Presentation
[…] case presented with similar histological findings. [doi.org]
Herein, we present a case report on segmental odontomaxillary dysplasia in a 13-year-old boy. [ncbi.nlm.nih.gov]
Thus, the present article describes a case of SOD focusing on its histopathological, immunohistochemical and scanning electron microscopic features. [readbyqxmd.com]
Entire Body System
- Developmental Disorder
Segmental odontomaxillary dysplasia (SOD) is a rare, unilateral developmental disorder of the maxilla involving abnormal growth and maturation of the bone, lack of one or both premolars, altered primary molar structure, delayed tooth eruption, and fibrous [ncbi.nlm.nih.gov]
February 2018: Journal of the American Dental Association # 2 REVIEW Shalu Rai, Rohit Malik, Sapna Panjwani, Deepankar Misra, Sankalp Verma Segmental odontomaxillary dysplasia (SOD) is an uncommon, nonhereditary, rare developmental disorder primarily [readbyqxmd.com]
Background: Segmental odontomaxillary dysplasia (SOD) is a rare developmental disorder of the maxilla characterised by abnormal growth and maturation of bone, teeth and gingiva of the affected segment. [scinapse.io]
Abstract Segmental odontomaxillary dysplasia (SOD) is a rare, unilateral developmental disorder of the maxilla involving abnormal growth and maturation of the bone, lack of one or both premolars, altered primary molar structure, delayed tooth eruption [unboundmedicine.com]
- Soft Tissue Swelling
Soft tissue swelling also has been reported. [16], [17], [18] The histology in our case did not indicate regional odontodysplasia; however, the predominant tissue consisted of immature woven bone. [doi.org]
Soft tissue swelling has also been reported. [5] Gingival fibromatosis Because of the maxillary enlargement and fibrous gingivae in the canine area, this condition was briefly considered. [5] Central hemangioma Radiographic imaging may show a honeycomb [ijdr.in]
Regional Odontodysplasia presenting as a soft tissue swelling. Oral Surg Oral Med Oral Pathol 1989;67:193-6. 16. Schmid-Meier E. Unilateral odontodysplasia with ipsilateral hypoplasia of the midface: A case report. [ijhas.in]
Items of hyperplasia included soft tissue swelling of the ipsilateral hand (70), hyperplasia of the ipsilateral lower limb (72), and enlargement of the ipsilateral foot (71). [medicaljournals.se]
Jaw & Teeth
- Gingival Overgrowth
Intraoral examination revealed a marked buccopalatal expansion of the maxillary right alveolus with a gingival overgrowth extending from the distal of 14 to the distal portion of 18, and was more pronounced on the buccal side. [ijdr.in]
Delayed development of permanent tooth germs in the mandibular arch was also evident which was in agreement with some cases reported previously. [10] Typical clinical features in this case included gingival hyperplasia and teeth embedded in the gingival [contempclindent.org]
- Tooth Loss
[…] and pulp exposure rare (slow and pulp adapts) early diagnosis -replacement of loss posterior teeth -pathologic loss of tooth structure secondary to the action of an external agent -commonly by toothbrushing -cervical notches showing exposed dentin on [quizlet.com]
Familial Expansile Osteolysis( FEO) Autosomal dominant trait Manifest in the second decade Osteoclastic resorption with cancellous bone expansion and elevated serum alkaline phosphatase. Early tooth loss by external resorption Deafness Histologically [slideshare.net]
Ears
- Ear Lobe Crease
lobe crease Slide 16 16 Radiographic feature : Rapid enlargement on right side of maxilla only -accelerated dental development for this 5- year-old patient Slide 17 17 Enlargement of bones include mand.maxilla,zygoma, frontal and temporal bone Enlargement [dokumen.tips]
lobe crease -dysmorphic face left hemi facial hypertrophy 16 Radiographic feature : Rapid enlargement on right side of maxilla only -accelerated dental development for this 5-year-old patient 17 Enlargement of bones include mand.maxilla,zygoma, frontal [slideplayer.com]
Musculoskeletal
- Bony Swelling
Erupting left maxillary second molar was present over the bony swelling. Mucosa over the swelling was normal and there was no tenderness on palpation over the swelling. Clinically retained first and second deciduous molar teeth were present. [jisppd.com]
Skin
- Cutaneous Manifestation
The most common facial cutaneous manifestations are hypertrichosis followed by facial erythema, lip hypopigmentation; and Becker's nevus. [jisppd.com]
[9], [10], [11], [12] The most common facial cutaneous manifestations are hypertrichosis followed by facial erythema, lip hypopigmentation, and Becker's nevus. [1], [3], [5], [6], [8], [12] Other cutaneous manifestations include "hairy nevus," discontinuity [doi.org]
Becker nevus is among the most common cutaneous manifestations of HATS syndrome and can be treated effectively with the Q-switched laser or the erbium:YAG laser. [mdedge.com]
Reported cutaneous manifestations include facial asymmetry, Becker's nevus, "hairy nevus," lip hypopigmentation, discontinuity of the vermilion border, depression of the cheek, and erythema... [readbyqxmd.com]
Face, Head & Neck
- Facial Swelling
He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxillary enlargement and ipsilateral failure of eruption of [dovepress.com]
He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxill... more mented and hypertrichotic skin lesion with unilateral [scinapse.io]
