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Segmental Odontomaxillary Dysplasia

SOD


Presentation

  • […] case presented with similar histological findings.[doi.org]
  • We report a case of segmental odontomaxillary dysplasia presenting with hypertrichosis of the face, hyperlinear palms with faint erythema, and commissural lip clefting.[ncbi.nlm.nih.gov]
Aspiration
  • Before biopsying the lesion, aspiration was attempted but no excessive blood flow occurred.[doi.org]
  • Before biopsying the lesion, aspiration was attempted but no excessive blood flow occurred. [5] Treatment of SOD remains unknown as the management protocol in most case reports has not been discussed to date.[ijdr.in]
  • One interesting finding in these children is the frequency of blood aspiration during routine injection procedures. Guzman et al. reported the case with hematoma formation subsequent to infiltration anesthesia administration.[ijhas.in]
Gingival Overgrowth
  • Intraoral examination revealed a marked buccopalatal expansion of the maxillary right alveolus with a gingival overgrowth extending from the distal of 14 to the distal portion of 18, and was more pronounced on the buccal side.[ijdr.in]
  • overgrowth; both of these features were consistent with the majority of cases reported previously. [7] A differential diagnosis of RO includes hereditary conditions, such as dentin dysplasia, dentinogenesis imperfecta, and amelogenesis imperfecta as[contempclindent.org]
Cutaneous Manifestation
  • [9], [10], [11], [12] The most common facial cutaneous manifestations are hypertrichosis followed by facial erythema, lip hypopigmentation, and Becker's nevus. [1], [3], [5], [6], [8], [12] Other cutaneous manifestations include "hairy nevus," discontinuity[doi.org]
  • The most common facial cutaneous manifestations are hypertrichosis followed by facial erythema, lip hypopigmentation; and Becker's nevus.[jisppd.com]
  • , [8] , [9] , [10] , [11] , [12] The most common facial cutaneous manifestations are hypertrichosis followed by facial erythema, lip hypopigmentation, and Becker's nevus. [1] , [3] , [5] , [6] , [8] , [12] Other cutaneous manifestations include "hairy[amsjournal.com]
  • Reported cutaneous manifestations include facial asymmetry, Becker's nevus, "hairy nevus," lip hypopigmentation, discontinuity of the vermilion border, depression of the cheek, and erythema...[readbyqxmd.com]
  • Becker nevus is among the most common cutaneous manifestations of HATS syndrome and can be treated effectively with the Q-switched laser or the erbium:YAG laser.[mdedge.com]
Facial Swelling
  • He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxillary enlargement and ipsilateral failure of eruption of[dovepress.com]
  • He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxill... more mented and hypertrichotic skin lesion with unilateral[scinapse.io]

Treatment

  • The treatment plan should be based on the degree of involvement as well as the functional and esthetic needs in each case.[ncbi.nlm.nih.gov]
  • Clinicians should be aware of its presence when encountering patients presenting with a facial cutaneous lesion especially when it is associated with facial asymmetry and unresponsive to treatment.[dovepress.com]

Prognosis

  • Furcal bone loss is present on teeth 54 and 55, and the long-term prognosis of these teeth is poor. A small portion of the crown of the developing tooth 48 is captured in this imaging volume.[canaray.com]
  • BiopsyResults TheNephroticSyndrome Treatment Prognosis KidneyTransplantinFSGSWhatisFSGS?FSGSstandsforFocalSegmentalGlomerulosclerosis,andisarelativelycommonformofkidneydisease, especiallyintheUS.[docslide.us]
  • It has a poor prognosis. 15. Morphology Immunofluorescence microscopy: It reveals nonspecific trapping of immunoglobulins, usually IgM & complement in the areas of hyalinosis.[dokumen.tips]
  • PROGNOSIS AND MANAGEMENT The lesion is benign and asymptomatic. Therefore, except for cosmesis, no treatment is necessary. Reassurance may be all that is needed.[consultant360.com]

Etiology

  • Segmental Odontomaxillary Dysplasia (SOD) is an uncommon developmental disorder of unknown etiology that causes a unilateral alteration of the maxilla associated with an abnormal growth and maturation of bone, lack of one or both premolars and delayed[ncbi.nlm.nih.gov]
  • It can be caused by various etiologic factors ranging from facial trauma to serious hereditary conditions.[readbyqxmd.com]
  • It is a rare condition of uncertain etiology that results in painless unilateral expansion of the posterior dentoalveolar complex, gingival hyperplasia, lack of one or both premolars in the affected area, delayed eruption of adjacent teeth and malformations[doaj.org]

Epidemiology

  • […] morphogenesis of the ecto-mesodermal tissues in a segment of the maxilla and the overlying facial tissues. [8] A viral or bacterial infection of the maxillary division branches of the trigeminal nerve have been proposed as initial causative factors in SOD. [3] Epidemiology[doi.org]
  • […] a circumscribed, brownish patch with geographical borders and sometimes hypertrichosis. 1 This disorder is named after Samuel William Becker, who in 1949 reported 2 young men with focal, unilateral, acquired, hyperpigmentation and hypertrichosis. 2 EPIDEMIOLOGY[consultant360.com]
  • Ingordo V, Gentile C, Iannazzone SS, Cusano F, Naldi L (2007) The ‘EpiEnlist’ project: a dermo-epidemiologic study on a representative sample of young Italian males. Prevalence of selected pigmentary lesions.[springermedizin.de]
Sex distribution
Age distribution

Pathophysiology

  • Although several factors such as local trauma, infection, ischemia, neural damage, and somatic mutations of neural crest cell migration have been advocated, the underlying pathophysiology of the condition remains unclear. [3] , [4] It is reported that[contempclindent.org]
  • Juvenile Paget Disease (Idiopathic Hyperphosphatasia)  Inherited as an autosomal recessive trait  Deformities in the long bones, kyphosis, acetabular protrusion and pathophysiologically by rapid turnover.  Long bone widening with pathologic fracture[slideshare.net]

Prevention

  • Includes prevention techniques as well as treatment regimes Contains many colour clinical photographs Accompanied by a large number of references Provides helpful tables to categorise the causes and characteristics of lesions Written by a leading expert[books.google.com]
  • Segmental odontomaxillary dysplasia 83 Journal of Indian Society of Pedodontics and Preventive Dentistry. 2014; 32 (1). Rai, S. Malik, R. Unilateral segmental odontomaxillary dysplasia: A rare entity of 3 cases and review.[revistas.ucr.ac.cr]
  • January 2014: Journal of the Indian Society of Pedodontics and Preventive Dentistry # 4 Rebeca S Azevedo, Luísa J da Silveira, Luis Flávio M Moliterno, Águida Maria M A Miranda, Oslei P de Almeida, Fábio R Pires Segmental odontomaxillary dysplasia (SOD[readbyqxmd.com]
  • […] common on maxilla, lateral incisors, central incisors, premolars -misshapen crown -coronal - more common -radicular - rare -dialted invagination lined by enamel on lateral surface of the root Treatment of dens in dente -depend on severity -restore to prevent[quizlet.com]
  • This is done to prevent development of facial cellulitis. This should be followed by use of removable partial denture (RPD) till the implant can be placed.[ijhas.in]

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