[…] case presented with similar histological findings. [doi.org]

We report a case of segmental odontomaxillary dysplasia presenting with hypertrichosis of the face, hyperlinear palms with faint erythema, and commissural lip clefting. [ncbi.nlm.nih.gov]

• Asymptomatic

  There is no osteoblastic rimming of the bone trabeculae (H & E stain, 20x) Click here to view Patient was clinically asymptomatic after 6-month follow-up and was placed on interim prosthetic rehabilitation. [doi.org]

  […] coarse vertically orieted trabeculae 2)Monostatic fibrous dysplasia -not associated with missing teeth 3) Regional odontodysplasia -the teeth appear more radiolucent than normal, so described as "ghost teeth" Slide 26 Lingual salivary depression 26 Asymptomatic [dokumen.tips]

  Treatment  Often difficult, not very satisfactory.  In the asymptomatic patient observation  Antibiotics  Sequestration of the cementum-like masses will occur slowly and followed by healing.  Saucerization or surgical excision 50. [slideshare.net]

  […] is belief to be due to a) bone marrow hyperplasia b) persistent embryologic marrow remnant c) site of abnormal healing after extraction, trauma or local inflammation 33 Incidental radiograph finding More common in middle aged-women Clinical features: Asymptomatic [slideplayer.com]

• Short Stature

  Figure 1: Hyperpigmented, hyperkeratotic, indurated plaque over groins, vulva, and anteromedial aspect of the thighs Click here to view On a general examination, the patient was found to be mentally retarded and deaf with a short stature. [e-ijd.org]

• Hypertension

  Hematuria, Hypertension. 2. Nonselective proteinuria. 3. Poor response to corticosteroids. 4. >50% individuals develop ESRF within 10 y. 5. Adults in general fare even less well than children. 8. Pathogenesis - unknown MCD may transform to FSGS. [dokumen.tips]

• Eruptions

  Abstract Segmental odontomaxillary dysplasia (SOD) is a rare, unilateral developmental disorder of the maxilla involving abnormal growth and maturation of the bone, lack of one or both premolars, altered primary molar structure, delayed tooth eruption [unboundmedicine.com]

  She presented with pre-maxillary enlargement and abnormal pattern of eruption of anterior maxillary permanent teeth. Radiographic imaging showed abnormal bony trabeculation. Histopathologic findings showed characteristic features of SOD. [ncbi.nlm.nih.gov]

  CASE REPORT: A 7-year-old boy was initially referred regarding failure of eruption of maxillary primary molars... [readbyqxmd.com]

• Hypertrichosis

  We report a case of segmental odontomaxillary dysplasia presenting with hypertrichosis of the face, hyperlinear palms with faint erythema, and commissural lip clefting. [ncbi.nlm.nih.gov]

  Unlike the earlier report, Danforth et al did not report facial hypertrichosis. Because of the absence of facial features, Danforth et al suggested the term segmental odontomaxillary dysplasia (SOD). [dev.docslide.net]

  Simultaneous occurrence of segmental odontomaxillary dysplasia and Becker's nevus. 10.1016/S0278-2391(99)90498-6 Becker's nevus is a unilateral, hyperpigmented cutaneous hamartoma usually with hypertrichosis. [scinapse.io]

  Concurrent melanosis and hypertrichosis in distribution of nevus unius lateris. Arch Derm Syphilol. 1949;60:155-160. Dasegowda SB, Basavaraj GB, Nischal KC, et al. Becker’s nevus syndrome. [consultant360.com]

• Skin Lesion

  He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxill... more mented and hypertrichotic skin lesion with unilateral [scinapse.io]

  lesion; the skin lesion is present at birth and has a serrated border like the “coast of Maine.” [consultant360.com]

  The acronym HATS (Hemimaxillary enlargement, Asymmetry of the face, Teeth abnormalities, Skin findings) was introduced in 2004 by Welsch and Stein. [3] They reported two cases with skin lesions. One patient reported having bakers nevus. [ijdr.in]

  The acronym HATS (Hemimaxillary enlargement, Asymmetry of the face, Teeth abnormalities, Skin findings) was introduced in 2004 by Welsch and Stein [6]. They reported two cases with skin lesions. One patient reported having Becker’s nevus. [hindawi.com]

The treatment plan should be based on the degree of involvement as well as the functional and esthetic needs in each case. [ncbi.nlm.nih.gov]

This article is intended to serve as baseline data for a future article, describing the natural history and possible treatment of SOD, which remain undocumented. [unboundmedicine.com]

