After intravenous administration of cyclophosphamide and the start of oral prednisolone, the anti-cardiolipin antibody level decreased and his physical condition improved. [ncbi.nlm.nih.gov]

Hypertension is the only risk factor significantly associated with a more severe course of the disease; no medication proved effective. [ncbi.nlm.nih.gov]

Sneddon's syndrome is a rare vascular disease affecting mainly skin and brain arterioles leading to their occlusion due to excessive endothelial proliferation. [ncbi.nlm.nih.gov]

The Journal of Headache and Pain 2009 10 :109 Springer-Verlag 2009 Received: 7 December 2008 Accepted: 4 February 2009 Published: 14 March 2009 Abstract Sneddon’s syndrome is a rare vascular disease affecting mainly skin and brain arterioles leading to [thejournalofheadacheandpain.springeropen.com]

Handbook of clinical neurology, volume 11: vascular diseases, part iii. New York: Elsevier Science, 1989:401–10. Tourbah A, Piette JC, Iba-Zizen MT, et al. The natural course of cerebral lesions in Sneddon syndrome. Arch Neurol1997;54:53–60. [jnnp.bmj.com]

Bell, Cerebral ischemic events associated with endocarditis, retinal vascular disease, and lupus anticoagulant, The American Journal of Medicine, 90, 3, (299), (1991). J. Dietl, G. Stroppel, M. Poremba and D. [doi.org]

On examination, he had livedo reticularis and perniosis and a systolic murmur. [ncbi.nlm.nih.gov]

Here, we describe the case of a 64-year-old woman presenting with a 4-year history of a throbbing, bilateral, parieto-occipital headache associated with facial pain, but without any other accompanying symptom. [ncbi.nlm.nih.gov]

Delivery by Cesarean section in the 36th week of pregnancy resulted in marked improvement of the neurological signs and symptoms. [ncbi.nlm.nih.gov]

Considered in the context of increased risk of stroke with migraine, a higher frequency of livedo in migraineurs with stroke, and the association of migraine and livedo reticularis, the question of whether livedo reticularis may be a risk marker for stroke [ncbi.nlm.nih.gov]

The association between migraine and juvenile stroke: a case–control study. Headache 2003 ; 43: 90 – 5. Google Scholar Crossref Medline ISI 9. [doi.org]

The proportion with headache in this second group is 58% (102 individuals), with headache described as migraine in 28 (27.5%) of the headache subjects, including six with migraine with aura. [ncbi.nlm.nih.gov]

J Neurol Neurosurg Psychiatry 74:542–544 PubMed Central PubMed View Article Google Scholar Headache Classification Subcommittee of The International Headache Society (2004) The International Classification of Headache Disorders, 2nd edn. [thejournalofheadacheandpain.springeropen.com]

Nonspecific prodromal symptoms (headache, dizziness) frequently (80%) precede livedo racemosa for 3.5 and (multi)focal neurological symptoms of fully developed disease for 9 years followed by progressive cognitive impairment (60%) 10 years later. [ncbi.nlm.nih.gov]

Non-specific prodromal symptoms (headache, dizziness) often precede livedo reticularis by several years and this is followed by the development of focal neurological symptoms and then progressive cognitive impairment. [skin-disorders.net]

In the natural course of patients with SS, neurological events such as headache (62%) and dizziness (54%) have been recorded. [elsevier.es]

Nonspecific prodromal symptoms (headache, dizziness) often precede livedo reticularis by several years and this is followed by the development of focal neurological symptoms and then progressive cognitive impairment. [patient.info]

The pain, initially misdiagnosed as atypical trigeminal neuralgia, worsened up to chronic daily and such severely disabling headache that she was constrained to bed. [ncbi.nlm.nih.gov]

In this case the patient has not been properly treated for a 4-year period and an atypical bilateral trigeminal neuralgia was diagnosed. [thejournalofheadacheandpain.springeropen.com]

1 Infantile spasms broad thumbs Microcephaly glomerulonephritis Marfanoid habitus Laing distal myopathy MOGS-CDG (CDG-IIb) Sideroblastic anemia and mitochondrial myopathy Congenital mirror movement disorder Limb-girdle muscular dystrophy Trigeminal neuralgia [checkrare.com]

The pain, initially misdiagnosed as atypical trigeminal neuralgia, worsened up to chronic daily and such severely disabling headache that she was constrained to bed. [ncbi.nlm.nih.gov]

In this case the patient has not been properly treated for a 4-year period and an atypical bilateral trigeminal neuralgia was diagnosed. [thejournalofheadacheandpain.springeropen.com]

neuralgia Spinocerebellar ataxia autosomal recessive 8 Primary orthostatic tremor Spinocerebellar ataxia 18 Spinocerebellar ataxia 14 GAPO syndrome Dopa-responsive dystonia; Segawa syndrome AD Myosin storage myopathy Neurocutaneous melanosis Grubben [checkrare.com]

Visual field testing revealed a left homonymous hemianopia with macular sparing. [ncbi.nlm.nih.gov]

Sneddons syndrome in a patient with homonymous hemianopia with macular sparing. Bull Soc Belge Ophthalmol. 1996;263:103–107. 13. Rehany U, Kassif Y, Rumelt S. [journals.lww.com]

Narbay G: Sneddon’s syndrome in a patient with homonymous hemianopia with macular sparing. Bull Soc Belge Ophtalmol. 1996, 263: 103-107. 41. [ojrd.biomedcentral.com]