USH3 is characterized by postlingual, progressive hearing loss, variable vestibular dysfunction, and onset of retinitis pigmentosa symptoms, including nyctalopia, constriction of the visual fields, and loss of central visual acuity, usually by the second [uniprot.org]

Usher syndrome type III is characterized by postlingual, progressive hearing loss, variable vestibular dysfunction, and onset of retinitis pigmentosa symptoms, including nyctalopia, constriction of the visual fields, and loss of central visual acuity, [ncbi.nlm.nih.gov]

Progressive hearing loss is characteristic of USH3. Elsewhere USH3 has been regarded as a rarity covering only several percent of the whole Usher population. [link.springer.com]

People with Usher syndrome type III experience progressive hearing loss and vision loss beginning in the first few decades of life, according to Genetics Home Reference. [collive.com]

RP causes nightblindness and a loss of peripheral vision through the progressive degeneration of the retina. [sense.org.uk]

RP causes night-blindness and a loss of peripheral vision (side vision) through the progressive degeneration of the retina. The retina is a light-sensitive tissue at the back of the eye and is crucial for vision. [news-medical.net]

Loss of vision [ 4 ] usually starts with night blindness and this is followed by loss of peripheral vision. Some degree of tunnel vision can continue until quite late. [patient.info]

In adolescence, people with Usher syndrome type 1F develop retinitis pigmentosa, an eye disease which causes night blindness and a gradual loss of peripheral vision. Eventually only the central vision remains, creating “tunnel vision.” [jscreen.org]

Retinitis pigmentosa causes night-blindness and a loss of peripheral vision (side vision) through the progressive degeneration of the retina. The retina is a light-sensitive tissue at the back of the eye and is crucial for vision. [pvfla.org]

All three types are inherited in an autosomal recessive manner. 0000662 Reduced visual acuity Decreased clarity of vision 0007663 Rod-cone dystrophy 0000510 Showing of 7 Last updated: 5/1/2019 Usher syndrome is inherited in an autosomal recessive manner [rarediseases.info.nih.gov]

Some patients have the so-called 'Charles Bonnet syndrome,' involving decreased visual acuity and vivid visual hallucinations. [uniprot.org]

Some patients have the so-called Charles Bonnet syndrome, involving decreased visual acuity and vivid visual hallucinations. [genecards.org]

Three clinical entities have been defined: type 1 (around 40% of cases), in which hearing loss is congenital, profound, nonprogressive, and typically associated with vestibular areflexia leading to delayed acquisitions (delayed head control and unassisted [orpha.net]

[…] problems often begin in teens Vestibular function Balance problems from birth Normal Normal to near-normal, chance of later problem Usher syndrome type I (USH1) is the most severe form, characterized by severe to profound congenital deafness, vestibular areflexia [centogene.com]

Type 1 (USH1) accounts for almost 40% of cases and is the most severe form, characterized by severe to profound congenital deafness, vestibular areflexia, and prepubertal onset of progressive RP. [blueprintgenetics.com]

[…] majority of Usher syndrome cases can be clinically classified into three subtypes. 3, 4 USH type I (USH1; OMIM 276900, 276903, 276904, 601067, 602097, 602083 and 606943) is characterised by profound prelingual sensorineural hearing loss, vestibular areflexia [jmg.bmj.com]