Various schools of thought exist regarding the treatment. However, the treatment decision varies from case to case. [ijhas.in]

Furcal bone loss is present on teeth 54 and 55, and the long-term prognosis of these teeth is poor. A small portion of the crown of the developing tooth 48 is captured in this imaging volume. [canaray.com]

BiopsyResults TheNephroticSyndrome Treatment Prognosis KidneyTransplantinFSGSWhatisFSGS?FSGSstandsforFocalSegmentalGlomerulosclerosis,andisarelativelycommonformofkidneydisease, especiallyintheUS. [docslide.us]

It has a poor prognosis. 15. Morphology Immunofluorescence microscopy: It reveals nonspecific trapping of immunoglobulins, usually IgM & complement in the areas of hyalinosis. [dokumen.tips]

PROGNOSIS AND MANAGEMENT The lesion is benign and asymptomatic. Therefore, except for cosmesis, no treatment is necessary. Reassurance may be all that is needed. [consultant360.com]

Segmental Odontomaxillary Dysplasia (SOD) is an uncommon developmental disorder of unknown etiology that causes a unilateral alteration of the maxilla associated with an abnormal growth and maturation of bone, lack of one or both premolars and delayed [ncbi.nlm.nih.gov]

It is a rare condition of uncertain etiology that results in painless unilateral expansion of the posterior dentoalveolar complex, gingival hyperplasia, lack of one or both premolars in the affected area, delayed eruption of adjacent teeth and malformations [doaj.org]

This is illustrated by two examples, however, more examples are needed for the complete understanding of the etiology behind frenulae labii, which at present need to receive attention in the dental clinic. [dentalhypotheses.com]

It can be caused by various etiologic factors ranging from facial trauma to serious hereditary conditions. [readbyqxmd.com]

The discussion covers the phenotype spectrum, epidemiology, mode of inheritance, pathogenesis, and clinical profile of each condition, all of which is accompanied by a wealth of illustrations. [books.google.com]

[…] a circumscribed, brownish patch with geographical borders and sometimes hypertrichosis. 1 This disorder is named after Samuel William Becker, who in 1949 reported 2 young men with focal, unilateral, acquired, hyperpigmentation and hypertrichosis. 2 EPIDEMIOLOGY [consultant360.com]

[…] morphogenesis of the ecto-mesodermal tissues in a segment of the maxilla and the overlying facial tissues. [8] A viral or bacterial infection of the maxillary division branches of the trigeminal nerve have been proposed as initial causative factors in SOD. [3] Epidemiology [doi.org]

Ingordo V, Gentile C, Iannazzone SS, Cusano F, Naldi L (2007) The ‘EpiEnlist’ project: a dermo-epidemiologic study on a representative sample of young Italian males. Prevalence of selected pigmentary lesions. [springermedizin.de]

Although several factors such as local trauma, infection, ischemia, neural damage, and somatic mutations of neural crest cell migration have been advocated, the underlying pathophysiology of the condition remains unclear. [3], [4] It is reported that [contempclindent.org]

Juvenile Paget Disease (Idiopathic Hyperphosphatasia)  Inherited as an autosomal recessive trait  Deformities in the long bones, kyphosis, acetabular protrusion and pathophysiologically by rapid turnover.  Long bone widening with pathologic fracture [slideshare.net]

Includes prevention techniques as well as treatment regimes Contains many colour clinical photographs Accompanied by a large number of references Provides helpful tables to categorise the causes and characteristics of lesions Written by a leading expert [books.google.com]

DanielVasudevan Vijeev Medicine Journal of the Indian Society of Pedodontics and Preventive Dentistry 2014 A case report on segmental odontomaxillary dysplasia in a 13-year-old boy is presented and dense bone, which often exhibits a radiographic vertical [semanticscholar.org]

[…] common on maxilla, lateral incisors, central incisors, premolars -misshapen crown -coronal - more common -radicular - rare -dialted invagination lined by enamel on lateral surface of the root Treatment of dens in dente -depend on severity -restore to prevent [quizlet.com]

This is done to prevent development of facial cellulitis. This should be followed by use of removable partial denture (RPD) till the implant can be placed. [ijhas.in]

Segmental odontomaxillary dysplasia 83 Journal of Indian Society of Pedodontics and Preventive Dentistry. 2014; 32 (1). Rai, S. Malik, R. Unilateral segmental odontomaxillary dysplasia: A rare entity of 3 cases and review. [revistas.ucr.ac.cr]