Presentation
Sinus of Valsalva aneurysms rarely present until rupture occurs. [ncbi.nlm.nih.gov]
However, differentiation between these two conditions antenatally in the absence of antegrade right ventricular outflow appears to be unreliable at present. [jhu.pure.elsevier.com]
Cardiovascular
- Heart Disease
CONCLUSIONS: These data support the view that intravascular stenting will become an important adjunct in the management of children with congenital heart disease. [ncbi.nlm.nih.gov]
Epidemiology of Valvular Heart Disease. Valvular Heart Disease (4th ed.). Saunders. pp. 1–13. ^ Braverman AC. The Bicuspid Aortic Valve and Associated Aortic Disease. In: Valvular Heart Disease, 4th, Otto CM, Bonow RO. [en.wikipedia.org]
Cardiac cachexia is a common complication of chronic heart disease [ 3 ]. [ekjm.org]
Amplatz K, Moller JH, Castaneda-Zuniga W (1986) Radiology of heart disease. Thieme Medical Publishers, New York, pp 519–521 Google Scholar 3. [link.springer.com]
- Systolic Murmur
At 5 years of age, a harsh systolic murmur was detected for the first time. [ncbi.nlm.nih.gov]
Examination revealed an ejection systolic murmur in the pulmonary area. The electrocardiogram showed complete heart block. [onlinejacc.org]
Case presentation A 5-month-old female presented to our hospital with a harsh S1 sound and a grade IV systolic murmur on the left sternal boarder. [cardiothoracicsurgery.biomedcentral.com]
Auscultation of the chest wall revealed a harsh systolic grade V-VI/VI murmur at the left upper sternal border. She also showed Kussmaul’s sign. [ekjm.org]
Auscultating her heart, a systolic murmur and click are heard. Recorded with the stethoscope over the mitral valve. [en.wikipedia.org]
- Heart Murmur
Familiar and personal medical history was unremarkable except for a systolic heart murmur known since childhood. The ECG showed left axis deviation and left ventricular (LV) hypertrophy pattern (Panel A) in the absence of an obvious cause. [e-coretvasa.cz]
Musculoskeletal
- Severe Osteoporosis
Severe osteoporosis on bone densitometry was noted. We diagnosed near obstruction of the mid-RV by pectus excavatum and cachectic morphology. [ekjm.org]
Psychiatrical
- Suggestibility
We suggest that this is the plausible cause of the cardiac cachexia in this patient. [ekjm.org]
The importance of a low, fixed cardiac output and nonspecific physical findings in suggesting the clinical diagnosis is emphasized. [ncbi.nlm.nih.gov]
Doppler echocardiography suggested a significant mid-right ventricular pressure gradient ( Figure 2, top left and top right; Movie I). [circ.ahajournals.org]
Workup
X-Ray
- Mediastinal Mass
Chest radiography suggested a large anterior mediastinal mass, which was confirmed by thoracic computed tomography (CT). [heart.bmj.com]
- Anterior Mediastinal Mass
Chest radiography suggested a large anterior mediastinal mass, which was confirmed by thoracic computed tomography (CT). [heart.bmj.com]
Hypertrophy
- Left Ventricular Strain Pattern
An ECG showed left atrial abnormality, left axis deviation, and left ventricular strain pattern ( Figure 1 ). [circ.ahajournals.org]
Treatment
BACKGROUND: Intravascular stenting has been established as a useful treatment in adults with coronary and peripheral vascular disease. [ncbi.nlm.nih.gov]
Conn's Current Therapy provides faster access to the latest therapeutic treatment [books.google.com]
Surgical treatment of right ventricular outflow tract obstruction after Tetralogy of Fallot {S,D,I} repair.. European Journal of Cardio-Thoracic Surgery, 42(2), e28-30. [hsrc.himmelfarb.gwu.edu]
Standard treatment of right ventricular outflow tract or pulmonary artery obstruction involves open chest surgery. [nice.org.uk]
Prognosis
Conclusion: ATC is aggressive carcinoma with a miserable prognosis. It should be borne in mind that possibility of cardiac metastasis and a cause of cardiac death. [thyroidworldcongress.com]
Cardiac metastasis has been shown to have a dismal prognosis. Thus, simple noninvasive routine echocardiography as a part of metastatic work up in thyroid malignancy can help in early diagnosis of metastasis rather than at autopsy. [mjdrdypu.org]
Cardiac cachexia is a common complication of chronic heart disease, which is associated with a poor prognosis, independent of functional disease severity, age, measures of exercise capacity, and left ventricular ejection fraction [ 3 ]. [ekjm.org]
Mortality/Morbidity Prognosis mainly depends on the severity of stenosis in the absence of any additional lesions. Patients with mild-to-moderate stenosis live normal lives with no symptoms, apart from the risk of IE. [emedicine.medscape.com]
Etiology
[…] right ventricular outflow tract obstruction after Tetralogy of Fallot {S,D,I} repair Journal European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery Keywords Postoperative Complications--etiology [hsrc.himmelfarb.gwu.edu]
Epidemiology
Epidemiology of Valvular Heart Disease. Valvular Heart Disease (4th ed.). Saunders. pp. 1–13. ^ Braverman AC. The Bicuspid Aortic Valve and Associated Aortic Disease. In: Valvular Heart Disease, 4th, Otto CM, Bonow RO. [en.wikipedia.org]
Epidemiology Frequency United States In the United States, the relative frequency of IPS among all obstructive lesions of the RV outflow tract is 2-10%. Internationally, no reliable figures have been reported. [emedicine.medscape.com]
Pathophysiology
[…] doi: 10.1097/PCC.0000000000000818 Congenital Heart Disease Abstract Author Information Authors Article Metrics Metrics The objectives of this review are to discuss the anatomy, pathophysiology, clinical course, and current treatment strategies for pulmonary [journals.lww.com]
Most fundamentally, the study sample was comprised of symptomatic patients with heterogeneous pathophysiology. [journals.plos.org]
Pathophysiology IPS has 2 forms. In the more common type, stenosis of the proximal portion of the infundibulum is due to a fibrous or muscle band at the junction of the main cavity of the RV and the infundibulum. [emedicine.medscape.com]
Prevention
The Centers for Disease Control and Prevention (CDC) conducted a study that linked the development of congenital heart defects. [mblynchfirm.com]
Once this condition is recognized, surgical repair can prevent the complications associated with sudden development of an aortocardiac fistula, such as bacterial endocarditis and heart failure. Full English text available at: www.revespcardiol.org [revespcardiol.org]
In the absence of a shunt, minimal manipulation should be performed before cannulation to prevent hypoxic spells. Besides confirming the anatomy with transesophageal echocardiography, an external examination of the heart is conducted. [thoracickey.com]
Stenosis is characterized by a narrowing of the valvular orifice that prevents adequate outflow of blood. [en.wikipedia.org]
Louis, Missouri, USA (3) Department of Clinical Radiology and Imaging Diagnostics, 4th Military Hospital, Wrocław, Poland (4) Center for Diagnosis Prevention and Telemedicine, John Paul II Hospital, Kraków, Poland Abstract Congenital pulmonary valve abnormalities [radiologykey.com]