Presentation
The authors have treated a group of infants who presented with nonsynostotic scaphocephaly, or a so-called sticky sagittal suture. [thejns.org]
This article presents a ... [biomedsearch.com]
Acronym FSPC Synonyms Scaphocephaly with maxillary retrusion and mental retardation Keywords Any medical or genetic information present in this entry is provided for research, educational and informational purposes only. [uniprot.org]
We have been able to collect from the literature eleven cases exactly like those in Apert's series, and four others presenting the same deformity of the head but much less extensive deformities of the extremities. [jamanetwork.com]
Changes in the surgical technique are presented, with zigzag bicoronal incision and the osteotomies referred, which give better aesthetic and functional results. [medigraphic.com]
Entire Body System
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Turkish
Look up "scaphocephaly" at Merriam-Webster Look up "scaphocephaly" at dictionary.com In other languages: Spanish French Italian Portuguese Romanian German Dutch Swedish Russian Polish Czech Greek Turkish Chinese Japanese Korean Arabic Advertisements Advertisements [wordreference.com]
Deutsch (German) العربية (Arabic) Français (French) Русский (Russian) ಕನ್ನಡ (Kannada) 한국어 (Korean) עברית (Hebrew) Український (Ukrainian) اردو (Urdu) Magyar (Hungarian) मानक हिन्दी (Hindi) Indonesia (Indonesian) Italiano (Italian) தமிழ் (Tamil) Türkçe (Turkish [definitions.net]
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Collapse
Secondary synostosis results from a decrease in intracranial volume leading to collapse of the cranial vault. Since this represents a distinct etiopathogenesis different from that typically involved, the surgical approach should be altered. [read.qxmd.com]
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Vietnamese
Русский (Russian) ಕನ್ನಡ (Kannada) 한국어 (Korean) עברית (Hebrew) Український (Ukrainian) اردو (Urdu) Magyar (Hungarian) मानक हिन्दी (Hindi) Indonesia (Indonesian) Italiano (Italian) தமிழ் (Tamil) Türkçe (Turkish) తెలుగు (Telugu) ภาษาไทย (Thai) Tiếng Việt (Vietnamese [definitions.net]
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Pressured Speech
Children between the ages of three and five may also have increased intracranial pressure. Speech and language delay is another associated problem. This can be overcome with the help of a therapist. [hcahealthcare.co.uk]
Cardiovascular
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Heart Failure
The child was operated on at the age of 4 months with relatively satisfactory results, although she died suddenly of acute heart failure 4 months postoperatively... [read.qxmd.com]
Ears
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Low Set Ears
The other congenital deformities included scaphocephaly, somewhat low-set ears, accessory tragi, a high arched palate, and funnel chest. [read.qxmd.com]
Musculoskeletal
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Dolichocephaly
Scaphocephaly (also known as dolichocephaly ) is the most common form of craniosynostosis, where premature closure of the sagittal suture results in an impediment to the lateral growth of the skull while anteroposterior growth continues, producing a narrow [radiopaedia.org]
See also [ edit ] Dolichocephaly References [ edit ] External links [ edit ] Classification D ICD - 10 : Q75.0 ( EUROCAT Q75.01) ICD - 9-CM : 756.0 NINDS Overview [en.wikipedia.org]
Scaphocephaly, also called dolichocephaly, is a congenital birth defect characterized by an asymmetrical distortion or shape of the head. Scaphocephaly occurs frequently in premature infants. [kinderband.net]
This head shape is sometimes also referred to as Dolichocephaly. The head appears long and the forehead can protrude and become square shaped. It is more prevalent in babies that have spent time in neo-natal care. [londonorthotics.co.uk]
Scaphocephaly, also called dolichocephaly, is a congenital birth defect that is characterized by an asymmetric distortion or shape of the head. Scaphocephaly occurs frequently in premature babies. [scopeheal.com]
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Osteoporosis
Bone anomalies like osteoporosis are frequent findings in HIE. Apart from their clinical impact they could be related to factors involved in the pathogenesis of HIE, such as impairment of chemotaxis in tissues or monocyte differentiation... [read.qxmd.com]