- Frontal Bossing
Open metopic suture Frontal bossing Slide 8 8 Lack of normal coronoid process Multiple unerupted supernumerary teeth Mostly anterior max. n PM region Prolonged retention of 1 dentition Slide 9 9 Multiple of unerupted teeth Axial CT view Slide 10 done [dokumen.tips]
Frontal bossing Open metopic suture 8 Multiple unerupted supernumerary teeth Mostly anterior max. n PM region Lack of normal coronoid process Prolonged retention of 1˚ dentition 9 Multiple of unerupted teeth Axial CT view 10 -excessive mobility of movement [slideplayer.com]
Treatment
The treatment plan should be based on the degree of involvement as well as the functional and esthetic needs in each case. [ncbi.nlm.nih.gov]
Clinicians should be aware of its presence when encountering patients presenting with a facial cutaneous lesion especially when it is associated with facial asymmetry and unresponsive to treatment. [dovepress.com]
This article is intended to serve as baseline data for a future article, describing the natural history and possible treatment of SOD, which remain undocumented. [unboundmedicine.com]
[…] bone Short statue Bone osteoma Multiple intestinal polyps Differential Diagnosis Slide 12 -removal of 1 + supernumerary teeth -removal of bone overlying 2 to expose crown when half of the root is formed -monitor for any distal molar or cyst -surgical treatment [dokumen.tips]
Prognosis
Furcal bone loss is present on teeth 54 and 55, and the long-term prognosis of these teeth is poor. A small portion of the crown of the developing tooth 48 is captured in this imaging volume. [canaray.com]
BiopsyResults TheNephroticSyndrome Treatment Prognosis KidneyTransplantinFSGSWhatisFSGS?FSGSstandsforFocalSegmentalGlomerulosclerosis,andisarelativelycommonformofkidneydisease, especiallyintheUS. [docslide.us]
It has a poor prognosis. 15. Morphology Immunofluorescence microscopy: It reveals nonspecific trapping of immunoglobulins, usually IgM & complement in the areas of hyalinosis. [dokumen.tips]
PROGNOSIS AND MANAGEMENT The lesion is benign and asymptomatic. Therefore, except for cosmesis, no treatment is necessary. Reassurance may be all that is needed. [consultant360.com]
Etiology
Segmental Odontomaxillary Dysplasia (SOD) is an uncommon developmental disorder of unknown etiology that causes a unilateral alteration of the maxilla associated with an abnormal growth and maturation of bone, lack of one or both premolars and delayed [ncbi.nlm.nih.gov]
It can be caused by various etiologic factors ranging from facial trauma to serious hereditary conditions. [readbyqxmd.com]
It is a rare condition of uncertain etiology that results in painless unilateral expansion of the posterior dentoalveolar complex, gingival hyperplasia, lack of one or both premolars in the affected area, delayed eruption of adjacent teeth and malformations [scinapse.io]
Epidemiology
[…] morphogenesis of the ecto-mesodermal tissues in a segment of the maxilla and the overlying facial tissues. [8] A viral or bacterial infection of the maxillary division branches of the trigeminal nerve have been proposed as initial causative factors in SOD. [3] Epidemiology [doi.org]
[…] a circumscribed, brownish patch with geographical borders and sometimes hypertrichosis. 1 This disorder is named after Samuel William Becker, who in 1949 reported 2 young men with focal, unilateral, acquired, hyperpigmentation and hypertrichosis. 2 EPIDEMIOLOGY [consultant360.com]
Ingordo V, Gentile C, Iannazzone SS, Cusano F, Naldi L (2007) The ‘EpiEnlist’ project: a dermo-epidemiologic study on a representative sample of young Italian males. Prevalence of selected pigmentary lesions. [springermedizin.de]
Pathophysiology
Although several factors such as local trauma, infection, ischemia, neural damage, and somatic mutations of neural crest cell migration have been advocated, the underlying pathophysiology of the condition remains unclear. [3], [4] It is reported that [contempclindent.org]
Juvenile Paget Disease (Idiopathic Hyperphosphatasia) Inherited as an autosomal recessive trait Deformities in the long bones, kyphosis, acetabular protrusion and pathophysiologically by rapid turnover. Long bone widening with pathologic fracture [slideshare.net]
Prevention
Includes prevention techniques as well as treatment regimes Contains many colour clinical photographs Accompanied by a large number of references Provides helpful tables to categorise the causes and characteristics of lesions Written by a leading expert [books.google.com]
[…] common on maxilla, lateral incisors, central incisors, premolars -misshapen crown -coronal - more common -radicular - rare -dialted invagination lined by enamel on lateral surface of the root Treatment of dens in dente -depend on severity -restore to prevent [quizlet.com]
This is done to prevent development of facial cellulitis. This should be followed by use of removable partial denture (RPD) till the implant can be placed. [ijhas.in]
Segmental odontomaxillary dysplasia 83 Journal of Indian Society of Pedodontics and Preventive Dentistry. 2014; 32 (1). Rai, S. Malik, R. Unilateral segmental odontomaxillary dysplasia: A rare entity of 3 cases and review. [revistas.ucr.ac.cr]
Regional odontodysplasia: Report of an unusual case involving mandibular arch Department of Pedaitric and Preventive Dentistry, V. S. [contempclindent.org]