org.uk]
In some cases, this prevents the heart from filling with blood as it should. Over time, it can affect the other chambers. Symptoms Many people with dilated cardiomyopathy have no symptoms. Some that do have only minor ones, and live a normal life. [webmd.com]