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Sloping Shoulders
September 1984: Journal of Neurosurgery # 253 M Golabi, J Carey, B D Hall A male infant was evaluated with macrocephaly, scaphocephaly, a high forehead, a parietal foramen, a midline posterior occipital dermoid, and sloped shoulders. [read.qxmd.com]
Treatment
Almost all children affected with scaphocephaly require surgical treatment. The treatment for this condition is discussed in the Treatment section. Other types of single sutural synostosis: Plagiocephaly Trigonocephaly Posterior Plagiocephaly [thecraniofacialcenter.com]
Associations Marfan syndrome Treatment and prognosis Treatment is often with a cranioplasty. In contrast to other craniosynostoses, there is near normal IQ and no hydrocephalus. [radiopaedia.org]
Potential treatment options icon plus Your consultant will discuss your treatment options with you and help to determine the best approach for your child. Skull-reshaping surgery is often used to correct scaphocephaly. [hcahealthcare.co.uk]
Incidence: 2 – 3 per 10,000 births Treatment: Procedure – Extended strip cranial vault remodelling (ESCVR) at 6 months of age or total cranial vault remodelling (TCVR) at 1 year and over Age at treatment – At the NPCC our preference is to undertake surgery [craniofacial.ie]
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. [orpha.net]
Prognosis
Primary, single-suture craniosynostosis patients tend to do very well In secondary form, prognosis is dependent on underlying cause Scaphocephaly. [learningradiology.com]
Associations Marfan syndrome Treatment and prognosis Treatment is often with a cranioplasty. In contrast to other craniosynostoses, there is near normal IQ and no hydrocephalus. [radiopaedia.org]
Prognosis The clinical outcome of patients having undergone surgery is usually good with normal intelligence and psychomotor development. The documents contained in this web site are presented for information purposes only. [orpha.net]
Prognosis Surgical correction of scaphocephaly leads to significant improvement in the head shape over the ensuing months. Follow up to ensure normal brain and skull development is required. [skullbaseinstitute.com]
Prognosis for mental function in scaphocephaly. J Neurosurg. 1995. 83: 476-9 3. Badve CA, K MM, Ishak GE, Khanna PC. Craniosynostosis: Imaging review and primer on computed tomography. Pediatr Radiol. 2013. 43: 728-42 4. [surgicalneurologyint.com]
Etiology
Etiology The underlying cause of isolated scaphocephaly remains to be determined: a mutation in the TWIST1 gene (7p21) has been reported in a single case. [orpha.net]
Etiology Craniosynostosis has been estimated to occur in 1:2000 to 1:2500 births. [www2.aofoundation.org]
The globes were almost covered by a fold of skin and the findings were interesting in regard to the etiology of cryptophthalmos. [read.qxmd.com]
Epidemiology
Summary Epidemiology It is a relatively common malformation accounting for around 50% of all cases of nonsyndromic craniosynostosis and with an incidence of 1/5,000 live births. [orpha.net]
Focus session on the changing “epidemiology” of craniosynostosis (comparing two quinquennia: 1985–1989 and 2003–2007) and its impact on the daily clinical practice: A review from Necker Enfants Malades. Childs Nerv Syst. 2009. 25: 807-11 9. [surgicalneurologyint.com]
Pathophysiology
Biochemical analysis of pathogenic liganddependent FGFR2 mutations suggests distinct pathophysiological mechanisms for craniofacial and limb abnormalities. Hum Mol Genet. 2004; 13 :2313–2324. [ PMC free article ] [ PubMed ] [ Google Scholar ] 42. [ncbi.nlm.nih.gov]
Prevention
Part II: prevention and treatment. J Craniofac Surg. 2011 Jan; 22(1):17-23. [connects.catalyst.harvard.edu]
When this happens, the bones put pressure on the brain and can prevent it from growing normally. Scaphocephaly also causes a child’s head to look deformed. [scopeheal.com]
The goals of Anesthesia include preventing blood loss, hypothermia and venous air embolism. [mjdrdypu.org]
Premature suture closure prevents perpendicular growth but allows parallel growth. This pattern is termed Virchow’s law and leads to clinically recognizable cranial bone deformations, all of which carry specific nomenclature ( Fig 28-2 ). [aao.org]
Surgery is not required to prevent mental retardation, blindness, seizures or headaches in the vast majority of cases. No amount of surgical expertise can produce a perfect result. [neurosurgery.ucla.edu]